Efficacy and Safety Study of BCX7353 as an Oral Treatment for the Prevention of Attacks in HAE

NCT ID: NCT03485911

Last Updated: 2023-06-26

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

View full results

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

COMPLETED

Clinical Phase

PHASE3

Total Enrollment

121 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-02-06

Study Completion Date

2022-04-06

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

This is a phase 3, multicenter, randomized, double-blind, placebo-controlled trial to evaluate the efficacy and safety of oral BCX7353 in preventing acute angioedema attacks in patients with Type I and Type II HAE.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Hereditary Angioedema HAE

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

PREVENTION

Blinding Strategy

TRIPLE

Participants Caregivers Investigators
Only Part 1 and Part 2 were blinded. As part 3 was open-label, no blinding was used

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

BCX7353 110 mg once daily

BCX7353 administered as oral capsules once daily

Group Type EXPERIMENTAL

BCX7353 capsules

Intervention Type DRUG

BCX7353 oral capsules administered once daily

BCX7353 150 mg once daily

BCX7353 administered as oral capsules once daily

Group Type EXPERIMENTAL

BCX7353 capsules

Intervention Type DRUG

BCX7353 oral capsules administered once daily

Placebo

Matching placebo administered as oral capsules once daily

Group Type PLACEBO_COMPARATOR

Placebo oral capsule

Intervention Type DRUG

Matching oral capsules administered once daily

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

BCX7353 capsules

BCX7353 oral capsules administered once daily

Intervention Type DRUG

Placebo oral capsule

Matching oral capsules administered once daily

Intervention Type DRUG

Other Intervention Names

Discover alternative or legacy names that may be used to describe the listed interventions across different sources.

Berotralstat

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

* A clinical diagnosis of hereditary angioedema Type 1 or Type 2, defined as having a C1-INH functional level and a C4 level below the lower limit of the normal (LLN) reference range, as assessed during the Screening period.
* Subject weight of ≥ 40 kg
* Access to and ability to use one or more acute medications approved by the relevant competent authority for the treatment of acute attacks of HAE
* Subjects must be medically appropriate for on-demand treatment as the sole medicinal management for their HAE during the study.
* Subjects must have a specified number of investigator-confirmed attacks during the run-in period of a maximum of 56 days from the Screening visit.
* Acceptable effective contraception
* Written informed consent

Exclusion Criteria

* Pregnancy or breast-feeding
* Any clinically significant medical condition or medical history that, in the opinion of the Investigator or Sponsor, would interfere with the subject's safety or ability to participate in the study
* Any laboratory parameter abnormality that, in the opinion of the Investigator, is clinically significant and relevant for this study
* Severe hypersensitivity to multiple medicinal products or severe hypersensitivity/ anaphylaxis with unclear etiology
* Use of C1-INH within 14 days or use of androgens or tranexamic acid within 28 days prior to the Screening visit for prophylaxis of HAE attacks, or initiation of these drugs during the study
* Current participation in any other investigational drug study or received another investigational drug within 30 days of the Screening visit
* Prior enrollment in a BCX7353 study
Minimum Eligible Age

