Swiss Pediatric Inflammatory Brain Disease Registry (Swiss-Ped-IBrainD)

NCT ID: NCT05017142

Last Updated: 2024-12-16

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Total Enrollment

500 participants

Study Classification

OBSERVATIONAL

Study Start Date

2020-04-14

Study Completion Date

2071-01-01

Brief Summary

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The Swiss-Ped-IBrainD is a national patient registry that collects information on diagnosis, symptoms, treatment, and follow-up of pediatric patients with an inflammatory brain disease in Switzerland. It was first implemented in 2020 in the pediatric clinic of the university hospital in Bern. Further centers all over Switzerland opened for recruitment after that: Aarau, Basel, Bellinzona, Chur, Geneva, Lausanne, Lucerne, St. Gallen, Winterthur and Zurich. The center in Fribourg is expected open for recruitment in 2025. The registry provides data for national and international monitoring and research. It supports research on inflammatory brain diseases in Switzerland and the exchange of knowledge between clinicians, researchers, and therapists. The registry aims to improve the treatment of children with inflammatory brain diseases and optimizing their health care and quality of life.

Detailed Description

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Background:

Pediatric onset MS and other inflammatory brain diseases (IBrainDs) are severe diseases affecting children and adolescents in a period of essential brain development. This possibly leads to a variety of focal neurological deficits as well as early cognitive impairment. In turn, the cognitive impairment may impact school performance and vocational achievements.

Timely diagnosis and treatment initiation as well as individually tailored management are important for a favorable disease course. However, the diagnosis of the different IBrainDs can be challenging, especially in young children, since their first acute inflammation is often accompanied by unspecific symptoms common to all IBrainDs. A systematic assessment of similarities and differences between clinical signs, symptoms, and diagnostic workup of different IBrainDs will enable faster and more reliable diagnosis.

Furthermore, neither epidemiological data nor information on health care management and disease outcome of pediatric IBrainD patients exist in Switzerland. Therefore, a national registry is being established, which will allow a deeper understanding of pediatric IBrainD epidemiology, clinical presentation, and management. Ultimately, the registry will improve the care of children suffering from an IBrainD in Switzerland.

The Swiss-Ped-IBrainD Registry (title: "Swiss Pediatric Inflammatory Brain Disease Cohort Study", project number: 2019-00377) has been approved by the ethics committees of Bern, the Ethikkommission Nordwest- und Zentralschweiz (EKNZ), the Ethikkommission Ostschweiz (EKOS), and the ethics committees of Zürich, Lausanne, Geneva, and Bellinzona.

Objectives:

The registry pursues the following goals:

1. Gathering representative, population-based epidemiological data on pediatric IBrainD in Switzerland.
2. Monitoring treatment, clinical course, education, social aspects, and outcomes of pediatric IBrainD patients.
3. Providing a platform to facilitate research, national and international collaboration and exchange of knowledge between experts.

The registry thus addresses the increasing requests for medical trial participation and promotes the exchange with existing adult registries (e.g., Swiss MS Registry).

Inclusion/exclusion criteria:

All patients living and/or treated in Switzerland with an IBrainD specified in the following list diagnosed from 2005 onward and with a disease onset before the age of 18.

* Optic neuritis
* Transverse myelitis
* Acute disseminated encephalomyelitis
* Multiple sclerosis
* Neuromyelitis optica spectrum disorders
* Myelin oligodendrocyte glycoprotein antibody-associated disease
* Anti-NMDA-R associated autoimmune encephalitis
* Anti-GAD65 associated autoimmune encephalitis
* Anti-AMPAR-1/2 associated autoimmune encephalitis
* Anti-Lgi-1 associated autoimmune encephalitis
* Anti-CASPR-2 associated autoimmune encephalitis
* Anti-GABAR-1/2 associated autoimmune encephalitis
* Onconeuronal antibody (Hu, Ri, Yo, Amphiphysin, CRMP-5, Ma-1, Ma-2, SOX-1) associated autoimmune encephalitis
* Hashimoto encephalopathy
* CNS vasculitis
* CNS sarcoidosis
* CNS Lupus
* Rasmussen's encephalitis

Excluded are patients with:

1. Neurological symptoms due to infectious diseases of the CNS
2. Genetic/metabolic causes of central demyelinating diseases
3. Neurological symptoms due to Guillain-Barré-Syndrome

Registration of Patients and Collection of Medical Data:

Pediatricians, pediatric neurologists, neurologists, specialists in rehabilitation, and primary care physicians at the participating centers are responsible to identify children with the listed IBrainDs during regular medical consultations. Upon identification, treating physicians inform patients and their parents orally and in writing about the Swiss-Ped-IBrainD. Patients (and their legal representatives if applicable) who want to participate must give their informed consent. Once a patient consents to participate, their medical data will be entered in the registry.

