SEVENFACT® for Bleeding Events in Hemophilia With Inhibitors

NCT ID: NCT04647227

Last Updated: 2026-01-12

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE4

Total Enrollment

55 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-06-28

Study Completion Date

2027-03-31

Brief Summary

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Phase IV multi-center, US-centric, open-label, safety study enrolling participants with Hemophilia A or B with inhibitors, 12 years of age and older, who are either on long term prophylactic treatment (e.g., emicizumab) at risk of experiencing a breakthrough bleeding event (BE), or who are not on prophylactic treatment who may need to control a BE.

Detailed Description

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Primary Objective:

To evaluate the safety of SEVENFACT® when used to treat bleeding episodes in participants with Hemophilia A or B with inhibitors either with or without prophylactic treatment

Study Design:

Phase IV multi-center, US-centric, open-label, safety study enrolling participants with Hemophilia A and B with inhibitors12 years of age and older, who are either on long term prophylactic treatment (e.g., emicizumab) at risk of experiencing a breakthrough bleeding event (BE), or who are not on prophylactic treatment who may need to control a BE.

Study Duration:

Participants will be followed longitudinally from the time of enrollment to the end of their participation in the study. The maximal study duration for any participant in the study will be approximately 4 years from the time of enrollment.

Target Accrual:

This is a multi-site study in which it is anticipated approximately 28 to 55 participants will be enrolled. The study will target enrollment of participants with Hemophilia A and B with inhibitors on prophylaxis with FDA-approved therapies. Enrollment will continue until September 30, 2026, or until the time that the 28th participant is enrolled, whichever comes first.

Data Analysis:

Sample Size Determination:

Results from the study (March 19, 2024, data transfer) with 19 participants enrolled and 3 participant discontinuations were used to calculate the annual bleeding rate for participants receiving prophylactic treatment. Adjusted annualized bleeding rate was calculated at 0.58.

Based on these data, up to 28 participants with hemophilia A and B with inhibitors on FDA-approved prophylaxis treatments will be attempted to enroll.

Analysis Populations:

The Safety Analysis Set is defined as all participants who received at least a single dose of SEVENFACT®. All analyses of safety will be performed based on the safety population, and participants will be analyzed according to the dose of SEVENFACT® that they actually received.

Baseline Characteristics:

Baseline characteristics will be summarized using descriptive statistics for continuous variables, and frequencies and percentages for categorical variables.

Safety Evaluations:

All Adverse Events (AEs) will be graded for severity utilizing Common Terminology Criteria for Adverse Events (CTCAE) v5.0 and coded using Medical Dictionary of Regulatory Activities (MedDRA) version 23.x. The number and percentage of participants with treatment-emergent AEs (TEAEs), serious AEs (SAEs), serious TEAEs and treatment related TEAEs (i.e., adverse drug reactions \[ADRs\]) will be presented for all participants.

The number of TEAEs, as well as the number and percentage of participants with TEAEs, serious TEAEs, and treatment-related TEAEs will be presented by MedDRA System Organ Class (SOC) and preferred term for all participants.

The number and percentage of participants with treatment-emergent adverse event and/or allergic and anaphylactic reactions will be presented for all participants.

Efficacy Evaluations:

There are no pre-specified efficacy endpoints.

Interim Analysis:

An interim analysis will be conducted after 20 participants have been enrolled into the study. The analysis will seek to characterize baseline, disease, dosing and safety outcome profiles of participants treated with SEVENFACT.

Conditions

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Hemophilia A With Inhibitor Hemophilia B With Inhibitor

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

ATHN 16 is a phase IV multi-center, US-centric, open-label, safety study
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Hemophilia A and B Cases

SEVENFACT® has been approved for the treatment of bleeding events in individuals with hemophilia A or B with inhibitors. This study is intended to further investigate the safety and tolerability of SEVENFACT in participants with hemophilia A or B with inhibitors in the presence or absence of prophylactic therapies. Dosing will be at the discretion of the attending physician, and each participant will be supplied with the equivalent of nine 75 µg/kg doses, which aligns with the recommended dosing schedule as provided in SEVENFACT's United States Prescribing Information (USPI). In the event of a bleeding episode (BE), the participant will either self-administer the correct dose under the guidance of the treating investigator or the dose will be administered at a treatment facility.

Group Type OTHER

coagulation factor VIIa [recombinant]-jncw

Intervention Type DRUG

a transgenically produced, activated, recombinant, human factor VII (rhFVIIa) protein with the brand name of SEVENFACT®. This protein is a clotting factor in the coagulation cascade that is produced in and purified from the milk of transgenic rabbits. SEVENFACT is approved for the treatment and control of bleeding episodes occurring in adults and adolescents (12 years of age and older) with hemophilia A or B with inhibitors.

Interventions

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coagulation factor VIIa [recombinant]-jncw

a transgenically produced, activated, recombinant, human factor VII (rhFVIIa) protein with the brand name of SEVENFACT®. This protein is a clotting factor in the coagulation cascade that is produced in and purified from the milk of transgenic rabbits. SEVENFACT is approved for the treatment and control of bleeding episodes occurring in adults and adolescents (12 years of age and older) with hemophilia A or B with inhibitors.

