A Study to Test How Safe Pozelimab and Cemdisiran Combination Therapy and Cemdisiran Alone Are and How Well They Work in Adult Patients With Generalized Myasthenia Gravis

NCT ID: NCT05070858

Last Updated: 2025-08-22

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

288 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-12-14

Study Completion Date

2028-11-11

Brief Summary

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This study is researching the experimental drugs called pozelimab and cemdisiran, and cemdisiran monotherapy. The study is focused on patients with generalized myasthenia gravis (gMG). Myasthenia gravis is a disease that causes weakness and fatigue in muscles in the body because the nerves and muscles are not communicating properly. The aim of the study is to see how effective pozelimab and cemdisiran are when used in combination and when pozelimab and cemdisiran are used alone for patients with gMG.

The study is looking at several other research questions, including:

* What side effects may happen from taking the study drugs
* How the study drugs work inside the body
* How much study drugs are in the blood at different times
* Whether the body makes antibodies against pozelimab and cemdisiran (which could make the drugs less effective or could lead to side effects)

Detailed Description

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DBTP- Double blind treatment period (24 weeks) ETP - Extension treatment period (28 weeks) OLTP- Open label treatment period (68 weeks) Off-treatment follow up period (52 weeks)

Conditions

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Generalized Myasthenia Gravis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Group 1

Placebo in DBTP; Re-randomized to Combination or Cemdisiran in ETP and OLTP

Group Type EXPERIMENTAL

Pozelimab + Cemdisiran

Intervention Type DRUG

Subcutaneous administration as described in the protocol

Cemdisiran

Intervention Type DRUG

SC administration as described in the protocol

Placebo

Intervention Type OTHER

SC administration as described in the protocol

Group 2

Combination regimen throughout the study

Group Type EXPERIMENTAL

Pozelimab + Cemdisiran

Intervention Type DRUG

Subcutaneous administration as described in the protocol

Group 3

Cemdisiran throughout the study

Group Type EXPERIMENTAL

Cemdisiran

Intervention Type DRUG

SC administration as described in the protocol

Group 4

Pozelimab monotherapy in DBTP followed by combination in ETP and OLTP

Group Type EXPERIMENTAL

Pozelimab

Intervention Type DRUG

SC administration as described in the protocol

Interventions

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Pozelimab + Cemdisiran

Subcutaneous administration as described in the protocol

Intervention Type DRUG

Cemdisiran

SC administration as described in the protocol

Intervention Type DRUG

Placebo

SC administration as described in the protocol

Intervention Type OTHER

Pozelimab

SC administration as described in the protocol

Intervention Type DRUG

Other Intervention Names

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ALN-CC5 REGN3918

Eligibility Criteria

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Inclusion Criteria

1. Male or female patients ≥18 years of age at screening (or ≥ legal age of adulthood based on local regulations, whichever is older)
2. Patient with documented diagnosis of myasthenia gravis (MG) based on medical history and supported by previous evaluations as described in the protocol
3. Documented prior history of positive serologic test or a positive result during screening of anti-acetylcholine receptor (AChR) antibodies or anti-LRP4 antibodies.
4. Myasthenia Gravis Foundation of America (MGFA) Clinical Classification Class II to IVa at screening
5. Myasthenia Gravis-Activities of Daily Living (MG-ADL) score ≥6 at screening. Ocular items should not contribute more than 50% of MG-ADL total score as described in the protocol
6. Currently receiving an acetylcholinesterase inhibitor or documented reason for not using acetylcholinesterase inhibitor therapy per investigator
7. Currently receiving an immunosuppressive therapy (IST) for MG, or documented reason why the patient is not taking an IST per investigator
8. If currently receiving an IST, not anticipated to have IST dosage changed before randomization or during double-blind treatment period (DBTP).
9. Willing and able to comply with clinic visits and study-related procedures, including completion of the primary series of the meningococcal vaccinations required per protocol

