Extension Study of NS-065/NCNP-01 in Boys With Duchenne Muscular Dystrophy (DMD)

NCT ID: NCT03167255

Last Updated: 2022-12-28

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

16 participants

Study Classification

INTERVENTIONAL

Study Start Date

2017-07-06

Study Completion Date

2021-11-15

Brief Summary

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This is an open-label, extension study of NS-065/NCNP-01 administered intravenously once weekly for an additional 192 weeks to boys with DMD who complete Study NS-065/NCNP-01-201.

Detailed Description

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This is a Phase II, multicenter, open-label, extension study of NS-065/NCNP-01 administered intravenously once weekly for an additional 192 weeks to boys with DMD who complete Study NS-065/NCNP-01-201. This study will evaluate the safety, tolerability, and clinical efficacy of NS-065/NCNP-01 at dose levels of up to 80 mg/kg/week administered by weekly IV infusion over an additional treatment period of 192 weeks or until enrollment in a separate long-term follow up program of NS-065/NCNP-01, whichever is earlier.

Patients who complete the Phase II Dose-finding Study NS-065/NCNP-01-201 are eligible to enroll.

Conditions

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Duchenne Muscular Dystrophy

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

PARALLEL

Low Dose cohort of 40 mg/kg and High Dose cohort of 80 mg/kg
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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NS-065/NCNP-01 40mg/kg

Patients receiving 40mg/kg in the NS-065-NCNP-201 study will continue their current dose for an additional 192 weeks or until enrollment in a separate long-term follow up program of NS-065/NCNP-01, whichever is earlier.

Group Type EXPERIMENTAL

NS-065/NCNP-01

Intervention Type DRUG

Received during weekly intravenous infusions

NS-065/NCNP-01 80mg/kg

Patients receiving 80mg/kg in the NS-065-NCNP-201 study will continue their current dose for an additional 192 weeks or until enrollment in a separate long-term follow up program of NS-065/NCNP-01, whichever is earlier.

Group Type EXPERIMENTAL

NS-065/NCNP-01

Intervention Type DRUG

Received during weekly intravenous infusions

Interventions

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NS-065/NCNP-01

Received during weekly intravenous infusions

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

1. Completed Study NS-065/NCNP-01-201 through Week 25.
2. Willing and able to comply with scheduled visits, investigational product administration plan, and study procedures.
3. Stable dose of glucocorticoid (GC), and is expected to remain on the stable dose for the duration of the study.

Exclusion Criteria

1. Serious or severe adverse event in Study NS-065/NCNP-01-201 that precludes safe use of NS-065/NCNP-01.
2. Patient had a treatment which was made for the purpose of dystrophin or its related protein induction after completion of Study NS-065/NCNP-01-201.
3. Patient took any other investigational drugs after completion of Study NS-065/NCNP-01-201.
4. Patient was judged by the investigator and/or the Sponsor that it was not appropriate to participate in the extension study for other reasons.
Minimum Eligible Age

4 Years

Maximum Eligible Age

10 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Nippon Shinyaku Co., Ltd.

INDUSTRY

Sponsor Role collaborator

Cooperative International Neuromuscular Research Group

NETWORK

Sponsor Role collaborator

Therapeutic Research in Neuromuscular Disorders Solutions

INDUSTRY

Sponsor Role collaborator

NS Pharma, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Paula R. Clemens, MD

Role: STUDY_CHAIR

University of Pittsburgh

Locations

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UC Davis

Sacramento, California, United States

Site Status

Lurie Children's Hospital

Chicago, Illinois, United States

Site Status

Washington University

St Louis, Missouri, United States

Site Status

Duke University Medical Center

Durham, North Carolina, United States

Site Status

Children's Hospital of Richmond at VCU

Richmond, Virginia, United States

Site Status

Alberta Children's Hospital

Calgary, Alberta, Canada

Site Status

Countries

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United States Canada

Provided Documents

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Document Type: Study Protocol and Statistical Analysis Plan

View Document

Other Identifiers

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NS-065/NCNP-01-202

Identifier Type: -

Identifier Source: org_study_id