Study of AOC 1044 in Healthy Adult Volunteers and Participants With Duchenne Muscular Dystrophy (DMD) Mutations Amenable to Exon 44 Skipping

NCT ID: NCT05670730

Last Updated: 2025-07-14

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE1/PHASE2

Total Enrollment

70 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-11-09

Study Completion Date

2024-11-25

Brief Summary

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AOC 1044-CS1 (EXPLORE44) is a Phase 1/2 study to evaluate the safety, tolerability, pharmacokinetics, and pharmacodynamic effects of single and multiple ascending doses of AOC 1044 in healthy adult volunteers and participants with DMD mutations amenable to exon 44 skipping.

Part A is a single dose design with multiple cohorts (dose levels) in healthy adult volunteers.

Part B is a multiple-ascending dose design with 3 cohorts (dose levels) in participants with Duchenne.

Detailed Description

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Conditions

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Duchenne Muscular Dystrophy Exon 44

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

SEQUENTIAL

AOC 1044-CS1 (EXPLORE44) is a 2-part study:

Part A: 5 cohorts with single ascending doses conducted in healthy adult volunteers

Part B: 3 cohorts with multiple ascending doses in participants with DMD mutations amenable to exon 44 skipping
Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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AOC 1044-CS1 Part A - Single Dose Levels 1-5

AOC 1044 will be administered once.

Group Type EXPERIMENTAL

AOC 1044

Intervention Type DRUG

AOC 1044 will be administered via intravenous (IV) infusion

AOC 1044-CS1 Part A - Single Dose: Placebo

Placebo will be administered once.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Placebo will be administered via intravenous (IV) infusion.

AOC 1044-CS1 Part B - Multiple Ascending Dose Levels 1-3

AOC 1044 will be administered three times.

Group Type EXPERIMENTAL

AOC 1044

Intervention Type DRUG

AOC 1044 will be administered via intravenous (IV) infusion

AOC 1044-CS1 Part B - Multiple Ascending Dose: Placebo

Placebo will be administered three times.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Placebo will be administered via intravenous (IV) infusion.

Interventions

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AOC 1044

AOC 1044 will be administered via intravenous (IV) infusion

Intervention Type DRUG

Placebo

Placebo will be administered via intravenous (IV) infusion.

Intervention Type DRUG

Other Intervention Names

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Saline

Eligibility Criteria

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Inclusion Criteria

* Aged 18 to 55 years, inclusive, at the time of informed consent
* Body mass index (BMI) of 18.5 to 32.0 kg/m2


* Aged 7 to 27 years, inclusive, at the time of informed consent
* Clinical diagnosis of DMD or clear onset of DMD symptoms at or before the age of 6 years
* Confirmation of DMD gene mutation amenable to exon 44 skipping
* Weight ≥ 23 kg
* Ambulatory or non-ambulatory

* Ambulatory participants: LVEF ≥50% and FVC≥50%
* Non-ambulatory participants: LVEF ≥45% and FVC≥40%
* PUL 2.0 entry item A ≥3
* If on corticosteroids, stable dose for 30 days before screening and throughout the study

Exclusion Criteria

* Clinically significant abnormalities in laboratory results, ECGs, or vitals
* Current or recent use of prescription or nonprescription drugs
* Positive drug/alcohol test at Screening or Day -1
* Elevated blood pressure (BP) \>130/80 mmHg at Screening
* Participation in a clinical study in which an investigational product was received within 1 month of screening or 5 half-lives of the investigational product

Part B:


* Biceps brachii muscles unsuitable for biopsy
* Serum hemoglobin \< lower limit of normal
* Uncontrolled hypertension or diabetes
* Prior treatment with any cell or gene therapy
* Prior treatment with another exon 44 skipping agent within 6 months prior to informed consent
* Recently treated with an investigational drug
* History of multiple drug allergies
Minimum Eligible Age

7 Years

Maximum Eligible Age

55 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

Yes

Sponsors

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Avidity Biosciences, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Carmen Castrillo, MD

Role: STUDY_DIRECTOR

Avidity Biosciences, Inc.

Locations

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Arkansas Children's

Little Rock, Arkansas, United States

Site Status

UCSD

La Jolla, California, United States

Site Status

Stanford University

Palo Alto, California, United States

Site Status

Rare Disease Research - Atlanta

Atlanta, Georgia, United States

Site Status

University of Iowa

Iowa City, Iowa, United States

Site Status

University of Massachusetts Chan Medical School

Worcester, Massachusetts, United States

Site Status

Gillette Children's

Saint Paul, Minnesota, United States

Site Status

Rare Disease Research NC

Hillsborough, North Carolina, United States

Site Status

Abigail Research Institute at Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

Worldwide Clinical Trials (Part A only)

San Antonio, Texas, United States

Site Status

Countries

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United States

Other Identifiers

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AOC 1044-CS1

Identifier Type: -

Identifier Source: org_study_id

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