Open-label Study of Adjunctive GNX Treatment in Children and Adults With TSC-related Epilepsy

NCT ID: NCT05604170

Last Updated: 2025-10-01

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

View full results

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

TERMINATED

Clinical Phase

PHASE3

Total Enrollment

117 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-05-16

Study Completion Date

2025-04-02

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

This is a Phase 3, global, open-label extension (OLE) study of adjunctive GNX treatment in children and adults with TSC who previously participated in either Study 1042-TSC-3001 or Study 1042-TSC-2001

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Tuberous Sclerosis Complex

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

This is an open-label, single arm study with no blinding as all participants will receive adjunctive GNX

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Ganaxolone (GNX) oral suspension, 3 times a day (TID)

Group Type EXPERIMENTAL

Ganaxolone

Intervention Type DRUG

GNX will be administered.

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

Ganaxolone

GNX will be administered.

Intervention Type DRUG

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

1. Completion of Study 1042-TSC-3001 or participants who continue to meet study requirements in Study 1042-TSC-2001.
2. Participant/parent(s)/LAR(s) willing and able to give written informed consent/assent, after being properly informed of the nature and risks of the study and prior to engaging in any study-related procedures. If the participant is not qualified or able to provide written informed consent based on age, developmental stage, intellectual capacity, or other factors, parent(s)/LAR(s) must provide assent for study participation, if appropriate.
3. Parent(s)/caregiver(s) is (are) willing and able to maintain an accurate and complete daily seizure diary for the duration of the study.
4. Willing and able to take Investigational product (IP) (suspension) as directed with food TID.
5. Women of childbearing potential (WOCBP) must be using a medically acceptable method of birth control and have a negative quantitative serum beta-human chorionic growth hormone (β-HCG) test collected at the initial visit. Childbearing potential is defined as a female who is biologically capable of becoming pregnant. Medically acceptable methods of birth control include intrauterine devices (that have been in place for at least 1 month prior to the screening visit), hormonal contraceptives (eg, combined oral contraceptives, patch, vaginal ring, injectables, and implants), and surgical sterilization (such as oophorectomy or tubal ligation). When used consistently and correctly, "double-barrier" methods of contraception can be used as an effective alternative to highly effective contraception methods. Contraceptive measures such as Plan B™, sold for emergency use after unprotected sex, are not acceptable methods for routine use
6. Male participants must agree to use highly effective contraceptive methods during the study and for 30 days after the last dose of IP. Highly effective methods of contraception include surgical sterilization (such as a vasectomy) and adequate "double-barrier" methods.

Exclusion Criteria

1. Pregnant or breastfeeding.
2. An active Central nervous system (CNS) infection, demyelinating disease, or degenerative neurological disease.
3. History of psychogenic nonepileptic seizures.
4. Any disease or condition (other than TSC) at the initial visit that could compromise the hematologic, cardiovascular (including any cardiac conduction defect), pulmonary, renal, gastrointestinal, or hepatic systems; or other conditions that might interfere with the absorption, distribution, metabolism, or excretion of the IP, or would place the participant at increased risk or interfere with the assessment of safety/efficacy. This may include any illness in the past 4 weeks which in the opinion of the investigator may affect seizure frequency.
5. Unwillingness to avoid excessive alcohol use or cannabis use throughout the study.
6. Have active suicidal plan/intent or have had active suicidal thoughts in the past 6 months or a suicide attempt in the past 6 months.
7. Known sensitivity or allergy to any component in the IP(s), progesterone, or other related steroid compounds.
8. Exposed to any other investigational drug (except for GNX in Study 1042-TSC-2001 or Study 1042-TSC-3001) or investigational device within 30 days or fewer than 5 half-lives prior to Visit 1 (first visit of the OLE). For therapies in which half-life cannot be readily established, the Sponsor's medical monitor should be consulted.
Minimum Eligible Age

1 Year

Maximum Eligible Age

65 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Marinus Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Arkansas Children's Research Institute