The diagnostic workup and treatment of patients continue as usual and are independent from participation; no examination will be carried out specifically for the Swiss-Ped-IBrainD.

Medical data is collected through the following sources:

* Medical records and reports
* Oral/written information from treating physician
* Oral/written information from patient/family
* Routine statistics and other medical registries
* Questionnaires for patients and families The data collection focuses on diagnostic, follow-up, and relapse variables.

Routine data and linkages:

Communities; Federal Statistical Office (e.g. the birth register, cause of death statistics, hospital statistics)

Current status:

Since 2020, the investigators have included 128 people diagnosed with an IBrainD.

Funding:

* Schweizerische Multiple Sklerose Gesellschaft
* PedNet Bern
* SwissPedRegistry, University of Bern
* Roche Pharma (Switzerland) Ltd
* Novartis Pharma Schweiz AG
* Biogen
* Sanofi
* Anna Mueller Grocholski-Stiftung
* Gottfried und Julia Bangerter-Rhyner Stiftung
* Fondation Johanna Dürmüller-Bol

Conditions

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Optic Neuritis Transverse Myelitis Acute Disseminated Encephalomyelitis Multiple Sclerosis Neuromyelitis Optica Spectrum Disorder Anti-NMDAR Encephalitis Anti-GAD65 Associated Autoimmune Encephalitis Anti-AMPAR-1/2 Associated Autoimmune Encephalitis Anti-Lgi-1 Associated Autoimmune Encephalitis Anti-CASPR-2 Associated Autoimmune Encephalitis Anti-GABAR-1/2 Associated Autoimmune Encephalitis Onconeuronal Antibody (Hu, Ri, Yo, Amphiphysin, CRMP-5, Ma-1, Ma-2, SOX-1) Associated Autoimmune Encephalitis Hashimoto Encephalitis CNS Vasculitis CNS Sarcoidosis CNS Lupus Rasmussen Encephalitis Myelin Oligodendrocyte Glycoprotein Antibody-Associated Disease (MOGAD)

Study Design

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Observational Model Type

COHORT

Study Time Perspective

OTHER

Study Groups

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Patient population

Children, adolescents and adults diagnosed with an IBrainD from 2005 onward and with disease onset before age 18, who are born, treated or living in Switzerland

No interventions assigned to this group

Eligibility Criteria

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Inclusion Criteria

All patients living and/or treated in Switzerland with an IBrainD specified in the following list diagnosed from 2005 onward and with a disease onset before the age of 18.

* Written informed consent by patients (and/or legal representative(s), if applicable)
* Optic Neuritis
* Transverse Myelitis
* Acute disseminated encephalomyelitis
* Multiple Sclerosis
* Neuromyelitis Optica Spectrum Disorders
* Myelin oligodendrocyte glycoprotein antibody-associated disease
* Anti-NMDA-R Encephalitis
* Anti-GAD65 Associated Autoimmune Encephalitis
* Anti-AMPAR-1/2 Associated Autoimmune Encephalitis
* Anti-Lgi-1 Associated Autoimmune Encephalitis
* Anti-CASPR-2 Associated Autoimmune Encephalitis
* Anti-GABAR-1/2 Associated Autoimmune Encephalitis
* Onconeuronal Antibody (Hu, Ri, Yo, Amphiphysin, CRMP-5, Ma-1, Ma-2, SOX-1) Associated Autoimmune Encephalitis
* Hashimoto Encephalopathy
* CNS Vasculitis
* CNS Sarcoidosis
* CNS Lupus
* Rasmussen Encephalitis

Exclusion Criteria

* Neurological symptoms due to infectious diseases of the CNS
* Genetic/metabolic causes of central demyelinating diseases
* Neurological symptoms due to Guillain-Barré-Syndrome
Maximum Eligible Age

36 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Schweizerische Multiple Sklerose Gesellschaft

