Safety and Efficacy of EPI-743 in Patients With Friedreich's Ataxia

NCT ID: NCT01728064

Last Updated: 2020-08-31

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

60 participants

Study Classification

INTERVENTIONAL

Study Start Date

2012-12-31

Study Completion Date

2016-02-29

Brief Summary

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The purpose of this study is to examine the effects of EPI-743 on visual function and neurologic function in patients with Friedreich's ataxia.

Detailed Description

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Conditions

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Friedreich's Ataxia

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Placebo

Placebo capsules three times daily

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Placebo capsules

EPI-743 400 mg

EPI-743 at a dose of 400 mg three times daily

Group Type ACTIVE_COMPARATOR

EPI-743 400 mg

Intervention Type DRUG

EPI-743 200 mg

EPI-743 at a dose of 200 mg three times daily

Group Type ACTIVE_COMPARATOR

EPI-743 200 mg

Intervention Type DRUG

Interventions

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Placebo

Placebo capsules

Intervention Type DRUG

EPI-743 400 mg

Intervention Type DRUG

EPI-743 200 mg

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

1. Diagnosis of genetically confirmed Friedreich's ataxia
2. Visual acuity at baseline more than 15 letters on EDTRS at four meters
3. FARS score of 20 to 90
4. Agreement to use contraception if within reproductive years (see specifics in section D1, page 21)
5. Hormone replacement therapy, if used, must remain stable for the duration of the study
6. Willingness and ability to comply with study procedures
7. Willingness and ability to arrive at study site day prior to evaluations
8. Abstention from use of dietary supplements and non-prescribed medications at least 30 days prior to initiation of treatment and for the duration of the study. This would specifically include idebenone, Coenzyme Q10 and vitamin E
9. Abstention from use of other investigative or non-approved drugs within 30 days of enrollment and for the duration of the study

Exclusion Criteria

1. Allergy to EPI-743 or sesame oil or nuts
2. Clinically significant bleeding condition or abnormal PT/PTT INR (INR \> two; PTT \> two-times normal)
3. Liver insufficiency with LFTs greater than three-times upper normal limit at screening
4. Renal insufficiency with creatinine \> 1.5 at screening
5. Fat malabsorption syndromes
6. Any other respiratory chain diseases of the mitochondria or inborn errors of metabolism
7. Any other ophthalmologic conditions
8. History of alcohol or drug abuse
9. Clinically significant cardiomyopathy with ejection fraction \< 40 percent at screening
10. Clinically significant arrhythmia within past two years requiring treatment
11. Anticoagulant therapy within 30 days of enrollment.
Minimum Eligible Age

18 Years

Maximum Eligible Age

45 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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PTC Therapeutics

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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University of California Los Angeles

Los Angeles, California, United States

Site Status

University of South Florida

Tampa, Florida, United States

Site Status

Childrens Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

Countries

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United States

Related Links

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http://edisonpharma.com

Edison Pharmaceuticals Web Site

Other Identifiers

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EPI2010-006

Identifier Type: -

Identifier Source: org_study_id

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