Intervention Type DRUG

Other Intervention Names

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SEVENFACT

Eligibility Criteria

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Inclusion Criteria

1. Have a diagnosis of hemophilia A or B with inhibitors.
2. Be 12 years of age and older
3. Be capable of understanding and willing to comply with the conditions of the protocol or have a legal guardian who is capable of understanding and complying with the conditions of the protocol
4. Have read, understood, and documented written informed consent/assent
5. Be able to provide medical evidence through prior medical history of previous inhibitor levels
6. Be willing and able to use the ATHN mobile application or a paper diary to document BEs and medication usage

Exclusion Criteria

1. Have a disorder of hemostasis in addition to Hemophilia A or B
2. Have a known or suspected intolerance or hypersensitivity to SEVENFACT® or its ingredients
3. Have a known allergy or hypersensitivity to rabbits or rabbit proteins
4. Are receiving prophylactic treatment for bleeding with a drug or biologic that is not approved for this use by the FDA
5. Have had implantation of an investigational medical device within the prior 6 months
6. Have received an investigational drug within 30 days of the baseline visit
7. Have an elective surgical procedure planned during the duration of their participation in the study\*
8. Have any life-threatening disease, or other disease or condition which, in the investigator's judgment, could pose a potential hazard to the patient or interfere with study participation or study outcome (e.g., a history of non responsiveness to bypassing products or thromboembolic disease)

* Should a participant require an unplanned surgery, the participant will not be withdrawn from the study unless the investigator deems it necessary. Instead, the participant will receive standard of care treatment as determined by the attending physician. If the participant is not withdrawn from the study, the participant's participation in the study will be paused until the investigator feels it is safe for them to continue.
Minimum Eligible Age

12 Years

Maximum Eligible Age

100 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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LFB USA, Inc.

INDUSTRY

Sponsor Role collaborator

American Thrombosis and Hemostasis Network

NETWORK

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Tammuella Chrisentery-Singleton, MD

Role: PRINCIPAL_INVESTIGATOR

American Thrombosis and Hemostasis Network

Mark Reding, MD

Role: PRINCIPAL_INVESTIGATOR

University of Minnesota

Locations

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Arizona Hemophilia and Thrombosis Center at Phoenix Children's Hospital

Phoenix, Arizona, United States

Site Status COMPLETED

Arkansas Center for Bleeding Disorders

Little Rock, Arkansas, United States

Site Status RECRUITING

Orthopaedic Institute for Children

Los Angeles, California, United States

Site Status RECRUITING

University of California at Davis UC Davis Hemostasis and Thrombosis Center

Sacramento, California, United States

Site Status RECRUITING

Children's National Hemophilia Center

Washington D.C., District of Columbia, United States

Site Status COMPLETED

Arnold Palmer Hospital for Children - The Haley Center for Children's Cancer and Blood Disorders

Orlando, Florida, United States

Site Status COMPLETED

Hemophilia of Georgia Center for Bleeding and Clotting Disorders of Emory, Adult Division

Atlanta, Georgia, United States

Site Status RECRUITING

Willett Children's Hospital at Memorial University Medical Center

Savannah, Georgia, United States

Site Status RECRUITING

Massachusetts General Hospital Comprehensive Hemophilia and Thrombosis Treatment Center

Boston, Massachusetts, United States

Site Status RECRUITING

Children's Hospital of Michigan

Detroit, Michigan, United States

Site Status RECRUITING

Henry Ford Health System

Detroit, Michigan, United States

Site Status RECRUITING

MSU Center for Bleeding and Clotting Disorders

Lansing, Michigan, United States

Site Status RECRUITING

Center for Bleeding and Clotting Disorders, University of Minnesota

Minneapolis, Minnesota, United States

Site Status NOT_YET_RECRUITING

Mayo Comprehensive Hemophilia Center

Rochester, Minnesota, United States

Site Status COMPLETED

Kansas City Regional Hemophilia Center

Kansas City, Missouri, United States

Site Status RECRUITING

Northwell Health, Long Island Jewish

New Hyde Park, New York, United States

Site Status RECRUITING

Brody School of Medicine at East Carolina University

Greenville, North Carolina, United States

Site Status NOT_YET_RECRUITING

University Hospitals Health System Cleveland

Cleveland, Ohio, United States

Site Status RECRUITING

Oklahoma Center for Bleeding and Clotting Disorders

Oklahoma City, Oklahoma, United States

Site Status RECRUITING

Vanderbilt University Medical Center

Nashville, Tennessee, United States

Site Status RECRUITING

Gulf States Hemophilia and Thrombophilia Center-University of Texas Health Science Center @Houston

Houston, Texas, United States

Site Status RECRUITING

Countries

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United States

Central Contacts

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Carol Fedor, ND, RN, CCRC

Role: CONTACT

(800)-360-2846 ext. 122

Jessica Callis

Role: CONTACT

800-360-2846 ext. 123

Facility Contacts

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Carol Pierce, RN

Role: primary

501-364-1076

Doris Quon, MD

Role: primary

Celynn Knight

Role: primary

Megan Brown, MD

Role: primary

Alta Castellano, RN

Role: primary

Carmen Zhou

Role: primary

617-726-2737

Meera Chitlur, MD

Role: primary

Philip Kuriakose, MD

Role: primary

Anna Burghardt

Role: primary

Mark Reding, MD

Role: primary

Eryn Bilynsky

Role: primary

816-302-6853

Suchitra Acharya, MD

Role: primary

Darla Liles

Role: primary

Julia Martiradonna

Role: primary

216-844-3329

Osman Khan, MD

Role: primary

Alyssa Weakley

Role: primary

Miguel Escobar, MD

Role: primary

Other Identifiers

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ATHN 16

Identifier Type: -

Identifier Source: org_study_id

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