A Study to Evaluate Efficacy and Safety of an Investigational Drug Named Volixibat in Patients With Itching Caused by Primary Sclerosing Cholangitis (PSC)

NCT ID: NCT04663308

Last Updated: 2026-01-15

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE2

Total Enrollment

182 participants

Study Classification

INTERVENTIONAL

Study Start Date

2020-12-18

Study Completion Date

2027-04-30

Brief Summary

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The purpose of this clinical research study is to learn more about the use of the study medicine, volixibat, for the treatment of pruritus (itching) associated with Primary Sclerosing Cholangitis (PSC), and to assess the possible impact on the disease progression of PSC.

Detailed Description

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Conditions

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Primary Sclerosing Cholangitis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

DOUBLE

Participants Investigators

Study Groups

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Part 1 Arm 1: Volixibat 20mg

Participants randomized to this arm will receive volixibat 20mg twice daily.

Group Type EXPERIMENTAL

Volixibat

Intervention Type DRUG

Oral capsules, administered twice daily. Volixibat is an Ileal Bile Acid Transporter (IBAT) inhibitor.

Part 1 Arm 2: Volixibat 80mg

Participants randomized to this arm will receive volixibat 80mg twice daily.

Group Type EXPERIMENTAL

Volixibat

Intervention Type DRUG

Oral capsules, administered twice daily. Volixibat is an Ileal Bile Acid Transporter (IBAT) inhibitor.

Part 1 Arm 3: Placebo

Participants in this arm will receive capsules matched to the study drug minus the active volixibat substance, twice daily.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Capsules matched to study drug minus active substance

Part 2 Arm 1: Volixibat Selected Dose 20mg

Participants randomized to this arm will receive volixibat 20mg twice daily.

Group Type EXPERIMENTAL

Volixibat

Intervention Type DRUG

Oral capsules, administered twice daily. Volixibat is an Ileal Bile Acid Transporter (IBAT) inhibitor.

Part 2 Arm 2: Placebo

Participants in this arm will receive capsules matched to the study drug minus the active volixibat substance, twice daily.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Capsules matched to study drug minus active substance

Interventions

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Volixibat

Oral capsules, administered twice daily. Volixibat is an Ileal Bile Acid Transporter (IBAT) inhibitor.

Intervention Type DRUG

Placebo

Capsules matched to study drug minus active substance

Intervention Type DRUG

Other Intervention Names

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SHP626

Eligibility Criteria

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Inclusion Criteria

1. Provide freely signed informed consent and assent (as applicable) and be willing to comply with all study visits and requirements through end of study, including the follow-up period.
2. Subjects aged ≥12 years for eligible regions; otherwise ≥18 years
3. Confirmed diagnosis of large duct or small duct PSC based on American Association for the Study of Liver Disease (AASLD) guidelines.
4. Pruritus associated with PSC as assessed by Adult ItchRO.
5. Ursodeoxycholic acid (UDCA) and anti-pruritic medication use will be allowed if meeting additional criteria.
6. Concomitant Inflammatory Bowel Disease (IBD) is allowed if meeting additional criteria.

Exclusion Criteria

1. Pruritus associated with an etiology other than PSC
2. Evidence or clinical suspicion of decompensated cirrhosis, or a history of decompensation events
3. History of ileostomy or small bowel surgery/resection or other surgeries that may have disrupted the enterohepatic circulation
4. Evidence, history, or suspicion of other liver disease; PSC patients with AIH are not excluded.
5. Bile duct stent or percutaneous bile duct drain placement, or balloon dilatation procedure of a stricture within 12 weeks of Screening
6. Exceeding pre-defined biochemical values for alanine aminotransferase/aspartate aminotransferase (ALT/AST), estimated glomerular filtration rate (eGFR),serum creatinine (sCr), platelet count, international normalized ratio (INR) and total bilirubin
7. History of liver transplantation
Minimum Eligible Age

12 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Mirum Pharmaceuticals, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Southern California Research Center

