Registry for Patients With X-Linked Hypophosphatemia

NCT ID: NCT03193476

Last Updated: 2024-09-19

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Total Enrollment

1343 participants

Study Classification

OBSERVATIONAL

Study Start Date

2017-09-12

Study Completion Date

2029-07-01

Brief Summary

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This is an international, multicentre, prospective, non-interventional, observational Registry of patients with X-Linked hypophosphatemia (XLH). The main objective of this XLH Registry is to collect data to characterise the treatment, progression and long-term outcomes of XLH in both adult and paediatric settings.

Detailed Description

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Methodology

This is an international, multicentre, prospective, non-interventional, observational Registry of patients with X-Linked hypophosphatemia (XLH). The objectives of this XLH Registry is to collect natural history data of XLH to characterise the treatment, progression and long-term outcomes of XLH in both adult and paediatric patients.

This XLH Registry will invite \& include patients with XLH, of all ages \& gender, irrespective of whether they are on, or not on, a treatment regimen for their XLH.

However, patients who are concurrently participating in an interventional clinical trial, including Investigator-Initiated Studies, are excluded from the XLH Registry, as per the Exclusion Criteria as set in the Protocol. These patients participating in an interventional clinical trial, when their involvement in the trial has ended, will be approached and invited to be included in the XLH Registry.

A subset of the XLH Registry data will be used to fulfil a Post-Authorisation Safety Study (PASS) as requested by the European Medicines Agency's (EMA's) Committee for Medical Products for Human Use (CHMP). Study centres which agree to participate in the PASS will be asked to solicit adverse events on enrolled patients. Not all centres are expected to participate in the PASS. Furthermore, as part of burosumab's Risk Management Plan (RMP), the majority of the safety concerns are being investigated in a Category 3 Post-Authorisation Safety Study (PASS), which uses the XLH Registry. The data source to conduct the PASS is the data collected in the XLH Registry.

All eligible patients at the participating clinics will be asked to participate in the XLH Registry:

* Informed consent will be obtained from adult patients.
* Parental informed consent for the inclusion of a child will be obtained from the child's legally designated representative in line with national guidance.
* Assent will also be sought from children of applicable age in line with national guidance. In all cases the health professional responsible for enrolling the patient into the XLH Registry will assess the appropriateness of gaining assent from an individual at their discretion.

After the patient or legally designated representative has signed the informed consent, the patient data will be recorded in the XLH Registry, including baseline, retrospective and prospective data. Data will be collected using a web-based Electronic Data Capture (EDC) system. A patient identification number will be automatically generated by the system upon enrolment.

No pre-determined follow-up requirements will apply. However, physicians will be prompted to update patient data in the XLH Registry in relation to the patients' visits to the physician. Physicians will be reminded to update the XLH Registry at 12 months after the previous visit information was entered for a patient.

For those patients who attend clinic at more frequent intervals as part of their standard care, data for these visits will be entered at the 12-month intervals with an option to add multiple dates.

This is a prospective observational Registry and no additional interventions other than standard clinical practice are required by the protocol.

Conditions

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X-Linked Hypophosphatemia

Study Design

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Observational Model Type

OTHER

Study Time Perspective

OTHER

Eligibility Criteria

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Inclusion Criteria

1. Patients aged from ≥0 years of age at baseline
2. In the opinion of the treating physician the patient has a clinical presentation, radiological, biochemical or genetic investigation results that support diagnosis of XLH
3. Patient is not currently participating in an interventional clinical trial

A patient who meets any of the following criteria at the enrolment visit (baseline) will be excluded from this XLH Registry

Exclusion Criteria

1. Patient or their legally designated representative does not have the cognitive capacity to provide informed consent.
2. Patient is currently participating in an interventional clinical trial. Patients will be approached for inclusion into the registry once their involvement in the trial ends (including the completion of all trial follow up assessments).
3. Participation in a Compassionate Use Program, Pre-commercial Program (i.e. Named Patient Sales, Nominative ATU) or Investigator Initiated Study does not preclude a patient from participation in this XLH Registry
Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Iqvia Pty Ltd

INDUSTRY

Sponsor Role collaborator

Kyowa Kirin Pharmaceutical Development Ltd

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Hopital Universitaire des Enfants Reine Fabiola

