Lymphatic Morphology of Fontan Patients

NCT ID: NCT04163653

Last Updated: 2023-06-18

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Total Enrollment

41 participants

Study Classification

OBSERVATIONAL

Study Start Date

2018-01-01

Study Completion Date

2022-01-01

Brief Summary

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The Fontan procedure has revolutionized the treatment of patients born with a congenital univentricular heart defect. However, over time, it is associated with severe lymphatic complications such as plastic bronchitis, protein-losing enteropathy (PLE) and peripheral edema.

The hypothesis is that patients with a univentricular circulation have a changed morphology which may be associated with both the degree of lymphatic complications and their physical capacity.

The morphology will be described using T2-weighted non-contrast MRI.

Detailed Description

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The Fontan procedure has revolutionized the treatment of patients born with a congenital univentricular heart defect. However, over time, it is associated with severe lymphatic complications such as plastic bronchitis, protein-losing enteropathy (PLE) and peripheral edema. It has been proposed that these complications arise due to a elevated central venous pressure of the changed circulation.

The hypothesis of the study is that patients with a univentricular circulation have a changed morphology which may be associated with both the degree of lymphatic complications and their physical capacity.

The morphology will be described using T2-weighted non-contrast MRI. The main lymphatic vessel, the thoracic duct, will be rendered and measured using 3D software, and the lymphatic changes characterized by Dr. Yoav Dori (CHOP, Pennsylvania, USA), using a newly published grading system. The above will be correlated with the amount of complications experienced by the patients, and their physical capacity measured by both IPAQ questionaire and CPX test.

The study population consists of patients with a Fontan circulation operated at InCor Heart Institute, São Paulo, Brasil and Hospital das Clínicas, Ribeirão Preto, Brasil. Exclusion criteria were mental illness, genetic syndromes and age \<18 years. The patient group will be compared with age, gender and weight matched healthy controls.

Conditions

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Lymphatic Abnormality Plastic Bronchitis Protein-Losing Enteropathies Univentricular Heart Congenital Heart Disease

Study Design

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Observational Model Type

CASE_CONTROL

Study Time Perspective

CROSS_SECTIONAL

Study Groups

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Fontan Group

Fontan patients operated at the two centres between 1991 and 2014.

Non-contrast MRI

Intervention Type DIAGNOSTIC_TEST

Classification and characterization of the lymphatic vasculature using non-contrast MRI.

Cardiopulmonary exercise test

Intervention Type DIAGNOSTIC_TEST

Cardiopulmonary exercise test, measurement of VO2 and heart rate.

Healthy Control Group

Age, gender and weight matched healthy controls.

Non-contrast MRI

Intervention Type DIAGNOSTIC_TEST

Classification and characterization of the lymphatic vasculature using non-contrast MRI.

Cardiopulmonary exercise test

Intervention Type DIAGNOSTIC_TEST

Cardiopulmonary exercise test, measurement of VO2 and heart rate.

Interventions

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Non-contrast MRI

Classification and characterization of the lymphatic vasculature using non-contrast MRI.

Intervention Type DIAGNOSTIC_TEST

Cardiopulmonary exercise test

Cardiopulmonary exercise test, measurement of VO2 and heart rate.

Intervention Type DIAGNOSTIC_TEST

Eligibility Criteria

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Inclusion Criteria

\- Fontan Circulation

Exclusion Criteria

* Age \<18 years
* Mental illness
* Genetic syndromes
Minimum Eligible Age

18 Years

Maximum Eligible Age

100 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

Yes

Sponsors

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InCor Heart Institute

OTHER

Sponsor Role collaborator

Hospital das Clínicas de Ribeirão Preto

OTHER

Sponsor Role collaborator

University of Aarhus

OTHER

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Department of Cardiothoracic and Vascular Surgery

Aarhus N, , Denmark

Site Status

Countries

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Denmark

Other Identifiers

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BRALYMF

Identifier Type: -

Identifier Source: org_study_id

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