Coronado, California, United States

Site Status

Cedars Sinai Medical Center

Los Angeles, California, United States

Site Status

University of California, Davis

Sacramento, California, United States

Site Status

California Pacific Medical Center Research Institute

San Francisco, California, United States

Site Status

University of Colorado - Anschutz Medical Campus

Aurora, Colorado, United States

Site Status

MedStar Georgetown University Hospital

Washington D.C., District of Columbia, United States

Site Status

Florida Research Institute

Lakewood Rch, Florida, United States

Site Status

University of Miami - Schiff Center for Liver Diseases

Miami, Florida, United States

Site Status

Tampa General Hospital

Tampa, Florida, United States

Site Status

Beth Israel Deaconess Medical Center

Boston, Massachusetts, United States

Site Status

Henry Ford Hospital

Detroit, Michigan, United States

Site Status

Mayo Clinic

Rochester, Minnesota, United States

Site Status

Southern Therapy and Advanced Research LLC

Jackson, Mississippi, United States

Site Status

Northwell Health

Manhasset, New York, United States

Site Status

New York University Langone Health

New York, New York, United States

Site Status

Weill Cornell Medical College

New York, New York, United States

Site Status

Columbia University Medical Center - Presbyterian Hospital and Vanderbilt Clinic

New York, New York, United States

Site Status

University of Rochester Medical Center - Strong Memorial Hospital

Rochester, New York, United States

Site Status

Duke Health - Duke University Medical Center

Durham, North Carolina, United States

Site Status

Science 37, Inc (Remote-homebased Telemedicine)

Morrisville, North Carolina, United States

Site Status

Cleveland Clinic

Cleveland, Ohio, United States

Site Status

Einstein Healthcare Network - Einstein Medical Center

Philadelphia, Pennsylvania, United States

Site Status

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, United States

Site Status

Galen Medical Group

Hixson, Tennessee, United States

Site Status

Vanderbilt University Medical Center

Nashville, Tennessee, United States

Site Status

The Liver Institute At Methodist Dallas Medical Center

Dallas, Texas, United States

Site Status

University of Texas Southwestern Medical Center

Dallas, Texas, United States

Site Status

Houston Methodist Hospital

Houston, Texas, United States

Site Status

Liver Associates of Texas

Houston, Texas, United States

Site Status

University of Utah Health Care

Salt Lake City, Utah, United States

Site Status

Bon Secours Liver Institution of Hampton Roads Mary Immaculate Hospital Office

Newport News, Virginia, United States

Site Status

Richmond Community Hospital LLC

Richmond, Virginia, United States

Site Status

University of Washington - Harborview Medical Center

Seattle, Washington, United States

Site Status

Liver Institute Northwest

Seattle, Washington, United States

Site Status

Hospital Italiano de Buenos Aires

Buenos Aires, , Argentina

Site Status

Glenny Corp S.A.

Ciudad Autónoma Buenos Aires, , Argentina

Site Status

Hospital El Cruce

San Juan Bautista, , Argentina

Site Status

Royal Adelaide Hospital

Adelaide, , Australia

Site Status

Northern Health

Epping, , Australia

Site Status

Liverpool Hospital

Liverpool, , Australia

Site Status

Austin Health

Melbourne, , Australia

Site Status

University of the Sunshine Coast

Sippy Downs, , Australia

Site Status

Cliniques Universitaires Saint-Luc

Brussels, , Belgium

Site Status

Universitair Ziekenhuis Antwerpen (UZA)

Ghent, , Belgium

Site Status

University Hospital Ghent

Ghent, , Belgium

Site Status

Hospital das Clinicas da UFMG

Belo Horizonte, , Brazil

Site Status

Hospital Das Clínicas Da Ufg

Goiânia, , Brazil

Site Status

Hospital de Clinicas de Porto Alegre

Porto Alegre, , Brazil

Site Status

Escola Bahiana de Medicina e Saude Publica

Salvador, , Brazil

Site Status

Hospital do Rim e Hipertensao

São Paulo, , Brazil

Site Status

University of Alberta

Edmonton, Alberta, Canada

Site Status

McMaster University Hospital

Hamilton, Ontario, Canada

Site Status

The Ottawa Hospital - General Campus

Ottawa, Ontario, Canada

Site Status

University Health Network - Toronto General Hospital

Toronto, Ontario, Canada

Site Status

University of Calgary

Calgary, , Canada

Site Status

London Health Sciences Centre University Hospital

London, , Canada

Site Status

McGill University Health Centre - Royal Victoria Hospital

Montreal, , Canada

Site Status

Centre Hospitalier Universitaire Grenoble Alpes (CHU Grenoble Alpes)