12 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

BioCryst Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Bruce Zuraw, MD

Role: PRINCIPAL_INVESTIGATOR

UC San Diego School of Medicine, US HAE Angioedema Center

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Study center

Birmingham, Alabama, United States

Site Status

Study center

Scottsdale, Arizona, United States

Site Status

Study center

Little Rock, Arkansas, United States

Site Status

Study Center

San Diego, California, United States

Site Status

Study center

Santa Monica, California, United States

Site Status

Study Center

Walnut Creek, California, United States

Site Status

Study center

Colorado Springs, Colorado, United States

Site Status

Study Center

Tampa, Florida, United States

Site Status

Study center

Chevy Chase, Maryland, United States

Site Status

Study Center

Boston, Massachusetts, United States

Site Status

Study Center

Ann Arbor, Michigan, United States

Site Status

Study center

Plymouth, Minnesota, United States

Site Status

Study Center

St Louis, Missouri, United States

Site Status

Study center

Belleville, New Jersey, United States

Site Status

Study Center

Fair Lawn, New Jersey, United States

Site Status

Study center

Piscataway, New Jersey, United States

Site Status

Study Center

New York, New York, United States

Site Status

Study Site

Charlotte, North Carolina, United States

Site Status

Study Center

Durham, North Carolina, United States

Site Status

Study Center

Cincinnati, Ohio, United States

Site Status

Study center

Columbus, Ohio, United States

Site Status

Study center

Clackamas, Oregon, United States

Site Status

Study Center

Hershey, Pennsylvania, United States

Site Status

Study center

Austin, Texas, United States

Site Status

Study center

Dallas, Texas, United States

Site Status

Study Center

San Antonio, Texas, United States

Site Status

Study Center

Spokane, Washington, United States

Site Status

Study Center

Vienna, , Austria

Site Status

Study Center

Ottawa, Ontario, Canada

Site Status

Study Center

Toronto, Ontario, Canada

Site Status

Study Center

Québec, , Canada

Site Status

Study Center

Brno, , Czechia

Site Status

Study Center

Pilsen, , Czechia

Site Status

Study Center

Grenoble, , France

Site Status

Study Center

Paris, , France

Site Status

Study Center

Berlin, , Germany

Site Status

Study Center

Frankfurt, , Germany

Site Status

Study Center

Budapest, , Hungary

Site Status

Study Center

Skopje, , North Macedonia

Site Status

Study Center

Sângeorgiu de Mureș, Jud. Mureș, Romania

Site Status

Study Center

Barcelona, , Spain

Site Status

Study Center

Madrid, , Spain

Site Status

Study Center

Seville, , Spain

Site Status

Study Center

Cambridge, , United Kingdom

Site Status

Study Center

Frimley, , United Kingdom

Site Status

Study Center

London, , United Kingdom

Site Status

Study Center

Plymouth, , United Kingdom

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States Austria Canada Czechia France Germany Hungary North Macedonia Romania Spain United Kingdom

References

Explore related publications, articles, or registry entries linked to this study.

Farkas H, Balla Z. A review of berotralstat for the treatment of hereditary angioedema. Expert Rev Clin Immunol. 2023 Feb;19(2):145-153. doi: 10.1080/1744666X.2023.2150611. Epub 2022 Nov 29.

Reference Type DERIVED
PMID: 36408587 (View on PubMed)

Beard N, Frese M, Smertina E, Mere P, Katelaris C, Mills K. Interventions for the long-term prevention of hereditary angioedema attacks. Cochrane Database Syst Rev. 2022 Nov 3;11(11):CD013403. doi: 10.1002/14651858.CD013403.pub2.

Reference Type DERIVED
PMID: 36326435 (View on PubMed)

Wedner HJ, Aygoren-Pursun E, Bernstein J, Craig T, Gower R, Jacobs JS, Johnston DT, Lumry WR, Zuraw BL, Best JM, Iocca HA, Murray SC, Desai B, Nagy E, Sheridan WP, Kiani-Alikhan S. Randomized Trial of the Efficacy and Safety of Berotralstat (BCX7353) as an Oral Prophylactic Therapy for Hereditary Angioedema: Results of APeX-2 Through 48 Weeks (Part 2). J Allergy Clin Immunol Pract. 2021 Jun;9(6):2305-2314.e4. doi: 10.1016/j.jaip.2021.03.057. Epub 2021 Apr 15.

Reference Type DERIVED
PMID: 33866032 (View on PubMed)

Zuraw B, Lumry WR, Johnston DT, Aygoren-Pursun E, Banerji A, Bernstein JA, Christiansen SC, Jacobs JS, Sitz KV, Gower RG, Gagnon R, Wedner HJ, Kinaciyan T, Hakl R, Hanzlikova J, Anderson JT, McNeil DL, Fritz SB, Yang WH, Tachdjian R, Busse PJ, Craig TJ, Li HH, Farkas H, Best JM, Clemons D, Cornpropst M, Dobo SM, Iocca HA, Kargl D, Nagy E, Murray SC, Collis P, Sheridan WP, Maurer M, Riedl MA. Oral once-daily berotralstat for the prevention of hereditary angioedema attacks: A randomized, double-blind, placebo-controlled phase 3 trial. J Allergy Clin Immunol. 2021 Jul;148(1):164-172.e9. doi: 10.1016/j.jaci.2020.10.015. Epub 2020 Oct 21.

Reference Type DERIVED
PMID: 33098856 (View on PubMed)

Provided Documents

Download supplemental materials such as informed consent forms, study protocols, or participant manuals.

Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

BCX7353-302

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

STOP-HAE: A Phase 3 Study of ADX-324 in HAE
NCT06960213 RECRUITING PHASE3