A Study to Evaluate the Effect of Venglustat Tablets on Neuropathic and Abdominal Pain in Male and Female Participants ≥16 Years of Age With Fabry Disease

NCT ID: NCT05206773

Last Updated: 2025-07-20

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

122 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-03-11

Study Completion Date

2027-01-04

Brief Summary

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This is a 12-month, parallel treatment, Phase 3, double-blind, randomized, placebo-controlled study to evaluate the effect of venglustat on neuropathic and abdominal pain symptoms of Fabry disease in participants ≥16 years of age with Fabry disease who are treatment-naïve or untreated for at least 6 months.

* Study visits will take place approximately every 3 months.
* The double-blind period will be followed by an open-label extension (OLE) during which participants who have completed the double-blind period will be treated with venglustat for an additional 12 months or until the Common Study End of Treatment Day (CSEOTD).

Detailed Description

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Double blind period: the total duration will be up to approximately of 14 months (1 month of screening 12 month of treatment period, and a possible follow-up period of 1 month if no participation in the open label extension period)

Open-label extension period: the total duration will be approximately of 46 months (12 month of OLE treatment, additional OLE treatment until a common study end of treatment date (CSEOTD, approximately 33 months), and 1 month of follow-up period)

Conditions

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Fabry Disease

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

DOUBLE

Participants Investigators
Participants enrolled in the open-label extension will be treated with venglustat only.

Study Groups

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Venglustat

Participant will receive venglustat dose once daily for 12 months

Group Type EXPERIMENTAL

Venglustat (GZ402671)

Intervention Type DRUG

Pharmaceutical form: Tablet Route of administration: Oral

Placebo

Participants will receive placebo once daily for 12 months

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Pharmaceutical form: Tablet Route of administration: Oral

Interventions

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Venglustat (GZ402671)

Pharmaceutical form: Tablet Route of administration: Oral

Intervention Type DRUG

Placebo

Pharmaceutical form: Tablet Route of administration: Oral

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Male and female adult patients 16 year of age or older, who have had a previously confirmed diagnosis of Fabry disease and a history of clinical symptoms of Fabry disease
* Patients who are treatment-naïve or without prior treatment with an approved or experimental therapy for Fabry disease within at least 6 months prior to screening.
* Average score of ≥3 (0=no symptom, 10=symptom as bad as you can imagine) on the participant-defined most-bothersome symptom (among neuropathic pain in upper extremities, neuropathic pain in lower extremities, or abdominal pain), as measured by the Fabry Disease Patient-Reported Outcome (FD-PRO) at screening.
* Contraception (with double contraception methods) for male and female participants; not pregnant or breastfeeding for female participants; no sperm donation for male participants.
* Weight ≥30 Kg
* A signed informed consent must be provided prior to any study-related procedures.

Exclusion Criteria

* Any manifestations of Fabry disease that preclude placebo administration.
* History of transient ischemic attack, stroke, myocardial infarction, heart failure, evidence of left ventricular hypertrophy and/or cardiac fibrosis, major cardiovascular surgery, or kidney transplantation.
* History of clinically significant cardiac arrhythmia. Atrial fibrillation that is well controlled on a stable medical regimen for at least 12 months is not an exclusion if the CHA2DS2-VASc score is 0 for males or 1 for females.
* Patients with hepatitis C, HIV, or hepatitis B infection.
* Neuropathic pain in upper or lower extremities, or abdominal pain not related to Fabry disease.
* History of seizures currently requiring treatment.
* Uncontrolled hypertension over the past 12 months prior to screening, or systolic BP \>=150 or diastolic BP \>=100 at screening.
* Estimated glomerular filtration rate \<60 mL/min/1.73m².
* Urine protein to creatinine ratio \>= 1 g/g at screening.
* Presence of severe depression as measured by Beck's Depression Inventory (BDI)-II \>28 and/or a history of an untreated, unstable major affective disorder within 1 year of the screening visit.
* Positive SARS-CoV-2 virus test within 2 weeks of enrollment, or COVID 19 requiring hospitalization within 6 months of enrollment.
* Moderate to severe hepatic impairment.
* History of drug and/or alcohol abuse.
* History of or active hepatobiliary disease.
* Liver enzymes (alanine aminotransferase (ALT)/aspartate aminotransferase (AST)) or total bilirubin \>2 times the upper limit of normal (ULN).
* Initiation of chronic treatment for pain, or change in pain medication regimen, within 3 months prior to randomization.
* Strong or moderate inducers or inhibitors of cytochrome P450 3A within 14 days or 5 half-lives, whichever is longer, prior to randomization.

