Study of Elafibranor in Patients With Primary Biliary Cholangitis (PBC)

NCT ID: NCT04526665

Last Updated: 2025-12-03

Study Results

Results available

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Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

161 participants

Study Classification

INTERVENTIONAL

Study Start Date

2020-09-24

Study Completion Date

2028-12-01

Brief Summary

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The participants of this study will have confirmed Primary Biliary Cholangitis (PBC) with inadequate response or intolerance to ursodeoxycholic acid (which is a medication used in the management and treatment of cholestatic liver disease).

PBC is a slowly progressive disease characterized by damage of the bile ducts in the liver, leading to a buildup of bile acids which causes further damage. The liver damage in PBC may lead to scarring (cirrhosis). PBC may also be associated with multiple symptoms. Many patients with PBC may require liver transplant or may die if the disease progresses and a liver transplant is not done.

The main aim of this study is to determine if elafibranor (the study drug) is better than placebo (a dummy treatment) at decreasing the levels of a specific blood test (alkaline phosphatase) that provides information about participant's disease. This study will also evaluate the safety of long-term treatment with elafibranor, as well as the impact on symptoms such as itchy skin (pruritus) and tiredness (fatigue).

This study has two main parts:

Part 1 will compare a daily dose of elafibranor to a daily dose of placebo and will last between a minimum of one year and a maximum of two years.

Part 2, all participants will receive elafibranor for a period of up to 5 years or until the total treatment duration (part 1 and part 2) reaches 6 years, whichever occurs first.

Detailed Description

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Conditions

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Primary Biliary Cirrhosis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

This is a double-blind (DB), randomized, placebo-controlled study followed by an open-label long term extension (LTE)
Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Elafibranor 80mg double-blind

Study participants will take 1 tablet per day orally before breakfast with a glass of water each morning

Group Type EXPERIMENTAL

Elafibranor 80mg

Intervention Type DRUG

Elafibranor 80mg daily

Placebo

Study participants will take 1 tablet per day orally before breakfast with a glass of water each morning

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Placebo daily

Elafibranor 80mg open label

Study participants will take 1 tablet per day orally before breakfast with a glass of water each morning

Group Type EXPERIMENTAL

Elafibranor 80mg

Intervention Type DRUG

Elafibranor 80mg daily

Interventions

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Elafibranor 80mg

Elafibranor 80mg daily

Intervention Type DRUG

Placebo

Placebo daily

Intervention Type DRUG

Other Intervention Names

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Iqirvo®

Eligibility Criteria

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Inclusion Criteria

* Males or females age of 18 to 75 years (inclusive)
* Definite or probable Primary biliary cholangitis (PBC) diagnosis
* Alkaline phosphatase (ALP) ≥ 1.67x upper limit of normal (ULN)
* Total bilirubin (TB) ≤ 2x ULN
* Ursodeoxycholic acid (UDCA) for at least 12 months (stable dose ≥ 3 months) prior to screening, or unable to tolerate UDCA treatment (no UDCA for ≥ 3 months) prior to screening (per country standard-of-care dosing)
* Must have PBC Worst Itch Numeric rating scale (NRS) collected prior to randomization
* Females participating in this study must be of non-child bearing potential or must be using highly efficient contraception for the full duration of the study and for 1 month after the last drug intake

Exclusion Criteria

* History or presence of other concomitant liver disease
* Clinically significant hepatic decompensation, including patients with complications of cirrhosis/portal hypertension
* Medical conditions that may cause non-hepatic increases in ALP (e.g., Paget's disease) or which may diminish life expectancy to \< 2 years, including known cancers
* Patient has a positive test for HIV Type 1 or 2 at screening, or patient is known to have tested positive for HIV
* Evidence of any other unstable or untreated clinically significant disease
* History of alcohol abuse
* For female patients: known pregnancy or lactating
* Use of fibrates and glitazones within 2 months prior to screening
* Use of Obeticholic acid (OCA), azathioprine, cyclosporine, methotrexate, mycophenolate, pentoxifylline, budesonide and other systemic corticosteroids (parenteral and oral chronic administration only); potentially hepatotoxic drugs
* (including α-methyl-dopa, sodium valproic acid isoniazid, or nitrofurantoin) within 3 months prior to screening
* Use of antibodies or immunotherapy directed against interleukins (ILs) or other cytokines or chemokines within 12 months prior to screening
* For patients with previous exposure to OCA, OCA should be discontinued 3 months prior to screening
* Patients who are currently participating in, plan to participate in, or have participated in an investigational drug study or medical device study containing active substance within 30 days or five half-lives, whichever is longer, prior to screening; for patients with previous exposure to seladelpar, seladelpar should be discontinued 3 months prior to screening
* Alanine aminotransferase (ALT) and/or Aspartate aminotransferase (AST) values \> 5 x ULN
* For patients with AT or TB\>ULN at SV1, variability of AT or TB \> 40% (see section 3.5.1)
* Albumin\<3.0 g/dl
* Severely advanced patients according to Rotterdam criteria (TB \> ULN and albumin \<LLN)
* INR \> 1.3 due to altered hepatic function
* CPK \> 2 x ULN
* Screening serum creatinine \> 1.5 mg/dl
* Significant renal disease, including nephritic syndrome, chronic kidney disease (defined as patients with markers of kidney failure damage or eGFR \< 60 mL/min/1.73 m\^2) calculated by Modification of diet in renal disease (MDRD)
* Platelet count \< 150 x 10\^3/μL
* AFP \> 20 ng/mL with 4-phase liver CT or MRI imaging suggesting presence of liver cancer
* Known hypersensitivity to the investigational product or to any of the formulation excipients of the elafibranor or placebo tablet Mental instability or incompetence, such that the validity of informed consent or ability to be compliant with the study is uncertain
Minimum Eligible Age

