A Study to Assess Safety, Tolerability and Efficacy of Garetosmab Versus Placebo Administered Intravenously (IV) in Adult Participants With Fibrodysplasia Ossificans Progressiva (FOP)

NCT ID: NCT05394116

Last Updated: 2026-01-16

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

63 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-11-21

Study Completion Date

2029-02-27

Brief Summary

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This study is researching an experimental drug called garetosmab. The study is focused on adult patients with fibrodysplasia ossificans progressiva (FOP).

The aim of the study is to see how safe and effective the study drug is in patients with FOP.

The study is looking at several other research questions, including:

* What side effects may happen from receiving the study drug
* How much study drug is in the blood at different times
* Whether the body makes antibodies against the study drug (which could make the drug less effective or could lead to side effects)

Detailed Description

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Conditions

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Fibrodysplasia Ossificans Progressiva

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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High dose Garetosmab

Garetosmab is administered by intravenous (IV) administration every 4 weeks (Q4W)

Group Type EXPERIMENTAL

Garetosmab

Intervention Type DRUG

Garetosmab is supplied as a liquid drug product and will be administered IV.

Low dose Garetosmab

Garetosmab is administered by IV administration Q4W

Group Type EXPERIMENTAL

Garetosmab

Intervention Type DRUG

Garetosmab is supplied as a liquid drug product and will be administered IV.

Placebo

Placebo to match garetosmab, is supplied as a liquid solution without the monoclonal antibody (or the protein) and is administered IV Q4W.

Group Type EXPERIMENTAL

Placebo

Intervention Type DRUG

Placebo to match garetosmab, is supplied as a liquid solution without the monoclonal antibody (or the protein) and is administered IV.

Interventions

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Garetosmab

Garetosmab is supplied as a liquid drug product and will be administered IV.

Intervention Type DRUG

Placebo

Placebo to match garetosmab, is supplied as a liquid solution without the monoclonal antibody (or the protein) and is administered IV.

Intervention Type DRUG

Other Intervention Names

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REGN2477

Eligibility Criteria

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Inclusion Criteria

1. Clinical diagnosis of Fibrodysplasia Ossificans Progressiva (FOP) \[(based on findings of congenital malformation of the great toes, episodic soft tissue swelling, and/or progressive Heterotopic Ossification (HO)\]
2. Confirmation of FOP diagnosis with documentation of Type I activin A receptor (ACVR1) FOP causing mutation
3. FOP disease activity within 1 year of screening visit. FOP disease activity is defined as pain, swelling, stiffness, or other signs and symptoms associated with FOP flare-ups; or worsening of joint function, or radiographic progression of HO lesions (increase in size or number of HO lesions) with/without being associated with flare-up episodes
4. Willing and able to undergo CT imaging procedures and other procedures as defined in the protocol

Exclusion Criteria

1. Cumulative Analog Joint Involvement Scale (CAJIS) score at screening \>19
2. Participant has significant concomitant illness or history of significant illness such as but not limited to cardiac, renal, rheumatologic, neurologic, psychiatric, endocrine, metabolic, or lymphatic disease, that in the opinion of the study investigator might confound the results of the study or pose additional risk to the patient by their participation in the study
3. Previous history or diagnosis of cancer
4. Severely impaired renal function defined as estimated glomerular filtration rate \<30 milliliter per minute (mL/min) (/1.73 m\^2 calculated by the Modification of Diet in Renal Disease equation
5. Uncontrolled diabetes defined as hemoglobin A1C (HbA1c) \>9% at screening
6. History of poorly controlled hypertension, as defined by:

