Safety Study of Eteplirsen to Treat Early Stage Duchenne Muscular Dystrophy

NCT ID: NCT02420379

Last Updated: 2021-01-25

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

33 participants

Study Classification

INTERVENTIONAL

Study Start Date

2015-06-30

Study Completion Date

2018-12-17

Brief Summary

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This is an open-label study to assess the safety, tolerability, efficacy and pharmacokinetics of eteplirsen in patients with early stage Duchenne muscular dystrophy (DMD) who are amenable to exon 51 skipping.

Detailed Description

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Safety, including adverse event monitoring and routine laboratory assessments, will be followed on an ongoing basis for all patients.

Clinical efficacy, including functional tests and MRI, will be assessed at regularly scheduled study visits. Patients will undergo one baseline and one follow-up muscle biopsy.

Population and serial PK will be collected.

Conditions

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Duchenne Muscular Dystrophy (DMD)

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Control Group

Approximately 20 patients with DMD not amenable to exon 51 skipping will be observed for 96 weeks.

Group Type NO_INTERVENTION

No interventions assigned to this group

Open-Label

Approximately 20 patients will receive weekly infusions of eteplirsen 30 mg/kg .

Group Type EXPERIMENTAL

eteplirsen

Intervention Type DRUG

Eteplirsen 30 mg/kg will be administered as an IV infusion once a week for 96 weeks.

Interventions

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eteplirsen

Eteplirsen 30 mg/kg will be administered as an IV infusion once a week for 96 weeks.

Intervention Type DRUG

Other Intervention Names

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AVI-4658 EXONDYS 51®

Eligibility Criteria

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Inclusion Criteria

* Male 4-6 years of age.
* Diagnosis of DMD, genotypically confirmed.
* Stable dose of oral corticosteroids for at least 12 weeks or has not received corticosteroids for at least 12 weeks.
* Intact right and left biceps muscles or two alternative upper arm muscle groups.
* Parent that is willing to provide consent and comply with study procedures.

Exclusion Criteria

* Use of any pharmacologic treatment (other than corticosteroids) within 12 weeks that may have an effect on muscle strength or function (e.g., growth hormone, anabolic steroids).
* Previous or current treatment with any other experimental treatments within 12 weeks or participation in any other clinical trial within 6 months.
* Major surgery within 3 months prior to the first dose of study drug, or planned surgery during this study which would interfere with the ability to perform study activities.
* Presence of other clinically significant illness.
Minimum Eligible Age

4 Years

Maximum Eligible Age

6 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Sarepta Therapeutics, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Medical Director

Role: STUDY_DIRECTOR

Sarepta Therapeutics, Inc.

Locations

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Neuromuscular Research Center of Arizona

Phoenix, Arizona, United States

Site Status

Ronald Reagan UCLA Medical Center

Los Angeles, California, United States

Site Status

University of California, Davis Medical Center

Sacramento, California, United States

Site Status

Stanford University Medical Center

Stanford, California, United States

Site Status

University of Florida, Shands Hospital

Gainesville, Florida, United States

Site Status

Rare Disease Research Center

Atlanta, Georgia, United States

Site Status

Children's Hospital of Atlanta

Atlanta, Georgia, United States

Site Status

University of Iowa Children's Hospital

Iowa City, Iowa, United States

Site Status

St. Louis Children's Hospital

St Louis, Missouri, United States

Site Status

Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

Shriners Hospital for Children

Portland, Oregon, United States

Site Status

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

Seattle Children's Hospital

Seattle, Washington, United States

Site Status

Countries

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United States

Provided Documents

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Document Type: Statistical Analysis Plan

View Document

Document Type: Study Protocol

View Document

Other Identifiers

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4658-203

Identifier Type: -

Identifier Source: org_study_id

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