A Clinical Trial of Retinal Gene Therapy for X-linked Retinitis Pigmentosa Using BIIB112

NCT ID: NCT03116113

Last Updated: 2024-01-18

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

View full results

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

COMPLETED

Clinical Phase

PHASE1/PHASE2

Total Enrollment

50 participants

Study Classification

INTERVENTIONAL

Study Start Date

2017-03-08

Study Completion Date

2020-11-18

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

The objective of the study is to evaluate the safety, tolerability and efficacy of a single sub-retinal injection of BIIB112 in participants with X-linked retinitis pigmentosa (XLRP).

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

This study was previously posted by NightstaRx Ltd. In October 2020, sponsorship of the trial was transferred to Biogen.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

X-Linked Retinitis Pigmentosa

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

RANDOMIZED

Intervention Model

SEQUENTIAL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Part 1: BIIB112 Dose 1

Participants will receive a single Dose 1 of BIIB112 by sub-retinal injection on Day 0.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 1: BIIB112 Dose 2

Participants will receive a single Dose 2 of BIIB112 by sub-retinal injection on Day 0.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 1: BIIB112 Dose 3

Participants will receive a single Dose 3 of BIIB112 by sub-retinal injection on Day 0.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 1: BIIB112 Dose 4

Participants will receive a single Dose 4 of BIIB112 by sub-retinal injection on Day 0.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 1: BIIB112 Dose 5

Participants will receive a single Dose 5 of BIIB112 by sub-retinal injection on Day 0.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 1: BIIB112 Dose 6

Participants will receive a single Dose 6 of BIIB112 by sub-retinal injection on Day 0.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 2: BIIB112 High Dose

Participants will receive a single high dose of BIIB112 by sub-retinal injection.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 2: BIIB112 Low Dose

Participants will receive a single low dose of BIIB112 by sub-retinal injection.

Group Type EXPERIMENTAL

BIIB112

Intervention Type BIOLOGICAL

Administered as specified in the treatment arm.

Part 2: Untreated Group

Participants will receive no intervention to allow for a controlled comparison.

Group Type NO_INTERVENTION

No interventions assigned to this group

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

BIIB112

Administered as specified in the treatment arm.

Intervention Type BIOLOGICAL

Other Intervention Names

Discover alternative or legacy names that may be used to describe the listed interventions across different sources.

AAV8-RPGR

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

Part 1:

* Participants with genetically confirmed diagnosis of XLRP (with RPGR mutation).
* Participant with active disease clinically visible within the macular region in both eyes.

Part 2:

\- Participant with mean total retinal sensitivity in the study eye as assessed by microperimetry ≥ 0.1 dB and ≤8 dB.

Exclusion Criteria

Parts 1 and 2:

* Participant with history of amblyopia in either eye.
* Participated in a gene therapy trial previously or a clinical trial with an investigational drug in the past 12 weeks or received a gene/cell-based therapy at any time previously.
Minimum Eligible Age

10 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Biogen

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Medical Director

Role: STUDY_DIRECTOR

Biogen

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Research Site

Gainesville, Florida, United States

Site Status

Research Site

Miami, Florida, United States

Site Status

Research Site

Portland, Oregon, United States

Site Status

Research Site

Philadelphia, Pennsylvania, United States

Site Status

Research Site

Dallas, Texas, United States

Site Status

Research Site

Manchester, , United Kingdom

Site Status

Research Site

Oxford, , United Kingdom

Site Status

Research Site

Southampton, , United Kingdom

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States United Kingdom

References

Explore related publications, articles, or registry entries linked to this study.

Cehajic-Kapetanovic J, Xue K, Martinez-Fernandez de la Camara C, Nanda A, Davies A, Wood LJ, Salvetti AP, Fischer MD, Aylward JW, Barnard AR, Jolly JK, Luo E, Lujan BJ, Ong T, Girach A, Black GCM, Gregori NZ, Davis JL, Rosa PR, Lotery AJ, Lam BL, Stanga PE, MacLaren RE. Initial results from a first-in-human gene therapy trial on X-linked retinitis pigmentosa caused by mutations in RPGR. Nat Med. 2020 Mar;26(3):354-359. doi: 10.1038/s41591-020-0763-1. Epub 2020 Feb 24.

Reference Type RESULT
PMID: 32094925 (View on PubMed)

Raji S, Taylor LJ, Josan AS, MacLaren RE, Cehajic-Kapetanovic J. Early-Onset Cone Photoreceptor Degeneration Is Associated With High Myopia in RPGR-Related Retinal Dystrophy. J Ophthalmol. 2025 Jun 11;2025:4244740. doi: 10.1155/joph/4244740. eCollection 2025.

Reference Type DERIVED
PMID: 40535564 (View on PubMed)

Lam BL, Pennesi ME, Kay CN, Panda S, Gow JA, Zhao G, MacLaren RE; XIRIUS Study Group. Assessment of Visual Function with Cotoretigene Toliparvovec in X-Linked Retinitis Pigmentosa in the Randomized XIRIUS Phase 2/3 Study. Ophthalmology. 2024 Sep;131(9):1083-1093. doi: 10.1016/j.ophtha.2024.02.023. Epub 2024 Feb 28.

Reference Type DERIVED
PMID: 38423215 (View on PubMed)

von Krusenstiern L, Liu J, Liao E, Gow JA, Chen G, Ong T, Lotery AJ, Jalil A, Lam BL, MacLaren RE; XIRIUS Part 1 Study GroupXOLARIS Study Group. Changes in Retinal Sensitivity Associated With Cotoretigene Toliparvovec in X-Linked Retinitis Pigmentosa With RPGR Gene Variations. JAMA Ophthalmol. 2023 Mar 1;141(3):275-283. doi: 10.1001/jamaophthalmol.2022.6254.

Reference Type DERIVED
PMID: 36757689 (View on PubMed)

Provided Documents

Download supplemental materials such as informed consent forms, study protocols, or participant manuals.

Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

2016-003852-60

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

274RP101

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

Long-term Follow-Up Study of RGX-314 and Fellow Eye Substudy
NCT03999801 ENROLLING_BY_INVITATION PHASE2
UGX202 Injection in Patients With Advanced Retinitis Pigmentosa
NCT07311863 NOT_YET_RECRUITING EARLY_PHASE1
Gene Therapy for Blindness Caused by Choroideremia
NCT01461213 COMPLETED PHASE1/PHASE2