The above information is not intended to contain all considerations relevant to a potential participation in a clinical trial.
Minimum Eligible Age

16 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Sanofi

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Clinical Sciences & Operations

Role: STUDY_DIRECTOR

Sanofi

Locations

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Nephrology Clinic at Kirklin Clinic of UAB Hospital_Investigational Site Number: 8400011

Birmingham, Alabama, United States

Site Status

UCLA Medical Center_Investigational Site Number: 8400006

Los Angeles, California, United States

Site Status

University of California Irvine Medical Center- Site Number : 8400019

Orange, California, United States

Site Status

Advent Health Orlando_Investigational Site Number: 8400008

Orlando, Florida, United States

Site Status

Emory Genetics- Site Number : 8400010

Atlanta, Georgia, United States

Site Status

Westchester Medical Center Healthcare Corporation- Site Number : 8400001

Hawthorne, New York, United States

Site Status

Cincinnati Children's Hospital Medical Center - PIN- Site Number : 8400013

Cincinnati, Ohio, United States

Site Status

Cleveland Clinic Site Number : 8400016

Cleveland, Ohio, United States

Site Status

Children's Hospital Of Pittsburgh- Site Number : 8400009

Pittsburgh, Pennsylvania, United States

Site Status

Renal Disease Research Institute, An affiliate of: Dallas Nephrology Associates_Investigational Site Number: 8400012

Dallas, Texas, United States

Site Status

University Of Utah Health Sciences Center- Site Number : 8400005

Salt Lake City, Utah, United States

Site Status

Lysosomal and Rare Disorders Research and Treatment Center_Investigational Site Number: 8400004

Fairfax, Virginia, United States

Site Status

Fundacion Cori para la Investigación y Prevención del Cancer_Investigational Site Number: 0320002

La Rioja, , Argentina

Site Status

Instituto de Investigaciones Clínicas Quilmes (IICQ) SRL_Investigational Site Number: 0320003

Quilmes, , Argentina

Site Status

Investigational Site Number : 0360001

Parkville, Victoria, Australia

Site Status

Investigational Site Number: 0400001

Vienna, , Austria

Site Status

Hospital de Clínicas de Porto Alegre_Investigational Site Number: 0760001

Porto Alegre, Rio Grande do Sul, Brazil

Site Status

Instituto de Genética e Erros Inatos do Metabolismo - IGEIM- Site Number : 0760002