Brussels, , Belgium

Site Status RECRUITING

Universitair Ziekenhuis Brussel

Brussels, , Belgium

Site Status RECRUITING

Cliniques Universitaires Saint-Luc

Brussels, , Belgium

Site Status RECRUITING

UZA

Edegem, , Belgium

Site Status RECRUITING

Universitair Ziekenhuis Gent

Ghent, , Belgium

Site Status RECRUITING

UZ Leuven

Leuven, , Belgium

Site Status RECRUITING

CHU de Liège

Liège, , Belgium

Site Status RECRUITING

SHATPD "Prof Ivan Mitev" EAD

Sofia, , Bulgaria

Site Status ACTIVE_NOT_RECRUITING

UMHAT "SofiaMed", OOD

Sofia, , Bulgaria

Site Status ACTIVE_NOT_RECRUITING

Children Hospital

Brno, , Czechia

Site Status ACTIVE_NOT_RECRUITING

Fakultni nemocnice v Motole

Prague, , Czechia

Site Status ACTIVE_NOT_RECRUITING

Aalborg University Hospital

Aalborg, , Denmark

Site Status ACTIVE_NOT_RECRUITING

Århus Universitetshospital - Aarhus sygehus

Aarhus, , Denmark

Site Status ACTIVE_NOT_RECRUITING

Århus Universitetshospital

Aarhus, , Denmark

Site Status ACTIVE_NOT_RECRUITING

Hospital South West Jutland

Esbjerg, , Denmark

Site Status COMPLETED

Rigshospitalet - Paediatric

København Ø, , Denmark

Site Status ACTIVE_NOT_RECRUITING

Rigshospitalet

København Ø, , Denmark

Site Status COMPLETED

OUH

Odense, , Denmark

Site Status ACTIVE_NOT_RECRUITING

Groupe Hospitalier Pellegrin - Hôpital des Enfants

Bordeaux, , France

Site Status ACTIVE_NOT_RECRUITING

CHU de Lyon - Hôpital Femme Mere Enfant

Bron, , France

Site Status ACTIVE_NOT_RECRUITING

CHRU Lille

Lille, , France

Site Status ACTIVE_NOT_RECRUITING

Hopital Roger Salengro - CHU Lille

Lille, , France

Site Status ACTIVE_NOT_RECRUITING

Hopital Arnaud de Villeneuve

Montpellier, , France

Site Status ACTIVE_NOT_RECRUITING

CHU de Nantes

Nantes, , France

Site Status NOT_YET_RECRUITING

Hôpital Cochin

Paris, , France

Site Status ACTIVE_NOT_RECRUITING

CHU Paris Sud - Hopital Bicêtre

Paris, , France

Site Status ACTIVE_NOT_RECRUITING

Hôpital Bicêtre

Paris, , France

Site Status ACTIVE_NOT_RECRUITING

"Hopital Pierre-Paul Riquet Centre de Rhumatologie"

