Study of ATX-01 in Participants With DM1

NCT ID: NCT06300307

Last Updated: 2026-01-21

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

56 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-10-15

Study Completion Date

2027-07-31

Brief Summary

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The goal of this clinical trial is to test ATX-01 in participants with myotonic dystrophy type 1 (DM1). The main question it aims to answer is if ATX-01 is safe and well tolerated. The trial will compare the safety and tolerability of ATX-01 and a matching placebo.

There will be a single-ascending dose part of the trial and a multiple-ascending dose part. In the single-ascending dose, participants will receive one dose of ATX-01 or placebo. In the multiple-ascending dose part, participants will receive three doses of ATX-01 or placebo.

ATX-01 is a novel anti-miR (synthetic single stranded oligonucleotide) that inhibits a microRNA called miR-23b.

Detailed Description

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Conditions

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Myotonic Dystrophy 1

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

TRIPLE

Participants Investigators Outcome Assessors

Study Groups

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ATX-01

ATX-01 is a formulation of the anti-microRNA 23b (anti-miR-23b), known as X82108, a novel type of antisense oligonucleotide

Group Type EXPERIMENTAL

ATX-01

Intervention Type DRUG

Solution for infusion

Placebo

Placebo to ATX-01

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Solution for infusion

Interventions

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ATX-01

Solution for infusion

Intervention Type DRUG

Placebo

Solution for infusion

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Participants with a documented clinical diagnosis of DM1 (CTG expansion of \>150 repeats in DMPK gene measured in peripheral blood mononuclear cells)
* Ambulatory, defined as able to complete a 10-meter walk/run test at screening without the use of assistive devices such as canes, walkers, or orthoses, except for ankle-foot orthoses
* Presence for \>3 seconds of grip myotonia as confirmed by a central reader

Exclusion Criteria

* Participants with congenital DM1
* Medical Research Council Muscle Scale score of less than 4 on ankle dorsiflexion or significant tibialis anterior atrophy that prevents a muscle biopsy
* Use of mexiletine or other agent for myotonia within 21 days or 5 half-lives, whichever is longer, prior to screening
Minimum Eligible Age

18 Years

Maximum Eligible Age

64 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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ARTHEx Biotech S.L.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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UCLA

Los Angeles, California, United States

Site Status RECRUITING

University of Florida

Gainesville, Florida, United States

Site Status RECRUITING

University of Kansas Medical Center, Department of Neurology

Fairway, Kansas, United States

Site Status RECRUITING

Virginia Commonwealth University

Richmond, Virginia, United States

Site Status RECRUITING

Centre Intégré Universitaire de Santé et Services Sociaux du Saguenay-Lac-St-Jean

Chicoutimi, Quebec, Canada

Site Status RECRUITING

Institute of Myology

Paris, , France

Site Status RECRUITING

The NeMO Clinical Center in Milan, Neurorehabilitation Unit, University of Milan

Milan, , Italy

Site Status RECRUITING

Fondazione Policlinico A. Gemelli- IRCCS

Rome, , Italy

Site Status RECRUITING

Radboudumc

Nijmegen, , Netherlands

Site Status RECRUITING

Hospital Universitario Donostia

Donostia / San Sebastian, , Spain

Site Status RECRUITING

St. George's University Hospital

London, , United Kingdom

Site Status RECRUITING

Countries

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United States Canada France Italy Netherlands Spain United Kingdom

Central Contacts

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Project Manager

Role: CONTACT

+34676229821

Facility Contacts

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Michael Yan

Role: primary

310-825-3264

Cami Swartz

Role: primary

Cassidy Nelson

Role: primary

913-588-3653

Jodie Howell

Role: primary

804-828-6110

Sabrina Côté

Role: primary

418-541-1000 ext. 3065

Study Co-ordinator

Role: primary

Clinical Research Co-ordinator

Role: primary

Professor

Role: primary

Spierziekten Research Team Radboudumc

Role: primary

Ioana Croitoru

Role: primary

Joana Teixeira

Role: primary

Other Identifiers

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CT-ATX-01-DM1-1.1

Identifier Type: -

Identifier Source: org_study_id

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