An Extension Study to Evaluate Casimersen or Golodirsen in Patients With Duchenne Muscular Dystrophy

NCT ID: NCT03532542

Last Updated: 2024-09-19

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

TERMINATED

Clinical Phase

PHASE3

Total Enrollment

171 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-08-02

Study Completion Date

2023-07-26

Brief Summary

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The main objective of this study is to evaluate the safety and tolerability of long-term treatment with casimersen or golodirsen in patients with Duchenne muscular dystrophy (DMD).

Detailed Description

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Conditions

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Duchenne Muscular Dystrophy

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Casimersen

Patients amenable to exon 45 skipping who have completed a clinical trial evaluating casimersen will receive open-label casimersen intravenous (IV) infusions, weekly, at 30 mg/kg for up to 144 Weeks.

Group Type EXPERIMENTAL

Casimersen

Intervention Type DRUG

Casimersen solution for IV infusion

Golodirsen

Patients amenable to exon 53 skipping who have completed a clinical trial evaluating golodirsen will receive open-label golodirsen intravenous (IV) infusions, weekly, at 30 mg/kg for up to 144 Weeks.

Group Type EXPERIMENTAL

Golodirsen

Intervention Type DRUG

Golodirsen solution for IV infusion

Interventions

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Casimersen

Casimersen solution for IV infusion

Intervention Type DRUG

Golodirsen

Golodirsen solution for IV infusion

Intervention Type DRUG

Other Intervention Names

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SRP-4045 AMONDYS 45 SRP-4053 VYONDYS 53

Eligibility Criteria

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Inclusion Criteria

* Completed a clinical trial evaluating casimersen or golodirsen, per protocol.
* Is between 7 and 23 years of age, inclusive, at enrollment.
Minimum Eligible Age

7 Years

Maximum Eligible Age

23 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Sarepta Therapeutics, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Medical Director

Role: STUDY_DIRECTOR

Sarepta Therapeutics, Inc.

Locations

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Neuromuscular Research Center

Phoenix, Arizona, United States

Site Status

Children's Hospital Los Angeles

Los Angeles, California, United States

Site Status

University of California Los Angeles

Los Angeles, California, United States

Site Status

Stanford Neuroscience Health Center

Palo Alto, California, United States

Site Status

Rady Children's Hospital- San Diego

San Diego, California, United States

Site Status

UF Health: University of Florida Clinical Research Center

Gainesville, Florida, United States

Site Status

NW Florida Clinical Research Group, LLC

Gulf Breeze, Florida, United States

Site Status

Rare Disease Research, LLC

Atlanta, Georgia, United States

Site Status

Ann and Robert H Lurie Childrens Hospital of Chicago

Chicago, Illinois, United States

Site Status

University of Iowa Childrens Hospital

Iowa City, Iowa, United States

Site Status

University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status

Kennedy Krieger Institute

Baltimore, Maryland, United States

Site Status

Boston Children's Hospital

Boston, Massachusetts, United States

Site Status

St. Louis Children's Hospital

St Louis, Missouri, United States

Site Status

Las Vegas Clinic

Las Vegas, Nevada, United States

Site Status

University of Rochester Medical Center - Department of Neurology

Rochester, New York, United States

Site Status

Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, United States

Site Status

Abigail Wexner Research Institute at Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

Shriners Hospital for Children

Portland, Oregon, United States

Site Status

Children's Hospital of Pittsburgh of UPMC

Pittsburgh, Pennsylvania, United States

Site Status

Children's Medical Center Dallas

Dallas, Texas, United States

Site Status

Texas Children's Hospital

Houston, Texas, United States

Site Status

University of Utah - PPDS

Salt Lake City, Utah, United States

Site Status

Children's Hospital of The King's Daughters

Norfolk, Virginia, United States

Site Status

Children's Hospital of Wisconsin, Corporate Center Suite 540

Milwaukee, Wisconsin, United States

Site Status

UZ Gent

Ghent, Oost-Vlaanderen, Belgium

Site Status

UZ Leuven

Leuven, , Belgium

Site Status

University Multiprofile Hospital for active treatment Aleksandrovska EAD Clinic of Neurological Diseases

Sofia, , Bulgaria

Site Status

Alberta Children's Hospital

Calgary, Alberta, Canada

Site Status

Children's Hospital of Eastern Ontario

Ottawa, Ontario, Canada

Site Status

Fakultni nemocnice Brno, Klinika detske neurologie LF MU a FN Brno

Brno, , Czechia

Site Status

Fakultni nemocnice v Motole

Prague, , Czechia

Site Status

Hotel Dieu- CHU Nantes

Nantes, , France

Site Status

Hôpital Armand Trousseau

Paris, , France

Site Status

Universitatsklinikum Freiberg

Freiburg im Breisgau, Baden-Wurttemberg, Germany

Site Status

Universitatsklinikum Essen

Essen, North Rhine-Westphalia, Germany

Site Status

Schneider Children's Medical Center of Israel

Petah Tikva, , Israel

Site Status

UOSD Centro Traslazionale di Miologia e Patologie Neurogenerative

Genoa, Liguria, Italy

Site Status

Azienda Ospedaliero-Universitaria di Ferrara - Arcispedale Sant' Anna

Cona, , Italy

Site Status

Fondazione Policlinico Universitario A Gemelli

Milan, , Italy

Site Status

Samodzielny Publiczny Centralny Szpital Kliniczny

Warsaw, Masovian Voivodeship, Poland

Site Status

Uniwersyteckie Centrum Kliniczne, Klinica Neurologii Rozwojowej

Gdansk, , Poland

Site Status

Hospital de La Santa Creu i Sant Pau

Barcelona, Catalonia, Spain

Site Status

Hospital Sant Joan de Deu

Barcelona, , Spain

Site Status

Hospital Universitari i Politecnic La Fe de Valencia

Valencia, , Spain

Site Status

Provningsenhet Barn, Drottning Silvias Och Ungdomssjukhus

Gothenburg, , Sweden

Site Status

Leeds General Infirmary, Leeds Teaching Hospitals NHS Trust

Leeds, , United Kingdom

Site Status

Alder Hey Children's NHS Foundation Trust

Liverpool, , United Kingdom

Site Status

Great Ormond Street Hospital (GOSH)

London, , United Kingdom

Site Status

Royal Victoria Infirmary

Newcastle upon Tyne, , United Kingdom

Site Status

Countries

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United States Belgium Bulgaria Canada Czechia France Germany Israel Italy Poland Spain Sweden United Kingdom

Provided Documents

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Document Type: Study Protocol

View Document

Other Identifiers

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2017-004625-32

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

4045-302

Identifier Type: -

Identifier Source: org_study_id

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