Osteofibrous Dysplasia (Kempson-Campanacci's Disease)

NCT ID: NCT04104763

Last Updated: 2022-08-23

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Total Enrollment

50 participants

Study Classification

OBSERVATIONAL

Study Start Date

2019-08-08

Study Completion Date

2021-09-30

Brief Summary

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The aim of the present study is to obtain long term follow-up in patients with osteofibrous dysplasia, to assess natural history of the disease, late results of treatment and in particular the potential and risk of progression to adamantinoma.

Detailed Description

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Conditions

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Osteofibrous Dysplasia

Study Design

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Observational Model Type

CASE_ONLY

Study Time Perspective

RETROSPECTIVE

Interventions

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study of osteofibrous dysplasia features

obtain long term follow-up in patients with osteofibrous dysplasia, to assess natural history of the disease, late results of treatment and in particular the potential and risk of progression to adamantinoma.

Intervention Type BEHAVIORAL

Eligibility Criteria

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Inclusion Criteria

* Male and female patients treated at Rizzoli Institute from 01 Jan 1943 to 31 Dic 2011
* Diagnosis of osteofibrous dysplasia pathologically confirmed
* Written informed consent prior to any study-specific analysis and/or data collection

Exclusion Criteria

* Patients with histological diagnosis different from osteofibrous dysplasia
Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Istituto Ortopedico Rizzoli

OTHER

Sponsor Role lead

Responsible Party

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Alberto Righi

Principal Investigator

Responsibility Role PRINCIPAL_INVESTIGATOR

Locations

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Dept. of Pathology of IRCCS Istituto Ortopedico Rizzoli

Bologna, , Italy

Site Status

Countries

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Italy

References

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Benassi MS, Campanacci L, Gamberi G, Ferrari C, Picci P, Sangiorgi L, Campanacci M. Cytokeratin expression and distribution in adamantinoma of the long bones and osteofibrous dysplasia of tibia and fibula. An immunohistochemical study correlated to histogenesis. Histopathology. 1994 Jul;25(1):71-6. doi: 10.1111/j.1365-2559.1994.tb00600.x.

Reference Type RESULT
PMID: 7525449 (View on PubMed)

Scholfield DW, Sadozai Z, Ghali C, Sumathi V, Douis H, Gaston L, Grimer RJ, Jeys L. Does osteofibrous dysplasia progress to adamantinoma and how should they be treated? Bone Joint J. 2017 Mar;99-B(3):409-416. doi: 10.1302/0301-620X.99B3.38050.

Reference Type RESULT
PMID: 28249983 (View on PubMed)

Gleason BC, Liegl-Atzwanger B, Kozakewich HP, Connolly S, Gebhardt MC, Fletcher JA, Perez-Atayde AR. Osteofibrous dysplasia and adamantinoma in children and adolescents: a clinicopathologic reappraisal. Am J Surg Pathol. 2008 Mar;32(3):363-76. doi: 10.1097/PAS.0b013e318150d53e.

Reference Type RESULT
PMID: 18300815 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Other Identifiers

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9261_2019

Identifier Type: -

Identifier Source: org_study_id

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