Toulouse, , France

Site Status ACTIVE_NOT_RECRUITING

Hopital Purpan

Toulouse, , France

Site Status ACTIVE_NOT_RECRUITING

Klinikum Ernst-von-Bergmann Potsdam und Bad Belzig

Bad Belzig, , Germany

Site Status ACTIVE_NOT_RECRUITING

Uniklinikum Bochum

Bochum, , Germany

Site Status WITHDRAWN

Uniklinikum Koeln

Cologne, , Germany

Site Status WITHDRAWN

MVZ Dr. Eberhard & Partner

Dortmund, , Germany

Site Status WITHDRAWN

Universitaetsklinikum Freiburg

Freiburg im Breisgau, , Germany

Site Status WITHDRAWN

Medizinische Hochschule Hannover

Hanover, , Germany

Site Status ACTIVE_NOT_RECRUITING

Universitaetsklinikum

Leipzig, , Germany

Site Status ACTIVE_NOT_RECRUITING

Hormon and Stoffwechselzentrum

Mainz, , Germany

Site Status ACTIVE_NOT_RECRUITING

Semmelweis Egyetem

Budapest, , Hungary

Site Status ACTIVE_NOT_RECRUITING

Semmelweis Egyetem

Budapest, , Hungary

Site Status ACTIVE_NOT_RECRUITING

The Children's University Hospital

Dublin, , Ireland

Site Status ACTIVE_NOT_RECRUITING

Rambam Health Care Center

Haifa, , Israel

Site Status ACTIVE_NOT_RECRUITING

Schneider Medical Center

Petah Tikva, , Israel

Site Status ACTIVE_NOT_RECRUITING

Sheba Medical Center

Ramat Gan, , Israel

Site Status ACTIVE_NOT_RECRUITING

Dana-Dwek Children's Hospital

Tel Aviv, , Israel

Site Status WITHDRAWN

Azienda Ospedaliero Universitaria Consorziale Policlinico di Bari

Bari, , Italy

Site Status ACTIVE_NOT_RECRUITING

AO S. Pio G. Rumno

Benevento, , Italy

Site Status ACTIVE_NOT_RECRUITING

Azienda Ospedaliera Universitaria Policlinico Sant'Orsola Malpighi

Bologna, , Italy

Site Status ACTIVE_NOT_RECRUITING

Presidio Ospedaliero Di Summa Antonio Perrino

Brindisi, , Italy

Site Status ACTIVE_NOT_RECRUITING

Azienda Ospedaliera Brotzu

Cagliari, , Italy

Site Status ACTIVE_NOT_RECRUITING

Azienda Ospedaliera Universitaria Careggi

Florence, , Italy

Site Status ACTIVE_NOT_RECRUITING

Istituto Giannina Gaslini-Ospedale Pediatrico IRCCS

Genova, , Italy

Site Status ACTIVE_NOT_RECRUITING

ICOT-Istituto Chirurgico Ortopedico Traumatologico

Latina, , Italy

Site Status NOT_YET_RECRUITING

Azienda Ospedaliera Universitaria Policlinico G. Martino

Messina, , Italy

Site Status ACTIVE_NOT_RECRUITING

Ospedale San Raffaele - Adult

Milan, , Italy

Site Status ACTIVE_NOT_RECRUITING

Ospedale San Raffaele

Milan, , Italy

Site Status ACTIVE_NOT_RECRUITING

Azienda Ospedaliera di Padova

Padua, , Italy

Site Status ACTIVE_NOT_RECRUITING

Azienda Ospedaliera di Padova

Padua, , Italy

Site Status ACTIVE_NOT_RECRUITING

Istituto Auxologico Italiano -I.R.C.C.S.

Piancavallo, , Italy

Site Status ACTIVE_NOT_RECRUITING

Stabilimento Ospedaliero Santa Chiara

Pisa, , Italy

Site Status ACTIVE_NOT_RECRUITING

Ospedale Pediatrico Bambino Gesù

Roma, , Italy

Site Status ACTIVE_NOT_RECRUITING

Azienda Ospedaliera Città della Salute e della Scienza di Torino (Presidio Sant'Anna)

Torino, , Italy

Site Status NOT_YET_RECRUITING

Azienda Ospedaliero-Universitaria Città della Salute e della Scienza di Torino

Torino, , Italy

Site Status ACTIVE_NOT_RECRUITING

I.R.C.C.S. Burlo Garofolo

Trieste, , Italy

Site Status ACTIVE_NOT_RECRUITING

Children's Clinical University Hospital

Riga, , Latvia

Site Status ACTIVE_NOT_RECRUITING

Universitair Medisch Centrum Groningen

Groningen, , Netherlands

Site Status ACTIVE_NOT_RECRUITING

Oslo University Hospital

Oslo, , Norway

Site Status ACTIVE_NOT_RECRUITING

Oslo Universitetssykehus HF, Ulleval

Oslo, , Norway

Site Status ACTIVE_NOT_RECRUITING

St. Olav's University Hospital

Trondheim, , Norway

Site Status ACTIVE_NOT_RECRUITING

Hospital Pediatrico de Coimbra

Coimbra, , Portugal

Site Status ACTIVE_NOT_RECRUITING

Centro Hospitalar de Lisboa Central, E.P.E. - Hospital Dona Estefânia

Lisbon, , Portugal

Site Status ACTIVE_NOT_RECRUITING

Centro Hospitalar de Lisboa Norte, E.P.E. - Hospital de Santa Maria

Lisbon, , Portugal

Site Status ACTIVE_NOT_RECRUITING

Centro Hospitalar do Porto, E.P.E. - Hospital de Santo António

Porto, , Portugal

Site Status ACTIVE_NOT_RECRUITING

Hospital de Sao Joao

Porto, , Portugal

Site Status ACTIVE_NOT_RECRUITING

National Institute of Childrenś Health NUDCH

Bratislava, , Slovakia

Site Status ACTIVE_NOT_RECRUITING

University Clinical Centre Ljubljana

Ljubljana, , Slovenia

Site Status ACTIVE_NOT_RECRUITING

Hospital de Cruces

Barakaldo, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Universitari Vall d'Hebron

Barcelona, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Clinic de Barcelona

Barcelona, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital General Universitario Santa Lucía

Cartagena, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Universitario Virgen de la Arrixaca

El Palmar, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Sant Joan de Deu

Esplugues de Llobregat, , Spain

Site Status ACTIVE_NOT_RECRUITING

Complejo Hospitalario Universitario Insular Materno-Infantil

Las Palmas de Gran Canaria, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Infantil Universitario Niño Jesus

Madrid, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Universitario Central de Asturias