São Paulo, , Brazil

Site Status

M.A.G.I.C Calgary LTD_Investigational Site Number: 1240003

Calgary, Alberta, Canada

Site Status

Medicine Dalhousie University_Investigational Site Number : 1240001

Halifax, Nova Scotia, Canada

Site Status

University Health Network_Investigational Site Number : 1240005

Toronto, Ontario, Canada

Site Status

No.8, Xishiku Street, Xicheng District_Site Number: 1560001

Beijing, , China

Site Status

No.197,2nd Ruijin road, Huangpu district_Site Number: 1560003

Shanghai, , China

Site Status

No.85 South Jiefang road, Yingze District_Site Number: 1560004

Taiyuan, , China

Site Status

Investigational Site Number : 1560006

Zhengzhou, , China

Site Status

Investigational Site Number: 2080001

Copenhagen, , Denmark

Site Status

Investigational Site Number: 2460001

Turku, , Finland

Site Status

Investigational Site Number : 2500001

Garches, , France

Site Status

ISphinCS GmbH_Investigational Site Number: 2760004

Hochheim am Main, , Germany

Site Status

Investigational Site Number : 2760005

Mainz, , Germany

Site Status

Investigational Site Number: 2760003

München, , Germany

Site Status

Investigational Site Number: 2760001

Würzburg, , Germany

Site Status

Investigational Site Number : 3000003

Athens, , Greece

Site Status

University Hospital of Heraklion_Investigational Site Number: 3000001

Heraklion, , Greece

Site Status

University Hospital of Ioannina_Investigational Site Number: 3000002

Ioannina, , Greece

Site Status

IRCCS Policlinico di Sant'Orsola_Investigational Site Number : 3800005

Bologna, , Italy

Site Status

Fondazione IRCCS San Gerardo dei Tintori, S.C. Nefrologia - Clinica Nefrologica_Investigational Site Number: 3800002

Monza, , Italy

Site Status

Azienda Ospedaliera Universitaria "Federico II", U.O. di Nefrologia- Diparimento di Sanità Pubblica_Investigational Site Number: 3800001

Napoli, , Italy

Site Status

Azienda Ospedaliera Universitaria_Investigational Site Number: 3800003

Palermo, , Italy

Site Status

Fondazione Policlinico Universitario_Investigational Site Number: 3800004

Roma, , Italy

Site Status

Investigational Site Number : 3920005

Kawasaki, Kanagawa, Japan

Site Status

Fukuoka University Hospital_Investigational Site Number: 3920004

Fukuoka-shi, Fukuoka, , Japan

Site Status

The Jikei University Hospital_Investigational Site Number: 3920003

Minato-ku, Tokyo, , Japan

Site Status

Tohoku University Hospital_Investigational Site Number: 3920001

Sendai-shi, Miyagi, , Japan

Site Status

Hospital Universitario "Dr. José Eleuterio González" Departamento de Genética Centro Universitario contra el cáncer_Investigational Site Number: 4840001

Monterrey, Nuevo León, Mexico

Site Status

Odette del Carmen DIAZ-AVENDAÑO Clinstile, S.A. de C.V. Durango_Investigational Site Number: 4840002

Mexico City, , Mexico

Site Status

Investigational Site Number: 5780001

Bergen, , Norway

Site Status

Investigational Site Number : 6160002

Poznan, Greater Poland Voivodeship, Poland

Site Status

Investigational Site Number : 6160004

Rzeszów, , Poland

Site Status

Investigational Site Number: 6160003

Wroclaw, , Poland

Site Status

Institutul Clinic Fundeni_Investigational Site Number: 6420001

Bucharest, , Romania

Site Status

Investigational Site Number : 7560001

Zurich, , Switzerland

Site Status

Investigational Site Number : 7920001

Ankara, , Turkey (Türkiye)

Site Status

Investigational Site Number : 7920002

İzmit, , Turkey (Türkiye)

Site Status

Investigational Site Number : 7920004

Malatya, , Turkey (Türkiye)

Site Status

Investigational Site Number: 8260001

Cambridge, Cambridgeshire, United Kingdom

Site Status

Investigational Site Number: 8260002

London, London, City of, United Kingdom

Site Status

Investigational Site Number : 8260003

Salford, Manchester, United Kingdom

Site Status

Countries

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United States Argentina Australia Austria Brazil Canada China Denmark Finland France Germany Greece Italy Japan Mexico Norway Poland Romania Switzerland Turkey (Türkiye) United Kingdom

Other Identifiers

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U1111-1256-9310

Identifier Type: REGISTRY

Identifier Source: secondary_id

2024-511990-31

Identifier Type: REGISTRY

Identifier Source: secondary_id

2021-002350-90

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

EFC17045

Identifier Type: -

Identifier Source: org_study_id

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