18 Years

Maximum Eligible Age

75 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Ipsen

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Ipsen Medical Director

Role: STUDY_DIRECTOR

Ipsen

Locations

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The Institute for Liver Health

Chandler, Arizona, United States

Site Status

Keck Medical Center of USC

Los Angeles, California, United States

Site Status

Ruane Clinical Research Group Inc.

Los Angeles, California, United States

Site Status

Cedars-Sinai Medical Center

Los Angeles, California, United States

Site Status

University of California, Davis Medical Center

Sacramento, California, United States

Site Status

California Pacific Medical Center - Sutter Pacific Medical Foundation

San Francisco, California, United States

Site Status

University of Colorado Denver and Hospital

Aurora, Colorado, United States

Site Status

South Denver Gastroenterology, P.C.

Englewood, Colorado, United States

Site Status

Yale School of Medicine, Digestive Diseases

New Haven, Connecticut, United States

Site Status

Encore Borland-Groover Clinical Research

Jacksonville, Florida, United States

Site Status

Schiff Center for Liver Diseases/University of Miami

Miami, Florida, United States

Site Status

Digestive Healthcare of Georgia

Atlanta, Georgia, United States

Site Status

University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status

Massachusetts General Hospital

Boston, Massachusetts, United States

Site Status

Beth Israel Deaconess Medical Center (BIDMC)

Boston, Massachusetts, United States

Site Status

Henry Ford Health System

Novi, Michigan, United States

Site Status

Saint Louis University

St Louis, Missouri, United States

Site Status

UPMC Center for Liver Diseases

New Hyde Park, New York, United States

Site Status

NYU Langone Health / NYU Grossman School of Medicine

New York, New York, United States

Site Status

Columbia University Medical Center - Center for Liver Disease and Transplantation

New York, New York, United States

Site Status

The New York-Presbyterian Hospital, David H. Koch Center

New York, New York, United States

Site Status

Duke University Medical Center

Durham, North Carolina, United States

Site Status

Carolinas Centre for Liver disease/ Atrium Health

Huntersville, North Carolina, United States

Site Status

Consultants for Clinical Research

Cincinnati, Ohio, United States

Site Status

University Hospitals Cleveland Medical Center

Cleveland, Ohio, United States

Site Status

The Ohio State University Wexner Medical Center

Columbus, Ohio, United States

Site Status

Investigational Drug Service Pharmacy Penn State Milton S. Hershey Medical Center

Hershey, Pennsylvania, United States

Site Status

Thomas Jefferson University

Philadelphia, Pennsylvania, United States

Site Status

Medical University of South Carolina- College of Medicine

Charleston, South Carolina, United States

Site Status

Vanderbilt Digestive Disease Center

Nashville, Tennessee, United States

Site Status

Texas Clinical Research Institute, LLC

Arlington, Texas, United States

Site Status

The Liver Institute at Methodist Dallas Medical Center

Dallas, Texas, United States

Site Status

Liver Center of Texas, PLLC

Dallas, Texas, United States

Site Status

The University of Texas Southwestern Medical Center-IDS Aston Pharmacy

Dallas, Texas, United States

Site Status

Texas Digestive Disease Consultants dba GI Alliance

Fort Worth, Texas, United States

Site Status

Liver Associates of Texas, P.A.

