A First in Human Study of RT001 in Patients With Friedreich's Ataxia

NCT ID: NCT02445794

Last Updated: 2020-11-27

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE1/PHASE2

Total Enrollment

19 participants

Study Classification

INTERVENTIONAL

Study Start Date

2015-08-31

Study Completion Date

2016-07-31

Brief Summary

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The purpose of this study is to evaluate the safety, tolerability and pharmacokinetics of RT001 in patients with Friedreich's ataxia.

Detailed Description

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Study RT001-002 is a randomized, double-blind, controlled, ascending dose study to evaluate the safety, tolerability, pharmacokinetic, disease state, and exploratory endpoints in patients with Friedreich's ataxia after oral administration. The study includes 2 dose levels of RT001.

Conditions

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Friedreich's Ataxia

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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RT001, oral, 1.8 g/day

RT001, oral, 1.8 g QD for 28 days or matching comparator

Group Type EXPERIMENTAL

Low dose cohort

Intervention Type DRUG

RT001 is encapsulated di-deutero synthetic homologue of linoleic acid ethyl ester. Each capsule contains 900 mg of RT001.

High dose cohort

Intervention Type DRUG

RT001 comparator is encapsulated non-deuterated linoleic acid ethyl ester.

RT001, oral, 9 g/day

RT001, oral, 4.5 g BID for 28 days or matching comparator

Group Type EXPERIMENTAL

Low dose cohort

Intervention Type DRUG

RT001 is encapsulated di-deutero synthetic homologue of linoleic acid ethyl ester. Each capsule contains 900 mg of RT001.

High dose cohort

Intervention Type DRUG

RT001 comparator is encapsulated non-deuterated linoleic acid ethyl ester.

Interventions

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Low dose cohort

RT001 is encapsulated di-deutero synthetic homologue of linoleic acid ethyl ester. Each capsule contains 900 mg of RT001.

Intervention Type DRUG

High dose cohort

RT001 comparator is encapsulated non-deuterated linoleic acid ethyl ester.

Intervention Type DRUG

Other Intervention Names

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RT001 1.8 g/d (2 capsule per day) RT001 comparator 1.8 g/d (2 capsule per day) RT001 9.0 g/d (9 capsule per day) RT001 comparator 9.0 g/d (9 capsule per day)

Eligibility Criteria

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Inclusion Criteria

1. Male or female 18 to 50 years of age
2. Medical history consistent with the symptoms of FRDA at ≤ 25 years of age
3. Homozygous for GAA repeat expansions in the Frataxin gene in the affected range for FRDA
4. FARS-Neurological score of 20-90 points
5. Ambulatory (with or without assistive device) and capable of performing assessments/evaluations
6. Body Mass Index ≤ 29.9 kg/m2
7. Agrees to dietary restrictions and agrees to receive calls from a dietary coach
8. Signed the informed consent form prior to entry into the study
9. Agrees to spend the required number of overnight clinic days
10. Able to provide the necessary repeated blood samples

Exclusion Criteria

1. Received treatment with other experimental therapies within the last 30 days prior to the first dose
2. Known point mutation in the FXN gene
3. History of malignancies (other than basal cell carcinomas)
4. Impaired renal function at screening
5. Alanine transaminase (ALT) or aspartate transaminase (AST) laboratory values \> 2 x upper limit of normal (ULN) at screening
6. Known hepatitis B surface antigen (HBsAg)-positive, or known or suspected active hepatitis C infection, or is known to be human immunodeficiency virus (HIV) positive
7. Female who is breastfeeding or has a positive pregnancy test
8. Male participant or female participant of child bearing potential, who is sexually active and unwilling/unable to use a medically acceptable and effective double barrier birth control method throughout the study
9. Unwilling or unable to comply with the requirements of the protocol
10. Clinically significant cardiac abnormalities at screening that, in the opinion of the Investigator, would make the patient unsuitable for enrollment
11. Diabetes mellitus (Type 1 or 2)
12. Suicidal ideation as determined by the Columbia-Suicide Severity Rating Scale
13. History, within the last 2 years, of alcohol abuse, significant mental illness, or physical opioid dependence
14. Cannot adhere to the dietary guidance required to be followed by the protocol
15. Cannot take the medication due to impairment in swallowing capsules
Minimum Eligible Age

18 Years

Maximum Eligible Age

50 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Biojiva LLC

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Curtis Scribner, MD

Role: STUDY_DIRECTOR

Biojiva LLC

Theresa Zesiewicz, MD

Role: PRINCIPAL_INVESTIGATOR

USF Ataxia Research Center

Locations

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Collaborative Neuroscience Network, LLC

Long Beach, California, United States

Site Status

University of South Florida

Tampa, Florida, United States

Site Status

Countries

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United States

Other Identifiers

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RT001-002

Identifier Type: -

Identifier Source: org_study_id