Little Rock, Arkansas, United States

Site Status

UCLA Mattel Children's Hospital, TSC Center

Los Angeles, California, United States

Site Status

Children's Hospital of Orange County

Orange, California, United States

Site Status

Rady Children's Hospital - San Diego

San Diego, California, United States

Site Status

Children's Hospital Colorado

Aurora, Colorado, United States

Site Status

Nemours Children's Hospital - Delaware Valley

Wilmington, Delaware, United States

Site Status

Boston Children's Hospital, Harvard Medical School

Boston, Massachusetts, United States

Site Status

Mayo Clinic - Rochester

Rochester, Minnesota, United States

Site Status

Children's Mercy Hospital

Kansas City, Missouri, United States

Site Status

University of Rochester Medical Center

Rochester, New York, United States

Site Status

University of North Carolina at Chapel Hill

Chapel Hill, North Carolina, United States

Site Status

Atrium Health/Levine Children's Hospital

Charlotte, North Carolina, United States

Site Status

Duke University Medical Center

Durham, North Carolina, United States

Site Status

Cincinnati Children's Hospital Medical Center

Cincinnati, Ohio, United States

Site Status

Le Bonheur Children's Hospital

Memphis, Tennessee, United States

Site Status

Child Neurology Consultants of Austin (CNCA)

Austin, Texas, United States

Site Status

University of Texas Southwestern Medical Center

Dallas, Texas, United States

Site Status

McGovern Medical School at the University of Texas Health Science Center

Houston, Texas, United States

Site Status

University of Utah Health Care-Pediatric Neurology

Salt Lake City, Utah, United States

Site Status

Seattle Children's Hospital

Seattle, Washington, United States

Site Status

Austin Health

Heidelberg, , Australia

Site Status

Royal Brisbane and Women's Hospital

Herston, , Australia

Site Status

Alfred Health

Melbourne, , Australia

Site Status

Royal Melbourne Hospital

Parkville, , Australia

Site Status

Hôtel Dieu de Montréal - CHUM

Montreal, , Canada

Site Status

CHU Sainte-Justine

Montreal, , Canada

Site Status

The Hospital for Sick Children

Toronto, , Canada

Site Status

Toronto Western Hospital

Toronto, , Canada

Site Status

BC Children's Hospital

Vancouver, , Canada

Site Status

Peking University First Hospital

Beijing, , China

Site Status

Beijing Children Hospital, Capital Medical University

Beijing, , China

Site Status

Chinese PLA General Hospital

Beijing, , China

Site Status

The Affiliated Hospital of Guizhou Medical University

Beijing, , China

Site Status

First Hospital of Jilin University

Jilin, , China

Site Status

University Hospital of Lyon

Bron, , France

Site Status

Hôpital Sud

Rennes, , France

Site Status

University of Strasbourg

Strasbourg, , France

Site Status

Epilepsie-Zentrum Bethel - Krankenhaus Mara

Bielefeld, , Germany

Site Status

University Hospital Bonn

Bonn, , Germany

Site Status

ZNN - Epilepsiezentrum Frankfurt am Main

Frankfurt, , Germany

Site Status

Universitäts Krankenhaus Freiburg

Freiburg im Breisgau, , Germany

Site Status

Gemeinschaftskrankenhaus Herdecke

Herdecke, , Germany

Site Status

Epilepsiezentrum Kleinwachau gGmbH

Radeberg, , Germany

Site Status

Schneider Children´s Medical Center

Petah Tikva, , Israel

Site Status

Pediatric Neurology and Muscular Diseases Unit - University of Genoa

Genova, , Italy

Site Status

Policlinico Umberto I

Rome, , Italy

Site Status

Hospital de la Santa Creu i Sant Pau

Barcelona, , Spain

Site Status

Hospital Sant Joan de Déu

Barcelona, , Spain

Site Status

Hospital Infantil Universitario Niño Jesús

Madrid, , Spain

Site Status

Hospital Ruber International

Madrid, , Spain

Site Status

Hospital Regional Universitario de Málaga

Málaga, , Spain

Site Status

Hospital Universitario y Politécnico La Fe

Valencia, , Spain

Site Status

Bristol Royal Hospital for Children

Bristol, , United Kingdom

Site Status

Sheffield Children's Hospital

Sheffield, , United Kingdom

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States Australia Canada China France Germany Israel Italy Spain United Kingdom

Provided Documents

Download supplemental materials such as informed consent forms, study protocols, or participant manuals.

Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

1042-TSC-3002

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

Randomized Therapy In Status Epilepticus
NCT04391569 COMPLETED PHASE3
RNS System RESPONSE Study
NCT04839601 TERMINATED NA