Houston, Texas, United States

Site Status

St. Luke's Health-Baylor St Luke's Medical center - Advanced Liver Therapies Research

Houston, Texas, United States

Site Status

American Research Corporation

San Antonio, Texas, United States

Site Status

Gastro health & Nutrition-Victoria

Victoria, Texas, United States

Site Status

Intermountain Medical Center - Transplant Services

Murray, Utah, United States

Site Status

University of Utah Hospital-Division of Gastroenterology, Hepatology, and Nutrition

Salt Lake City, Utah, United States

Site Status

University of Virginia Medical Center

Charlottesville, Virginia, United States

Site Status

Maryview Hospital Inc, Bon Secours Liver Institute of Hampton Roads

Newport News, Virginia, United States

Site Status

Richmond Community Hospital LLC, Bon Secours Liver Institute of Richmond

Richmond, Virginia, United States

Site Status

Virginia Commonwealth University Clinical Research Services Unit (CRSU)

Richmond, Virginia, United States

Site Status

Liver Institute Northwest

Seattle, Washington, United States

Site Status

Hospital Italiano de Buenos Aires

CABA, Buenos Aires, Argentina

Site Status

Hospital Alemán

Caba, Buenos Aires, Argentina

Site Status

Hospital Británico de Buenos Aires

CABA, Buenos Aires, Argentina

Site Status

Hospital Italiano de La Plata

La Plata, Buenos Aires, Argentina

Site Status

Hospital Espanol De Mendoza

Godoy Cruz, Mendoza Province, Argentina

Site Status

Hospital Provincial del Centenario

Rosario, Santa Fe Province, Argentina

Site Status

Hôpital Erasme

Brussels, , Belgium

Site Status

Antwerp University Hospital

Edegem, , Belgium

Site Status

Universitair Ziekenhuis Gent

Ghent, , Belgium

Site Status

University Hospital Leuven

Leuven, , Belgium

Site Status

Hospital de Clínicas de Porto Alegre

Porto Alegre, Rio Grande do Sul, Brazil

Site Status

Hospital das Clinicas da Faculdade de Medicina da Universidade de Sao Paulo-HCFMUSP

São Paulo, São Paulo, Brazil

Site Status

University of Calgary Liver Unit - Heritage Medical Research Clinic (HMRC)

Calgary, Alberta, Canada

Site Status

Gordon and Leslie Diamond Health Care Centre, Division of Gastroenterology

Vancouver, British Columbia, Canada

Site Status

Shared Health Inc.-Operating as Health Sciences Centre-John Buhler Research Centre

Winnipeg, Manitoba, Canada

Site Status

Centre de Recherche du Centre Hospitalier de l'Université de Montreal (CRCHUM)

Montreal, , Canada

Site Status

Hospital de La Serena

La Serena, Coquimbo Region, Chile

Site Status

Centro de Investigaciones Clinicas (CIC)

Viña del Mar, Región de Valparaíso, Chile

Site Status

Clínica Universidad de los Andes

Santiago, , Chile

Site Status

Hospital Clínico Universidad de Chile

Santiago, , Chile

Site Status

Centro de Investigacion Clinica Universidad Catolica CICUC

Santiago, , Chile

Site Status

CHU Amiens Picardie

Amiens, , France

Site Status

Hôpital Henri Mondor

Créteil, , France

Site Status

CHU Grenoble Alpes - Hôpital Albert Michallon

Grenoble, , France

Site Status

Centre Hospitalier Régional d'Orléans

Orléans, , France

Site Status

Hôpital Saint-Antoine

Paris, , France

Site Status

Hôpital Cochin

Paris, , France

Site Status

Hôpital Pitié-Salpétrière

Paris, , France

Site Status

Hôpital Haut Lévêque

Pessac, , France

Site Status

Hôpital Robert Debré - CHU de Reims

Reims, , France

Site Status

Hôpitaux Universitaires de Strasbourg - Hôpital de Hautepierre

Strasbourg, , France

Site Status

Gastro - Sudien

Berlin, , Germany

Site Status

Charite - Universitätsmedizin Berlin- CVK - Medizinische Klinik

Berlin, , Germany

Site Status

Universitätsklinikum Frankfurt

Frankfurt, , Germany

Site Status

Medizinische Hochschule Hannover

Hanover, , Germany

Site Status

Center for Gastroenterology and Hepatology (GHZ) Kiel

Kiel, , Germany

Site Status

EUGASTRO GmbH

Leipzig, , Germany

Site Status

Universitätsmedizin der Johannes Gutenberg-Universität Mainz

Mainz, , Germany

Site Status

Ospedale Civile di Baggiovara-Struttura Complessa di Medicina ad indririzzo Metabolico Nutrizionale