Exclusion Criteria

1. Patients with antibody profile that is only positive for muscle specific tyrosine kinase (MuSK) (MuSK positivity is based on a documented prior history of positive serologic test for antibodies to MuSK or a positive result during screening
2. History of thymectomy within 12 months prior to screening or planned during the study
3. History of malignant thymoma (patients with stage 1 may be enrolled), or history of cancer within the past 5 years, except for adequately treated basal cell skin cancer, squamous cell skin cancer, or in situ cervical cancer
4. Myasthenic crisis or Myasthenia Gravis Foundation of America (MGFA) Class V within 1 month of screening
5. Not meeting meningococcal vaccination requirements and, at a minimum, documentation of quadrivalent meningococcal vaccination within 5 years prior to randomization and serotype B vaccine (when available) within 3 years prior to randomization as described in the protocol
6. Known contraindication to meningococcal vaccines (group ACWY conjugate and group B vaccines) as described in the protocol
7. Patients who require antibiotics for meningococcal prophylaxis and have a contraindication, warning, or precaution precluding the use of penicillin class and penicillin-alternative antibiotics planned to be used for prophylaxis, or a history of intolerance leading to the discontinuation of these antibiotics
8. Positive hepatitis B surface antigen or hepatitis C virus ribonucleic acid (RNA) during screening. NOTE: Cases with unclear interpretation should be discussed with the medical monitor
9. History of HIV infection or a positive test at screening per local requirements
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Regeneron Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Clinical Trial Management

Role: STUDY_DIRECTOR

Regeneron Pharmaceuticals

Locations

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HonorHealth Neurology 2018

Scottsdale, Arizona, United States

Site Status

University of California Irvine

Irvine, California, United States

Site Status

University of Southern California

Los Angeles, California, United States

Site Status

Colorado Springs Neurological Associates

Colorado Springs, Colorado, United States

Site Status

SFM Clinical Research, LLC

Boca Raton, Florida, United States

Site Status

Diverse Clinical Research

Miami, Florida, United States

Site Status

Aqualane Clinical Research

Naples, Florida, United States

Site Status

Neurological Services of Orlando

Orlando, Florida, United States

Site Status

Medsol Clinical Research Center Inc

Port Charlotte, Florida, United States

Site Status

University of South Florida Morsani Center for Advanced Healthcare

Tampa, Florida, United States

Site Status

NorthShore University Health System

Glenview, Illinois, United States

Site Status

St. Elizabeth's Hospital

O'Fallon, Illinois, United States

Site Status

Northwest Neurology Ltd. - Clinedge - PPDS

Rolling Meadows, Illinois, United States

Site Status

Wayne State University School of Medicine

Detroit, Michigan, United States

Site Status

Dayton Center for Neurological Disorders

Centerville, Ohio, United States

Site Status

University of Cincinnati Gardner Neuroscience Institute

Cincinnati, Ohio, United States

Site Status

Penn Medicine University City

Philadelphia, Pennsylvania, United States

Site Status

National Neuromuscular Research Institute

Austin, Texas, United States

Site Status

Nerve and Muscle Center of Texas

Houston, Texas, United States

Site Status

Universitair Ziekenhuis Antwerpen

Edegem, Antwerp, Belgium

Site Status

AZ Sint-Lucas

Ghent, Oost-Vlaanderen, Belgium

Site Status

IMV Pesquisa Neurologica

Porto Alegre, Rio Grande do Sul, Brazil

Site Status

Jordy Sinapse Medicina LTDA

Itapevi, São Paulo, Brazil

Site Status

Faculdade de Medicina Do ABC

Santo André, São Paulo, Brazil

Site Status

Pseg Centro de Pesquisa Clinica S.A

São Paulo, , Brazil

Site Status

Hospital das Clinicas da Faculdade de Medicina da Universidade de Sao Paulo

São Paulo, , Brazil

Site Status

University of Alberta

Edmonton, Alberta, Canada

Site Status

London Health Sciences Centre

London, Ontario, Canada

Site Status

Toronto General Hospital

Toronto, Ontario, Canada

Site Status

Peking Union Medical College Hospital

Beijing, Beijing Municipality, China

Site Status

Fujian Medical University Union Hospital

Fuzhou, Fujian, China

Site Status

Guangdong Hospital of Traditional Chinese Medicine

Guangdong, Guangdong, China

Site Status

Nanfang Hospital Southern Medical University

Guangzhou, Guangdong, China

Site Status

The University of Hong Kong-Shenzhen Hospital

Shenzhen, Guangdong, China

Site Status

The First Affiliated Hospital of Guangzhou University of Chinese Medicine

Guangzhou, Guangzhou, China

Site Status

Hainan General Hospital

Haikou, Hainan, China

Site Status

Renmin Hospital of Wuhan University - Hubei Provincial People's Hospital

Wuhan, Hubei, China

Site Status

Xiangya Hospital Central South University

Changsha, Hunan, China

Site Status

The First Hospital of Jilin University

Changchun, Jilin, China

Site Status

Qilu Hospital of Shandong University (Qingdan)