Oviedo, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Central de Asturias

Oviedo, , Spain

Site Status ACTIVE_NOT_RECRUITING

Hospital Universitario Nuestra Señora de la Candelaria

Santa Cruz de Tenerife, , Spain

Site Status ACTIVE_NOT_RECRUITING

Queen Silvia Children's Hospital

Gothenburg, , Sweden

Site Status ACTIVE_NOT_RECRUITING

Lund University

Lund, , Sweden

Site Status COMPLETED

Karolinska Institute

Stockholm, , Sweden

Site Status ACTIVE_NOT_RECRUITING

Karolinska Institute (Pediatric)

Stockholm, , Sweden

Site Status ACTIVE_NOT_RECRUITING

Inselspital Bern

Bern, , Switzerland

Site Status RECRUITING

Hopitaux Universitaires de Geneve (HUG)

Geneva, , Switzerland

Site Status RECRUITING

Centre Hopitalier Universitaire Vaudois

Lausanne, , Switzerland

Site Status RECRUITING

Centre Hopitalier Universitaire Vaudois

Lausanne, , Switzerland

Site Status RECRUITING

Kantonsspital St. Gallen

Sankt Gallen, , Switzerland

Site Status RECRUITING

Klinik Hirslanden Zuerich

Zurich, , Switzerland

Site Status RECRUITING

Royal Belfast Hospital for Sick Children

Belfast, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Birmingham Children's Hospital

Birmingham, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

University Hospitals Bristol and Weston

Bristol, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Addenbrooke's Hospital

Cambridge, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

University Hospital of Wales

Cardiff, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Western General Hospital

Edinburgh, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Royal Hospital for Sick Children and Young People

Edinburgh, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Gartnavel General Hospital

Glasgow, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Queen Elizabeth University Hospital

Glasgow, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Raigmore Hospital

Inverness, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Leeds General Infirmary

Leeds, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Alder Hey Children's Hospital

Liverpool, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Royal Liverpool University Hospital

Liverpool, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

National Hospital for Neurology and Neurosurgery

London, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Evelina Childrens Hospital

London, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Great Ormond Street Hospital for Children

London, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Royal Manchester Children's Hospital

Manchester, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Oxford University Hospital NHS Trust

Oxford, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Sheffield Childrens Hospital

Sheffield, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Sheffield Teaching Hospitals

Sheffield, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Southampton General Hospital

Southampton, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Stanmore Royal Orthopaedic Hospital

Stanmore, , United Kingdom

Site Status ACTIVE_NOT_RECRUITING

Countries

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Belgium Bulgaria Czechia Denmark France Germany Hungary Ireland Israel Italy Latvia Netherlands Norway Portugal Slovakia Slovenia Spain Sweden Switzerland United Kingdom

Central Contacts

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Clinical Trial Cordinator

Role: CONTACT

+49 15114861167

Facility Contacts

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Emese Boros

Role: primary

Jean DeSchepper

Role: primary

Nathalie Godefroid

Role: primary

Koen Van Hoeck

Role: primary

Agnieszka Prytula

Role: primary

Elena Levtchenko

Role: primary

Caroline GERNAY

Role: primary

Lucile Figueres

Role: primary

Silverio Rotondi

Role: primary

Luisa de Sanctis

Role: primary

Fuster

Role: primary

Andrea Trombetti

Role: primary

Elena Gonzalez-Rodriguez

Role: primary

Hassib Chehade

Role: primary

Stefan Bilz

Role: primary

Serra

Role: primary

References

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Carpenter TO, Fukumoto S, Haffner D, Imel EA, Ozono K, Ishii H, Li Z, Sandilands K, Joos-Vandewalle P, Lee C, Kanematsu M, McCullough KP, Brandi ML. Advancing Patient Evidence in XLH (APEX): Baseline analysis of a global data unification program. Bone. 2025 Dec;201:117649. doi: 10.1016/j.bone.2025.117649. Epub 2025 Sep 15.

Reference Type DERIVED
PMID: 40962182 (View on PubMed)

Brandi ML, Ariceta G, Beck-Nielsen SS, Boot AM, Briot K, de Lucas Collantes C, Emma F, Giannini S, Haffner D, Keen R, Levtchenko E, Mӓkitie O, Nilsson O, Schnabel D, Tripto-Shkolnik L, Zillikens MC, Liu J, Tudor A, Mughal MZ. Post-authorisation safety study of burosumab use in paediatric, adolescent and adult patients with X-linked hypophosphataemia: rationale and description. Ther Adv Chronic Dis. 2022 Sep 5;13:20406223221117471. doi: 10.1177/20406223221117471. eCollection 2022.

Reference Type DERIVED
PMID: 36082134 (View on PubMed)

Other Identifiers

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XLH Registry Version 3.0

Identifier Type: -

Identifier Source: org_study_id

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