Modena, Località Baggiovara, Italy

Site Status

Azienda Ospedaliero-Universitaria di Bologna Policlinico S. Orsola-Malpighi

Bologna, , Italy

Site Status

Azienda Ospedaliera San Paolo, Dipartimento di Scienza della Salute, UO Medicina VI e Pathologia e Gastroenterologia

Milan, , Italy

Site Status

ASST Monza - Ospedale San Gerardo, Gastroenterologia

Monza, , Italy

Site Status

Azienda Ospedale- Università degli Studi di Padova UOC Gastroenterologia

Padua, , Italy

Site Status

Azienda Ospedaliera Universitaria Policlinico P. Giaccone, UOC di Gastroenterologia-Dip.Medicina Interna e Specialistica

Palermo, , Italy

Site Status

Tiervlei Trial Centre

Cape Town, Western Cape, South Africa

Site Status

Groote Schuur Hospital, University of Cape Town - Clinical Research Centre

Cape Town, Western Cap, South Africa

Site Status

Mediclinic Constantiaberg, North Suites

Cape Town, , South Africa

Site Status

Hospital Universitario Vall d'Hebron

Barcelona, , Spain

Site Status

Hospital Clinic de Barcelona

Barcelona, , Spain

Site Status

Hospital General Universitario Gregorio Marañón

Madrid, , Spain

Site Status

Hospital Universitario La Paz

Madrid, , Spain

Site Status

Hospital Universitario Puerta de Hierro -Madrid

Madrid, , Spain

Site Status

Complexo Hospitalario Universitario de Pontevedra

Pontevedra, , Spain

Site Status

Hospital Universitario Donostia

San Sebastián, , Spain

Site Status

Hospital Universitario Marqués de Valdecilla

Santander, , Spain

Site Status

Hospital Universitario Virgen del Rocio

Seville, , Spain

Site Status

Inselspital, Universitätsspital Bern Universitätsklinik für Viszerale chirurgie und Medizin Hepatologie

Bern, , Switzerland

Site Status

Fondazione Epatocentro Ticino

Lugano, , Switzerland

Site Status

Ege Universitesi Tip Fakultesi Hastanesi

Izmir, Bornova, Turkey (Türkiye)

Site Status

Marmara Universitesi Pendik Egitim ve Arastirma Hastanesi, Gastroentoloji Bilim Dali

Istanbul, Pendik, Turkey (Türkiye)

Site Status

Hacette Universitesi Hastenesi IC, Hastaliklari Anabilim Dali, Gastronenteroloji Bilim Dali, Mithapasa Cad. Hacettepe Mah.

Ankara, , Turkey (Türkiye)

Site Status

The Newcastle upon Tyne Hospitals NHS Foundation Trust-Freeman Hospital

Newcastle upon Tyne, Newcastle, United Kingdom

Site Status

Belfast Health and Social Care Trust-Royal Victoria Hospital

Belfast, , United Kingdom

Site Status

Frimley Health NHS Foundation Trust - Frimley Park Hospital

Camberley, , United Kingdom

Site Status

Cambridge University Hospitals NHS Foundation Trust - Addenbrookes Hospital

Cambridge, , United Kingdom

Site Status

Hull University Teaching Hospitals NHS Trust , Hull Royal Infirmary

Hull, , United Kingdom

Site Status

King's College Hospital. King's College NHS Foundation Trust

London, , United Kingdom

Site Status

Nottingham University Hospitals NHS Trust - Queen's Medical Centre (QMC)

Nottingham, , United Kingdom

Site Status

Plymouth Hospitals NHS Trust, Derriford Hospital

Plymouth, , United Kingdom

Site Status

Countries

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United States Argentina Belgium Brazil Canada Chile France Germany Italy South Africa Spain Switzerland Turkey (Türkiye) United Kingdom

References

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Kowdley KV, Bowlus CL, Levy C, Akarca US, Alvares-da-Silva MR, Andreone P, Arrese M, Corpechot C, Francque SM, Heneghan MA, Invernizzi P, Jones D, Kruger FC, Lawitz E, Mayo MJ, Shiffman ML, Swain MG, Valera JM, Vargas V, Vierling JM, Villamil A, Addy C, Dietrich J, Germain JM, Mazain S, Rafailovic D, Tadde B, Miller B, Shu J, Zein CO, Schattenberg JM; ELATIVE Study Investigators' Group; ELATIVE Study Investigators' Group. Efficacy and Safety of Elafibranor in Primary Biliary Cholangitis. N Engl J Med. 2024 Feb 29;390(9):795-805. doi: 10.1056/NEJMoa2306185. Epub 2023 Nov 13.

Reference Type DERIVED
PMID: 37962077 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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2019-004941-34

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

GFT505B-319-1

Identifier Type: -

Identifier Source: org_study_id

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