Qingdao, Shandong, China

Site Status

Huashan Hospital Fudan University

Shanghai, Shanghai Municipality, China

Site Status

The Second Affiliated Hospital of the Chinese Peoples' Liberation Army Air Force Medical University

Xi’an, Shanxi, China

Site Status

Sichuan Provincial People's Hospital

Chengdu, Sichuan, China

Site Status

Tianjin Medical University General Hospital

Tianjin, Tianjin Municipality, China

Site Status

Aalborg Universitetshospital

Aalborg, North Denmark, Denmark

Site Status

Aarhus University Hospital

Aarhus N, , Denmark

Site Status

Rigshospitalet, Copenhagen

Copenhagen, , Denmark

Site Status

Odense Universitetshospital

Odense, , Denmark

Site Status

Centre Hospitalier Universitaire de Nice

Nice, Alpes Maritimes, France

Site Status

CHU Bicetre

Le Kremlin-Bicêtre, , France

Site Status

Centre Hospitalier Regional Universitaire (CHRU) de Nancy

Nancy, , France

Site Status

Hopital de la Pitie Salpetriere

Paris, , France

Site Status

Israeli-Georgian Medical Research Clinic Healthycore, LTD

Tbilisi, , Georgia

Site Status

LTD New Hospitals

Tbilisi, , Georgia

Site Status

Pineo Medical Ecosystem

Tbilisi, , Georgia

Site Status

LTD National Center of Urology Named after L. Managadze

Tbilisi, , Georgia

Site Status

Multiprofile Clinic Consilium Medulla

Tbilisi, , Georgia

Site Status

Friedrich Baur Institute

München, Bavaria, Germany

Site Status

University Hospital Essen

Essen, North Rhine-Westphalia, Germany

Site Status

Universitatsklinikum Munster

Münster, North Rhine-Westphalia, Germany

Site Status

Universitatsklinikum Leipzig

Leipzig, Saxony, Germany

Site Status

Charite - Universitatsmedizin Berlin

Berlin, , Germany

Site Status

Universitatsklinikum Jena

Jena, , Germany

Site Status

Government General Hospital, Guntur

Guntur, Andhra Pradesh, India

Site Status

Institute of Neurosciences

Surat, Gujarat, India

Site Status

Nizam's Institute of Medical Sciences (NIMS)

Panjagutta, Hyderabad, India

Site Status

Kasturba Medical College (KMC)

Udupi, Karnataka, India

Site Status

Amrita Institute of Medical Sciences and Research Centre (AIMS)

