Study of rADAMTS-13 (SHP655) in the Treatment of Participants With Acquired Thrombotic Thrombocytopenic Purpura (aTTP)

NCT ID: NCT03922308

Last Updated: 2022-12-01

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

28 participants

Study Classification

INTERVENTIONAL

Study Start Date

2019-10-09

Study Completion Date

2021-08-05

Brief Summary

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The purpose of this study is to evaluate the pharmacokinetics, safety, and efficacy of rADAMTS-13 (SHP655) administered in addition to standard of care (SoC) treatment of acquired thrombotic thrombocytopenic purpura (aTTP) participants.

Detailed Description

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Conditions

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Acquired Thrombotic Thrombocytopenic Purpura (aTTP)

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

DOUBLE

Participants Investigators

Study Groups

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Standard of Care (SoC) + Placebo

Participants received SoC daily PEX followed by placebo immediately and 12 +/- 1 hours after completion of PEX until remission was achieved (up to approximately 6 months).

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type OTHER

Participants will receive injection of placebo matched to SHP655.

Standard of Care

Intervention Type OTHER

Participants will receive PEX as Standard of Care (SOC).

SoC + SHP655 + Placebo

Participants received SoC daily PEX and SHP655 40 +/- 4 international units per kilogram (IU/kg), IV injection, QD, immediately after PEX and placebo 12 +/- 1 hours after completion of PEX until remission was achieved (up to approximately 6 months).

Group Type EXPERIMENTAL

Placebo

Intervention Type OTHER

Participants will receive injection of placebo matched to SHP655.

SHP655

Intervention Type DRUG

Participants will receive injection of SHP655.

Standard of Care

Intervention Type OTHER

Participants will receive PEX as Standard of Care (SOC).

SoC + SHP655

Participants received SoC daily PEX and SHP655 40 +/- 4 IU/kg, IV injection, BID, immediately after PEX and 12 +/- 1 hours after completion of PEX until remission was achieved (up to approximately 6 months).

Group Type EXPERIMENTAL

SHP655

Intervention Type DRUG

Participants will receive injection of SHP655.

Standard of Care

Intervention Type OTHER

Participants will receive PEX as Standard of Care (SOC).

Interventions

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Placebo

Participants will receive injection of placebo matched to SHP655.

Intervention Type OTHER

SHP655

Participants will receive injection of SHP655.

Intervention Type DRUG

Standard of Care

Participants will receive PEX as Standard of Care (SOC).

Intervention Type OTHER

Other Intervention Names

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rADAMTS-13 PEX

Eligibility Criteria

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Inclusion Criteria

* Participant or legally authorized representative voluntarily signs informed consent. For participants unable to provide consent, a fully recognized medical proxy may be used according to local laws.
* Participant is 18 to 75 years old at the time of screening.
* Participant has been diagnosed with primary or secondary autoimmune acquired thrombotic thrombocytopenic purpura (aTTP) based on the following criteria:

a) Thrombocytopenia \[drop in platelet count \>=50% or platelet count \<100,000/microlitre (μL)\] i) No more than 3 participants per arm may be enrolled with a screening platelet count \>= 50,000/μL.

b) Microangiopathic hemolytic anemia \[elevation of lactate dehydrogenase (LDH) \>2-fold or by presence or increase of schistocytes in peripheral blood smear\].
* Willingness to fully comply with study procedures and requirements, and intention to initiate plasma exchange (PEX). Participants may be provisionally entered into the trial and undergo randomization pending the results of the ADAMTS-13 activity, anti-ADAMTS-13 antibody, and genetic testing for congenital thrombotic thrombocytopenic purpura (cTTP).
* If female of childbearing potential, participant presents with a negative pregnancy test and agrees to employ adequate birth control measures for the duration of the study. Sexually active males must use an accepted and effective method of contraception during the treatment and until a minimum of 16 days after the last dose administered.

