A Study of JR-141 in Patients With Mucopolysaccharidosis II

NCT ID: NCT03568175

Last Updated: 2022-11-14

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2/PHASE3

Total Enrollment

28 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-08-01

Study Completion Date

2020-02-20

Brief Summary

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A Phase II/ III multicenter, open-label, single-group, designed to evaluate the efficacy and safety of study drug for the treatment of the MPS II.

Detailed Description

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Conditions

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Mucopolysaccharidosis II

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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JR-141 2.0 mg/kg/week

Group Type EXPERIMENTAL

JR-141

Intervention Type DRUG

IV infusion, 2.0 mg/kg/week

Interventions

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JR-141

IV infusion, 2.0 mg/kg/week

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

1. Capable of providing written consent by himself (not mandatory for those aged under 20 years at the time of informed consent process, or those who is impossible to obtain consent from the patient himself due to intellectual disabilities associated with MPS II.)
2. In the case of a patient who is under the age of 20 years or from whom it is not possible to obtain consent due to intellectual disabilities associated with MPS II, he may be included if written consent can be provided by legal representative (however, written consent should be obtained from the patient himself too, whenever possible)
3. Males with confirmed diagnosis of MPS II, based on deficient activity of iduronate-2-sulfatase (IDS) in leucocytes, plasma or fibroblasts and/or pathogenic mutations identified in the IDS gene, etc.
4. Naïve patients or patients who are receiving stable enzyme replacement therapy with Elaprase for more than 8 weeks before the observational period starts.

Exclusion Criteria

1. Previous engrafted HSCT, excluding those who need enzyme replacement therapy even after HSCT.
2. Judged by the investigator or subinvestigator as being unable to undergo lumbar puncture, including those who have difficulties in taking position for lumbar puncture due to joint contracture or those who are likely experience difficulty breathing during the lumbar puncture process.
3. Judged by the investigator or subinvestigator to be ineligible to participate in the study due to a history of serious drug allergy or sensitivity.
4. Patients who have received other investigational product within 4 months before enrollment in the study.
5. Otherwise judged by the investigator or subinvestigator to be ineligible to participate in the study.
Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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JCR Pharmaceuticals Co., Ltd.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Fukui Clinical site

Fukui, , Japan

Site Status

Fukuoka Clinical site 2

Fukuoka, , Japan

Site Status

Fukuoka Clinical site

Fukuoka, , Japan

Site Status

Gifu Clinical site

Gifu, , Japan

Site Status

Hokkaido Clinical site

Hokkaido, , Japan

Site Status

Kanagawa Clinical site

Kanagawa, , Japan

Site Status

Kumamoto Clinical site

Kumamoto, , Japan

Site Status

Okayama Clinical site

Okayama, , Japan

Site Status

Okayama Clinical site 2

Okayama, , Japan

Site Status

Okinawa Clinical site

Okinawa, , Japan

Site Status

Osaka Clinical site 3

Osaka, , Japan

Site Status

Osaka Clinical site 2

Osaka, , Japan

Site Status

Osaka Clinical site

Osaka, , Japan

Site Status

Saitama Clinical site

Saitama, , Japan

Site Status

Shizuoka Clinical site

Shizuoka, , Japan

Site Status

Shizuoka Clinical site 2

Shizuoka, , Japan

Site Status

Tochigi Clinical site

Tochigi, , Japan

Site Status

Tokyo Clinical site

Tokyo, , Japan

Site Status

Tottori Clinical site

Tottori, , Japan

Site Status

Countries

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Japan

Related Links

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https://pubmed.ncbi.nlm.nih.gov/33038326/

A Phase 2/3 Trial of Pabinafusp Alfa, IDS Fused with Anti-Human Transferrin Receptor Antibody, Targeting Neurodegeneration in MPS-II

Other Identifiers

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JR-141-301

Identifier Type: -

Identifier Source: org_study_id

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