Kochi, Kerala, India

Site Status

Deenanath Mangeshkar Hospital and Research Centre

Pune, Maharashtra, India

Site Status

Seth G.S. Medical College & K.E.M. Hospital, Mumbai

Pārel, Mumbai, India

Site Status

All India Institute of Medical Sciences New Delhi

New Delhi, National Capital Territory of Delhi, India

Site Status

Polakulath Narayanan Renai Medicity Multi Specialty Hospital, Kochi

Kochi, Punjab, India

Site Status

Christian Medical College & Hospital

Ludhiana, Punjab, India

Site Status

Apex Hospital

Jaipur, Rajasthan, India

Site Status

City Neuro Centre, Hyderabad

Hyderabad, Telangana, India

Site Status

Bangalore Medical College and Research Institute (BMCRI) - Victoria Hospital

Bangalore, , India

Site Status

Postgraduate Institute of Medical Education & Research

Chandigarh, , India

Site Status

Azienda Ospedaliera Sant'andrea

Rome, Lazio, Italy

Site Status

Fondazione IRCCS Di Rilievo Nazionale Istituto Nazionale Neurologico Carlo Besta

Milan, Lombardy, Italy

Site Status

Azienda Ospedaliero Universitaria Pisana

Pisa, Tuscany, Italy

Site Status

Azienda Ospedaliera Papa Giovanni XXIII

Bergamo, , Italy

Site Status

Universita' Degli Studi di Roma La Sapienza

Roma, , Italy

Site Status

Kobe City Medical Center General Hospital

Kobe, Hyōgo, Japan

Site Status

Kochi Medical School Hospital

Nankoku, Kochi, Japan

Site Status

Okinawa National Hospital

Ginowan-Shi, Okinawa, Japan

Site Status

Okinawa Prefectural Nanbu Medical Center and Children's Medical Center

Shimajiri, Okinawa, Japan

Site Status

Saitama Medical University, Saitama Medical Center

Kawagoe, Saitama, Japan

Site Status

Medical Hospital of Tokyo Medical and Dental University

Bunkyo, Tokyo, Japan

Site Status

Tokyo Medical University Hospital

Shinjuku, Tokyo, Japan

Site Status

Nihon University Itabashi Hospital

tabashi City, Tokyo, Japan

Site Status

Yamaguchi University Hospital

Ube, Yamaguchi, Japan

Site Status

Chiba University Hospital

Chiba, , Japan

Site Status

Hiroshima City Hiroshima Citiz

Hiroshima, , Japan

Site Status

Japanese Red Cross Osaka Hospital

Osaka, , Japan

Site Status

Clinical Research Center Spolka z Ograniczona Odpowiedzialnoscia Medic-R Sp.k

Poznan, Greater Poland Voivodeship, Poland

Site Status

NZOZ Neuro-kard

Poznan, Greater Poland Voivodeship, Poland

Site Status

Centrum Neurologii Klinicznej, Krakowska Akademia Neurologii

Krakow, Lesser Poland Voivodeship, Poland

Site Status

NeuroProtect

Warsaw, Mazovian, Poland

Site Status

Uniwersyteckie Centrum Kliniczne WUM, Centralny Szpital Kliniczny

Warsaw, Mosavian, Poland

Site Status

Gdanski Uniwersytet Medyczny

Gdansk, Pomeranian Voivodeship, Poland

Site Status

University Clinical Centre Nis

Niš, , Serbia

Site Status

Kyungpook National University Chilgok Hospital

Daegu, , South Korea

Site Status

Samsung Medical Center

Seoul, , South Korea

Site Status

Hospital de la Santa Creu i Sant Pau

Barcelona, , Spain

Site Status

Hospital Universitari i Politecnic La Fe

Valencia, , Spain

Site Status

Chang Gung Memorial Foundation Kaohsiung Branch

Kaohsiung City, , Taiwan

Site Status

China Medical University

Taichung, , Taiwan

Site Status

National Cheng Kung University Hospital

Tainan City, , Taiwan

Site Status

Shin Kong Wu Ho Su Memorial Hospital

Taipei, , Taiwan

Site Status

Chang Gung Memorial Hospital at Linkou

Taoyuan District, , Taiwan

Site Status

Kocaeli University Hospital

Izmit, Van, Turkey (Türkiye)

Site Status

Dokuz Eylul University Medical Faculty

Izmir, , Turkey (Türkiye)

Site Status

Ondokuz Mayis Universitesi Tip Fakultesi Hastanesi

Samsun, , Turkey (Türkiye)

Site Status

Karadeniz Technical University Farabi Hospital

Trabzon, , Turkey (Türkiye)

Site Status

Sheffield Teaching Hospital NHS Foundation Trust

Sheffield, South Yorkshire, United Kingdom

Site Status

University Hospital Birmingham

Birmingham, , United Kingdom

Site Status

Countries

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United States Belgium Brazil Canada China Denmark France Georgia Germany India Italy Japan Poland Serbia South Korea Spain Taiwan Turkey (Türkiye) United Kingdom

Other Identifiers

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2020-003272-41

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

2023-508842-17-00

Identifier Type: CTIS

Identifier Source: secondary_id

R3918-MG-2018

Identifier Type: -

Identifier Source: org_study_id

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