A Study of SGT-212 Gene Therapy in Friedreich's Ataxia

NCT ID: NCT07180355

Last Updated: 2026-01-22

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

RECRUITING

Clinical Phase

PHASE1

Total Enrollment

10 participants

Study Classification

INTERVENTIONAL

Study Start Date

2025-10-22

Study Completion Date

2032-02-29

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

This is a phase 1b, first in-human, open-label, dose-finding study investigating the safety and tolerability of SGT-212 in participants with Friedreich's ataxia (FA). It will be delivered via dual intradentate nucleus (IDN) and intravenous (IV) administration to participants with FA.

All participants will receive SGT-212 and will be enrolled in the study for approximately 5 years.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Friedreich's Ataxia (FA)

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

NON_RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Cohort 1 (Non-Ambulatory)

Non-ambulatory participants will receive bilateral intradentate infusion (IDN) followed by systemic intravenous (IV) infusion.

Group Type EXPERIMENTAL

SGT-212

Intervention Type DRUG

Adeno-associated virus serotype AAVhu68 containing a codon-optimized complementary DNA (cDNA)

Cohort 2 (Ambulatory)

Ambulatory participants will receive bilateral IDN infusion followed by systemic IV infusion.

Group Type EXPERIMENTAL

SGT-212

Intervention Type DRUG

Adeno-associated virus serotype AAVhu68 containing a codon-optimized complementary DNA (cDNA)

Cohort 3 (Ambulatory and Non-Ambulatory)

Participants will receive bilateral IDN followed by systemic IV infusion.

Group Type EXPERIMENTAL

SGT-212

Intervention Type DRUG

Adeno-associated virus serotype AAVhu68 containing a codon-optimized complementary DNA (cDNA)

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

SGT-212

Adeno-associated virus serotype AAVhu68 containing a codon-optimized complementary DNA (cDNA)

Intervention Type DRUG

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

* Has history of FA symptom onset ≤25 years of age
* Has a clinical and genetic diagnosis of FA
* Has a staging score of ≥1 but \<6 on the Friedreich's Ataxia Rating Scale (FARS) Functional Disability Staging Score
* Is willing to agree to the following rules for use of omaveloxolone (Skyclarys):

1. For a candidate who is currently taking omaveloxolone, has been on a stable dose for 12 weeks, expects to continue taking omaveloxolone at that dose throughout the study, and is willing to stop taking omaveloxolone at the direction of the Investigator or Sponsor's Medical Monitor if evidence of transaminitis or synthetic liver dysfunction is detected during the study
2. For a candidate who is not actively taking omaveloxolone, at least 12 weeks have passed since the last dose and the candidate agrees not to resume omaveloxolone during the 18-month period after SGT-212 infusion NOTE: The use of any other approved or investigational medicinal product for the treatment of FA should be discussed with the study team.

Exclusion Criteria

* Antibodies against adeno-associated virus serotype 9 (AAV9)
* Has a modified FARS (mFARS) score \<20
* Has a body weight ≤25 kilogram (kg) or has body mass index (BMI) ≥33 kg/m\^2
* Has a contraindication to endomyocardial biopsy (EMB) or cardiac catheterization
* Is unable to undergo cardiac and brain MRI with contrast, including hypersensitivity to gadolinium contrast agent, presence of a non-MRI-compatible cardiac pacemaker, presence of a non-MRI-compatible implantable cardiac defibrillator, or physical condition (e.g., contractures)
* Has uncontrolled diabetes as defined by a hemoglobin (Hb) A1c \>9%
* Has participated in recent interventional clinical studies or received any investigational therapy administered within 3 months or 5 half-lives (whichever is longer) prior to Screening
* Has received gene therapy at any time
* Has contraindications to receiving corticosteroids
* Has any contraindication to the surgical procedures involved with IDN infusion of SGT-212
* Has any known cardiac disease not related to FA including known obstructive coronary artery disease (CAD)
Minimum Eligible Age

18 Years

Maximum Eligible Age

40 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Solid Biosciences Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

The Ohio State University

Columbus, Ohio, United States

Site Status RECRUITING

The Children's Hospital of Philadelphia (CHOP)

Philadelphia, Pennsylvania, United States

Site Status NOT_YET_RECRUITING

Countries

Review the countries where the study has at least one active or historical site.

United States

Central Contacts

Reach out to these primary contacts for questions about participation or study logistics.

Solid Biosciences Clinical Trials

Role: CONTACT

+1617-337-4680

Facility Contacts

Find local site contact details for specific facilities participating in the trial.

OSU Gene Therapy Research Team

Role: primary

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

SGT-212-101

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

Idebenone to Treat Friedreich's Ataxia
NCT00229632 COMPLETED PHASE2
Methylprednisolone Treatment of Friedreich Ataxia
NCT02424435 COMPLETED EARLY_PHASE1