Ph2 Open-label Study of AOC 1044 in Duchenne Muscular Dystrophy Participants With Mutations Amenable to Exon44 Skipping

NCT ID: NCT06244082

Last Updated: 2025-05-14

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE2

Total Enrollment

39 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-01-22

Study Completion Date

2027-07-31

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

AOC 1044-CS2 (EXPLORE44-OLE) is an Open-label Study to Evaluate the Long-Term Safety and Tolerability of AOC 1044 Administered Intravenously to DMD Participants with Mutations Amenable to Exon 44 Skipping.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

AOC 1044-CS2 (EXPLORE44-OLE) is an open label, extension study to Part B of AOC 1044-CS1 (EXPLORE44). AOC 1044-CS2 is designed to evaluate the long-term safety, tolerability, pharmacokinetics, and exploratory efficacy of AOC 1044.

All participants who enroll in AOC 1044-CS2 will receive active treatment. The treatment period is 2 years with IV dosing every 6 weeks.

Once participants have completed active treatment, they will be followed through a 3-month safety follow-up period. The sponsor may extend active treatment beyond 2 years at a future timepoint.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

DMD Duchenne Muscular Dystrophy Duchenne Exon 44

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Randomization from the parent study, AOC 1044-CS1 will remain blinded.

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

AOC 1044 Multiple Dose Levels

AOC 1044 will be IV infused every 6 weeks for approximately 2 years.

Group Type EXPERIMENTAL

AOC 1044

Intervention Type DRUG

AOC 1044 will be administered via intravenous (IV) infusion

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

AOC 1044

AOC 1044 will be administered via intravenous (IV) infusion

Intervention Type DRUG

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

Rollover Participants:

* Satisfactorily completed AOC 1044-CS1 (EXPLORE44) as determined by the Investigator and Sponsor
* No significant tolerability issues with AOC 1044

De novo Participants:

* Aged 7 to 27 years, inclusive, at the time of informed consent
* Clinical diagnosis of DMD or clear onset of DMD symptoms at or before the age of 6 years
* Confirmation of DMD gene mutation amenable to exon 44 skipping
* Weight ≥ 23 kg
* Ambulatory or non-ambulatory

* Ambulatory participants: LVEF ≥50% and FVC≥50%
* Non-ambulatory participants: LVEF ≥45% and FVC≥40%
* PUL 2.0 entry item A ≥3
* If on corticosteroids, stable dose for 30 days before screening and throughout the study

Exclusion Criteria

Rollover Participants:

* Presence of any new condition or worsening of existing condition that could affect a participant\'s safety or ability to comply with study procedures

De novo Participants:

* Serum hemoglobin \< lower limit of normal
* Uncontrolled hypertension or diabetes
* Prior treatment with any cell or gene therapy
* Prior treatment with another exon 44 skipping agent within 6 months prior to informed consent
* Recently treated with an investigational drug
* History of multiple drug allergies
Minimum Eligible Age

7 Years

Maximum Eligible Age

27 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Avidity Biosciences, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Carmen Castrillo, MD

Role: STUDY_DIRECTOR

Avidity Biosciences, Inc.

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Arkansas Children's Hospital

Little Rock, Arkansas, United States

Site Status

University of California, San Diego, Rady's Children's Hospital

La Jolla, California, United States

Site Status

UC Davis Medical Center

Sacramento, California, United States

Site Status

Lucille Packard Children's Hospital at Stanford

San Carlos, California, United States

Site Status

Rare Disease Research - Atlanta

Atlanta, Georgia, United States

Site Status

University of Massachusetts Medical School

Worcester, Massachusetts, United States

Site Status

Gillette Children's Specialty Healthcare

Saint Paul, Minnesota, United States

Site Status

Rare Disease Research

Hillsborough, North Carolina, United States

Site Status

Abigail Wexner Research Institute at Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

Neurology Rare Disease Center

Denton, Texas, United States

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

AOC 1044-CS2

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

Phase I/II Study of SRP-4053 in DMD Patients
NCT02310906 COMPLETED PHASE1/PHASE2
Exploratory Study of NS-089/NCNP-02 in DMD
NCT04129294 COMPLETED PHASE1/PHASE2