Exclusion Criteria

* Participant has been diagnosed with congenital TTP.
* Participant has plasma ADAMTS-13 activity \> 10% of normal at the central lab; if screening samples are not taken until after the first PEX, ADAMTS-13 activity from the local lab is permitted to determine eligibility.
* Participant has been diagnosed with another cause of thrombotic microangiopathy (TMA) including: DIC, disseminated malignancy, malignant hypertension, hematopoietic stem cell transplantation, shiga toxin related and atypical HUS, drug toxicity (e.g. gemcitabine, mitomycin C, clopidogrel) and pregnancy-related thrombocytopenia syndromes (e.g. HELLP, eclampsia).
* Participant has been exposed to another IP within 30 days prior to enrollment or is scheduled to participate in another clinical study involving IP or investigational device during the course of the study.
* Participant has received caplacizumab within 1 month prior to study enrollment.
* Participant is human immunodeficiency virus positive (HIV+) with unstable disease or CD4+ count \<=200 cells/mm\^3 within 3 months screening.
* Participants with conditions of severe immunodeficiency.
* Participant has had a previous aTTP event in the past 30 days.
* Participant has another underlying progressive fatal disease and/or life expectancy of less than 3 months.
* Participant is identified by the investigator as being unable or unwilling to cooperate with study procedures
* Participant suffers from a mental condition rendering him/her unable to understand the nature, scope, and possible consequences of the study and/or evidence of an uncooperative attitude. However, a fully recognized medical proxy will be permitted to provide consent.
* If female, participant is pregnant or lactating.
* Participant is a family member or employee of the Sponsor or investigator.
* Any contraindication to PEX, methylprednisolone and/or rituximab as per prescribing information.
* Known life-threatening hypersensitivity reaction, including anaphylaxis, to the parent molecule ADAMTS-13, hamster protein, or other constituents of SHP655.
Minimum Eligible Age

18 Years

Maximum Eligible Age

75 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Takeda Development Center Americas, Inc.

INDUSTRY

Sponsor Role collaborator

Shire

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Study Director

Role: STUDY_DIRECTOR

Shire

Locations

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The University of Alabama at Birmingham

Birmingham, Alabama, United States

Site Status

Brigham and Women's Hospital

Boston, Massachusetts, United States

Site Status

University of Minnesota

Minneapolis, Minnesota, United States

Site Status

University Hospitals Cleveland Medical Center

Cleveland, Ohio, United States

Site Status

The Ohio State University Wexner Medical Center

Columbus, Ohio, United States

Site Status

Stephenson Cancer Center

Oklahoma City, Oklahoma, United States

Site Status

Medical University of South Carolina (MUSC)

Charleston, South Carolina, United States

Site Status

London Health Sciences Centre (LHSC) - University Hospital

London, Ontario, Canada

Site Status

St. Michael's Hospital

Toronto, Ontario, Canada

Site Status

CHU de Reims - Hôpital Maison Blanche

Reims, Marne, France

Site Status

Hopital Conception

Marseille, , France

Site Status

Chu Saint-Antoine

Paris, , France

Site Status

CHU de Rouen

Seine Maritime, , France

Site Status

Hamatologie, Onkologie, Hämostaseologie

Frankfurt, , Germany

Site Status

Fondazione IRCCS CA' Granda Ospedale Maggiore Policlinico

Milan, , Italy

Site Status

Fondazione Policlinico Universitario Agostino Gemelli IRCCS

Rome, , Italy

Site Status

Hospital General Universitario de Alicante

Alicante, , Spain

Site Status

Hospital General Universitario Gregorio Maranon

Madrid, , Spain

Site Status

Hospital Universitario Virgen del Rocio

Seville, , Spain

Site Status

Hospital Dr. Peset

Valencia, , Spain

Site Status

Hospital Universitari i Politècnic la Fe

Valencia, , Spain

Site Status

University Hospital of Wales

Cardiff, West Glamorgan, United Kingdom

Site Status

Royal Liverpool University Hospital

Liverpool, , United Kingdom

Site Status

1st Floor, UCLH-Haematology

London, , United Kingdom

Site Status

Countries

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United States Canada France Germany Italy Spain United Kingdom

Provided Documents

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Document Type: Study Protocol: Original

View Document

Document Type: Study Protocol: Protocol Amendment 1

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Document Type: Study Protocol: Protocol Amendment 2

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Document Type: Study Protocol: Protocol Amendment 3

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Document Type: Study Protocol: Protocol Amendment 4

View Document

Document Type: Statistical Analysis Plan

View Document

Related Links

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https://clinicaltrials.takeda.com/study-detail/5f6b5fe84db2bf003ab47aea

To obtain more information on the study, click here/on this link

Other Identifiers

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2018-003775-35

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

SHP655-201

Identifier Type: -

Identifier Source: org_study_id

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