Grenoble, , France

Site Status

Centre Hospitalier Universitaire de Lille

Lille, , France

Site Status

APHP-Hôpital Saint Antoine

Paris, , France

Site Status

CHU Bordeaux - Haut Lévêque

Pessac, , France

Site Status

Hannover Medical School

Hanover, Lower Saxony, Germany

Site Status

Universitaetsklinikum Bonn

Bonn, Nordrhine-Westphalia, Germany

Site Status

Charité Universtitätsmedizin - Campus Virchow-Klinikum

Berlin, , Germany

Site Status

Universitaetsklinikum Erlangen

Erlangen, , Germany

Site Status

Universitätsklinikum Schleswig-Holstein - Campus Kiel

Kiel, , Germany

Site Status

Universitatsklinikum Leipzig

Leipzig, , Germany

Site Status

Otto-von-Guericke-Universitat Magdeburg

Magdeburg, , Germany

Site Status

University Hospital Tubingen Medical Clinic

Tübingen, , Germany

Site Status

St. Josefs-Hospital Wiesbaden

Wiesbaden, , Germany

Site Status

Hillel Yaffe Medical Center

Hadera, , Israel

Site Status

Rambam Medical Center

Haifa, , Israel

Site Status

Carmel Medical Center

Haifa, , Israel

Site Status

Shaare Zedek Medical Center

Jerusalem, , Israel

Site Status

Hadassah Medical Center - Ein Karem

Jerusalem, , Israel

Site Status

Galilee Medical Center

Nahariya, , Israel

Site Status

Rabin Medical Center

Petah Tikva, , Israel

Site Status

Sheba Medical Center

Ramat Gan, , Israel

Site Status

Tel Aviv Sourasky Medical Center

Tel Aviv, , Israel

Site Status

Azienda Ospedaliero-Universitaria di Bologna - Policlinico S. Orsola-Malpighi

Bologna, , Italy

Site Status

Fondazione IRCCS Ca Granda Ospedale Maggiore Policlinico

Milan, , Italy

Site Status

ASST Grande Ospedale Metropolitano Niguarda

Milan, , Italy

Site Status

Fondazione IRCCS San Gerardo dei Tintori

Monza, , Italy

Site Status

A.O.U. Federico II

Napoli, , Italy

Site Status

Azienda Ospedale Universita Padova

Padua, , Italy

Site Status

Amsterdam UMC - VU Medisch Centrum (VUmc)

Amsterdam, , Netherlands

Site Status

Universitair Medisch Centrum Groningen

Groningen, , Netherlands

Site Status

Radboud University Medical Centre (MC)

Nijmegen, , Netherlands

Site Status

Erasmus University Medical Center

Rotterdam, , Netherlands

Site Status

Hospital Clinic Barcelona

Barcelona, , Spain

Site Status

Hospital General Universitario Gregorio Maranon

Madrid, , Spain

Site Status

University Hospital Zurich

Zurich, , Switzerland

Site Status

Royal Free Hospital

London, Hampstead, United Kingdom

Site Status

John Radcliffe Hospital

Oxford, Headington, United Kingdom

Site Status

Royal Victoria Hospital

Belfast, , United Kingdom

Site Status

University Hospitals Birmingham NHS Foundation Trust - Wellcome Trust Birmingham Clinical Research Facility

Birmingham, , United Kingdom

Site Status

Cambridge University Hospitals NHS Foundation Trust - Addenbrooke's Hospital

Cambridge, , United Kingdom

Site Status

Lothian NHS Board

Edinburgh, , United Kingdom

Site Status

St James' University Hospital Leeds Teaching Hospitals NHS Trust

Leeds, , United Kingdom

Site Status

King's College Hospital NHS Foundation Trust

London, , United Kingdom

Site Status

The Newcastle upon Tyne Hospitals NHS Foundation Trust - Royal Victoria Infirmary

Newcastle upon Tyne, , United Kingdom

Site Status

Nottingham University Hospital NHS Trust

Nottingham, , United Kingdom

Site Status

University Hospital Southampton NHS Foundation Trust

Southampton, , United Kingdom

Site Status

Countries

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United States Argentina Australia Belgium Brazil Canada France Germany Israel Italy Netherlands Spain Switzerland United Kingdom

Other Identifiers

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2020-003027-41

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

2023-505764-11-00

Identifier Type: OTHER

Identifier Source: secondary_id

VLX-301

Identifier Type: -

Identifier Source: org_study_id

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