NS-050/NCNP-03 in Boys With DMD (Meteor50)

NCT ID: NCT06053814

Last Updated: 2025-09-10

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

20 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-09-18

Study Completion Date

2027-05-31

Brief Summary

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This is a Phase 1/2 study of Multiple-Ascending Dose (MAD) levels for 12 weeks of treatment followed by 24 weeks of open-label treatment with a selected dose of NS-050/NCNP-03 administered once weekly to ambulant boys with DMD, who have a DMD exon deletion amenable to exon 50 skipping.

Detailed Description

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Conditions

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Duchenne Muscular Dystrophy

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Part 1: NS-050/NCNP-03

Participants will be randomized and receive NS-050/NCNP-03 intravenous (IV) infusions once weekly for 2 weeks at each of MAD levels (1.95, 5, 10, 20, 40, and 80 mg/kg).

Group Type EXPERIMENTAL

NS-050/NCNP-03

Intervention Type DRUG

NS-050/NCNP-03 solution for IV infusion.

Part 1: Placebo

Participants will be randomized and receive NS-050/NCNP-03 placebo-matching IV infusions once weekly for 2 weeks at each of MAD levels.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

NS-050/NCNP-03 placebo-matching solution for IV infusion.

Part 2: NS-050/NCNP-03

Participants will receive NS-050/NCNP-03 IV infusions once weekly for 24 weeks at the dosage selected by the Data and Safety Monitoring Board (DSMB) at the conclusion of Part 1.

Group Type EXPERIMENTAL

NS-050/NCNP-03

Intervention Type DRUG

NS-050/NCNP-03 solution for IV infusion.

Interventions

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NS-050/NCNP-03

NS-050/NCNP-03 solution for IV infusion.

Intervention Type DRUG

Placebo

NS-050/NCNP-03 placebo-matching solution for IV infusion.

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Male ≥ 4 years and \<15 years of age;
* Confirmed DMD exon deletion in the dystrophin gene that is amenable to skipping of exon 50 to restore the dystrophin mRNA reading frame;
* Able to walk independently without assistive devices;
* Able to complete the TTSTAND without assistance in \<20 seconds;
* Stable dose of glucocorticoid for at least 3 months and the dose is expected to remain on a stable dose for the duration of the study.

Exclusion Criteria

* Evidence of symptomatic cardiomyopathy;
* Current or previous treatment with anabolic steroids (e.g., oxendolone, oxandrolone) or products containing resveratrol or adenosine triphosphate within 3 months prior to first dose of study drug;
* Currently taking another investigational drug or has taken another investigational drug within 3 months prior to the first dose of study drug;
* Surgery within the 3 months prior to the first dose of study drug or planned during the study duration;
* Having taken any gene therapy.
Minimum Eligible Age

4 Years

Maximum Eligible Age

14 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Nippon Shinyaku Co., Ltd.

INDUSTRY

Sponsor Role collaborator

NS Pharma, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Children's Hospital Los Angeles

Los Angeles, California, United States

Site Status NOT_YET_RECRUITING

Children's Hospital Colorado

Aurora, Colorado, United States

Site Status RECRUITING

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, United States

Site Status RECRUITING

University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status RECRUITING

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status RECRUITING

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, United States

Site Status RECRUITING

Alberta Children's Hospital

Calgary, Alberta, Canada

Site Status NOT_YET_RECRUITING

British Columbia Children's Hospital

Vancouver, British Columbia, Canada

Site Status NOT_YET_RECRUITING

London Health Sciences Centre

London, Ontario, Canada

Site Status RECRUITING

National Hospital Organization Nagara Medical Center

Nagara, Gifu, Japan

Site Status RECRUITING

Hyogo Medical University Hospital

Nishinomiya, Hyōgo, Japan

Site Status RECRUITING

NHO Osaka Toneyama Medical Center

Toyonaka, Osaka, Japan

Site Status RECRUITING

National Center of Neurology and Psychiatry

Kodaira, Tokyo, Japan

Site Status RECRUITING

Pusan National University Yangsan Hospital

Yangsan, Gyeongsangnam-do, South Korea

Site Status RECRUITING

Seoul National University Hospital

Seoul, , South Korea

Site Status NOT_YET_RECRUITING

Ankara Bilkent City Hospital

Ankara, , Turkey (Türkiye)

Site Status NOT_YET_RECRUITING

Istanbul University

Istanbul, , Turkey (Türkiye)

Site Status NOT_YET_RECRUITING

Yeditepe University Kosuyolu Hospital

Istanbul, , Turkey (Türkiye)

Site Status NOT_YET_RECRUITING

Countries

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United States Canada Japan South Korea Turkey (Türkiye)

Central Contacts

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Trial Info

Role: CONTACT

1-866-677-4276

Facility Contacts

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Martha Arellano-Garcia

Role: primary

CCHO Neuromuscular Research Team

Role: primary

Raven Hill

Role: primary

312-227-2937

Alex McNeil

Role: primary

913-945-9943

Caitlin Sworin

Role: primary

570-909-6858

Heather DiCostanzo

Role: primary

Julie Dao

Role: primary

Vesna Popovska

Role: primary

Rhiannon Hicks

Role: primary

Clinical Trial Management Office

Role: primary

Clinical Trial Management Office

Role: backup

Clinical Trial Office

Role: primary

JaeYoon Kim

Role: primary

Hyeon Ju Kwon

Role: primary

Other Identifiers

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NS-050/NCNP-03-101

Identifier Type: -

Identifier Source: org_study_id

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