OTHER

Sponsor Role collaborator

Insel Gruppe AG, University Hospital Bern

OTHER

Sponsor Role collaborator

Novartis

INDUSTRY

Sponsor Role collaborator

Anna Mueller Grocholski-Stiftung

UNKNOWN

Sponsor Role collaborator

Gottfried und Julia Bangerter- Rhyner-Stiftung, Basel

OTHER

Sponsor Role collaborator

Biogen

INDUSTRY

Sponsor Role collaborator

Roche Pharma (Switzerland) Ltd

UNKNOWN

Sponsor Role collaborator

Fondation Johanna Dürmüller-Bol

UNKNOWN

Sponsor Role collaborator

Kantonsspital Aarau

OTHER

Sponsor Role collaborator

University Children's Hospital Basel

OTHER

Sponsor Role collaborator

Ente Ospedaliero Cantonale, Bellinzona

OTHER

Sponsor Role collaborator

Kantonsspital Graubünden

OTHER

Sponsor Role collaborator

University Hospital, Geneva

OTHER

Sponsor Role collaborator

Centre Hospitalier Universitaire Vaudois

OTHER

Sponsor Role collaborator

Ostschweizer Kinderspital

OTHER

Sponsor Role collaborator

Kantonsspital Winterthur KSW

OTHER

Sponsor Role collaborator

Sanofi

INDUSTRY

Sponsor Role collaborator

Hôpital Fribourgeois

OTHER

Sponsor Role collaborator

University Children's Hospital, Zurich

OTHER

Sponsor Role collaborator

Luzerner Kantonsspital

OTHER

Sponsor Role collaborator

University of Bern

OTHER

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Sandra Bigi, PD MD

Role: PRINCIPAL_INVESTIGATOR

ISPM, University of Bern, Bern; Kinderspital Zentralschweiz, Luzern

Sandra Bigi, PD MD

Role: STUDY_DIRECTOR

ISPM, University of Bern, Bern Kinderspital Zentralschweiz, Luzern

Locations

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Kantonsspital Aarau

Aarau, Canton of Aargau, Switzerland

Site Status RECRUITING

Children's Hospital of Eastern Switzerland

Sankt Gallen, Canton of St. Gallen, Switzerland

Site Status RECRUITING

University Children's Hospital Lausanne (CHUV)

Lausanne, Canton of Vaud, Switzerland

Site Status RECRUITING

Kantonsspital Winterthur

Winterthur, Canton of Zurich, Switzerland

Site Status RECRUITING

Pediatric Institute of Southern Switzerland, Ospedale San Giovanni

Bellinzona, Canton Ticino, Switzerland

Site Status RECRUITING

Kantonsspital Graubünden

Chur, Kanton Graubünden, Switzerland

Site Status RECRUITING

University Children's Hospital Basel, UKBB

Basel, , Switzerland

Site Status RECRUITING

University Children's Hospital, Inselspital Bern

Bern, , Switzerland

Site Status RECRUITING

Institute of Social and Preventive Medicine, University of Bern

Bern, , Switzerland

Site Status RECRUITING

Hôpital Fribourgeois - Freiburger Spital

Fribourg, , Switzerland

Site Status NOT_YET_RECRUITING

University Hospitals of Geneva (HUG)

Geneva, , Switzerland

Site Status RECRUITING

Kinderspital Zentralschweiz

Lucerne, , Switzerland

Site Status RECRUITING

University Children's Hospital Zurich

Zurich, , Switzerland

Site Status RECRUITING

Countries

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Switzerland

Central Contacts

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Lorena F Hulliger, MSc

Role: CONTACT

Phone: +41316845678

Email: [email protected]

Facility Contacts

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Esmeralda Nava, Dr. med.

Role: primary

Oliver Maier, Dr. med.

Role: primary

Ingrid Beck

Role: backup

Stéphane Darteyre

Role: primary

Florian Bauder, Dr. med.

Role: primary

Barbara Goeggel Simonetti, PD Dr. med.

Role: primary

Susi Strozzi, Dr. med.

Role: primary

Patricia Dill, Dr. med.

Role: primary

Gabriela Oesch Nemeth, Dr. med.

Role: primary

Lorena F Hulliger

Role: primary

Mary Kurian, Dr. med.

Role: primary

Stéphanie Garcia-Tarodo, Dr. med.

Role: primary

Sandra Bigi

Role: primary

Annette Hackenberg, Dr. med.

Role: primary

Related Links

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http://www.swiss-ped-ibraind.ch

Website of the registry

Other Identifiers

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2019-00377

Identifier Type: -

Identifier Source: org_study_id