1. Systolic blood pressure ≥180 mm Hg or diastolic blood pressure ≥110 mm Hg at the screening visit
2. Systolic blood pressure of 160 mm Hg to 179 mm Hg or diastolic blood pressure of 100 mm Hg to 10\^9 mm Hg at the screening visit, AND a history of end-organ damage (including history of left-ventricular hypertrophy, heart failure, angina, myocardial infarction, stroke, transient ischemic attack, peripheral arterial disease, end-stage renal disease, and moderate-to-advanced retinopathy
7. Known history of cerebral vascular malformation
8. Cardiovascular conditions such as New York Heart Association class III or IV heart failure, cardiomyopathy, intermittent claudication, myocardial infarction, or acute coronary syndrome within 6 months prior to screening; symptomatic ventricular cardiac arrhythmia
9. History of severe respiratory compromise requiring oxygen, respiratory support (eg, bilevel positive airway pressure \[biPAP\] or continuous positive airway pressure \[CPAP\]), or a history of aspiration pneumonia requiring hospitalization
10. Prior use in the past year and concomitant use of bisphosphonates
11. Concurrent participation in another interventional clinical study or a non-interventional study with radiographic measures or invasive procedures (eg, collection of blood or tissue samples)
12. Treatment with another investigational drug, denosumab, imatinib or isotretinoin in the last 30 days or within 5 half-lives of the investigational drug, whichever is longer
13. Pregnant or breastfeeding women
14. Women of childbearing potential (WOCBP) who are unwilling to practice highly effective contraception, as defined in the protocol
15. Male patients with WOCBP partners who are not willing to use condoms with WOCBP partners to prevent potential fetal exposure, as defined in the protocol
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Regeneron Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Clinical Trial Management

Role: STUDY_DIRECTOR

Regeneron Pharmaceuticals

Locations

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University of California Los Angeles (UCLA) Medical Center

Los Angeles, California, United States

Site Status

Vanderbilt University Medical Center

Nashville, Tennessee, United States

Site Status

Royal North Shore Hospital

St Leonards, New South Wales, Australia

Site Status

Hospital Israelita Albert Einstein

São Paulo, , Brazil

Site Status

Universidad de Concepcion

Concepción, Bio Bio, Chile

Site Status

Tongji Hospital of Tongji University

Shanghai, , China

Site Status

Clinica Universidad de La Sabana

Chía, Cundinamarca, Colombia

Site Status

HUS Children and Adolescents Park Hospital Clinical Trial Unit

Helsinki, Stenbäckinkatu 11, Finland

Site Status

Hôpital Lapeyronie

Montpellier, , France

Site Status

Hopital Lariboisiere

Paris, , France

Site Status

Queen Mary Hospital

Hong Kong, , Hong Kong

Site Status

IRCCS Istituto Giannina Gaslini

Genoa, , Italy

Site Status

Nagoya University Hospital

Nagoya, Aichi-ken, Japan

Site Status

Oita University Hospital

Yufu, Oita Prefecture, Japan

Site Status

Kyushu University Hospital

Fukuoka, , Japan

Site Status

Hospital Kuala Lampur

Kuala Lumpur, , Malaysia

Site Status

Amsterdam University Medical Center

Amsterdam, North Holland, Netherlands

Site Status

Szpital Centrum Medyczne Medyk

Rzeszów, Podkarpackie Voivodeship, Poland

Site Status

University of Cape Town

Rondebosch, Cape Town, South Africa

Site Status

Seoul National University Hospital

Seoul, , South Korea

Site Status

Hospital Universitario Ramon y Cajal

Madrid, , Spain

Site Status

Royal National Orthropaedic Hospital NHS Trust

Middlesex, Greater London, United Kingdom

Site Status

Countries

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United States Australia Brazil Chile China Colombia Finland France Hong Kong Italy Japan Malaysia Netherlands Poland South Africa South Korea Spain United Kingdom

Other Identifiers

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2022-000880-40

Identifier Type: REGISTRY

Identifier Source: secondary_id

2023-508350-26-00

Identifier Type: REGISTRY

Identifier Source: secondary_id

R2477-FOP-2175

Identifier Type: -

Identifier Source: org_study_id

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