An Open-label Phase I/II Study of JR-446 in Mucopolysaccharidosis Type IIIB

NCT ID: NCT06488924

Last Updated: 2025-09-02

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

10 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-11-05

Study Completion Date

2030-04-30

Brief Summary

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A Phase I/ II, open-label study, designed to evaluate the safety and explore efficacy of the study drug in development for the treatment of MPS IIIB patients.

Detailed Description

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Conditions

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Mucopolysaccharidosis III-B

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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JR-446

Group Type EXPERIMENTAL

JR-446

Intervention Type DRUG

IV infusion

Interventions

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JR-446

IV infusion

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Chronological age of \<18 years
* Confirmed diagnosis of MPS IIIB

Exclusion Criteria

* Prior experience to gene therapy or HSCT with successful engraftment
* Past use of another investigational drug or product in last 4 months or 5 half-lives (whichever is longer) before signing ICF
* Current participation in a clinical trial or past participation (within 30 days of enrolment into this study) in a study involving invasive procedures
* Past use of Genistein or Kineret (anakinra) within 4 months before signing ICF
* Serious drug allergy or hypersensitivity
* Contraindication for lumbar puncture or MRI
* History of bleeding disorder or current use of medications that, in the opinion of the investigator, place them at risk of bleeding following lumbar puncture

The above information is not intended to contain all considerations relevant to a patient's potential participation in this clinical trial.
Maximum Eligible Age

17 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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JCR Pharmaceuticals Co., Ltd.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Hiroshima University Hospital

Hiroshima, , Japan

Site Status RECRUITING

University of the Ryukyus Hospital

Okinawa, , Japan

Site Status RECRUITING

National Center for Child Health and Development

Tokyo, , Japan

Site Status RECRUITING

Countries

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Japan

Central Contacts

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JCR Pharmaceuticals Co., Ltd.

Role: CONTACT

+81-797-32-8582

Facility Contacts

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Satoshi Okada

Role: primary

+81-82-257-5555

Koichi Nakanishi

Role: primary

+81-98-895-3331

Yuichi Abe

Role: primary

+81-3-3416-0181

Other Identifiers

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JR-446-101

Identifier Type: -

Identifier Source: org_study_id

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