Long-term Safety and Efficacy Follow-up of BIIB111 for the Treatment of Choroideremia and BIIB112 for the Treatment of X-Linked Retinitis Pigmentosa

NCT ID: NCT03584165

Last Updated: 2025-06-12

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ENROLLING_BY_INVITATION

Clinical Phase

PHASE3

Total Enrollment

330 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-06-04

Study Completion Date

2026-06-04

Brief Summary

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The objective of the study is to evaluate the long-term safety and efficacy of a sub-retinal injection of BIIB111 in participants with Choroideremia (CHM) who have been previously treated with BIIB111 and who have exited an antecedent study; these treated participants will be compared with untreated control participants who have exited the STAR (NCT03496012) study and BIIB112 in participants with X-linked retinitis pigmentosa (XLRP) who have been previously treated with BIIB112 and who have exited an antecedent study.

Detailed Description

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This study was previously posted by NightstaRx Ltd. In October 2020, sponsorship of the trial was transferred to Biogen.

Conditions

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Choroideremia X-Linked Retinitis Pigmentosa

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

OTHER

Blinding Strategy

SINGLE

Outcome Assessors

Study Groups

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BIIB111

Participants previously treated with sub-retinal injection of BIIB111 in antecedent studies 273CH301 (NCT03496012) and 273CH203 (NCT03507686) will be enrolled. Participants previously treated with this same sub-retinal injection (rAAV2-REP1) in antecedent studies 20150371 (NCT02553135), Pro00028599 (NCT02077361), THOR-TUE-01 (NCT02671539), CHM09/01 (NCT01461213) and REGEN2015 (NCT02407678) will also be invited for enrollment. This is a follow-up study, investigational product was administered in the previous study.

Group Type EXPERIMENTAL

BIIB111

Intervention Type GENETIC

Administered as specified in the treatment arm.

BIIB112

Participants previously treated with sub-retinal injection of BIIB112 in the antecedent study 274RP101 (NCT03116113) will be enrolled. This is a follow-up study, investigational product was administered in the previous study.

Group Type EXPERIMENTAL

BIIB112

Intervention Type GENETIC

Administered as specified in the treatment arm.

Untreated

Untreated participants who served as controls in the antecedent study 273CH301 (NCT03496012), investigating treatment with BIIB111, will be enrolled. This is a follow-up study, participants will not be administered study medication nor receive a sham surgery.

Group Type NO_INTERVENTION

No interventions assigned to this group

Interventions

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BIIB111

Administered as specified in the treatment arm.

Intervention Type GENETIC

BIIB112

Administered as specified in the treatment arm.

Intervention Type GENETIC

Other Intervention Names

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AAV2-REP1 rAAV2-REP1 AAV8-RPGR

Eligibility Criteria

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Inclusion Criteria

CHM Participants

a. Have participated in and exited from an interventional study that investigated the safety and efficacy of a sub-retinal injection of BIIB111 for CHM.

XLRP Participants

a. Have received a sub-retinal injection of BIIB112 for XLRP and have exited an antecedent study.

Exclusion Criteria

Participants are not eligible for study participation if they meet the following exclusion criterion.

a. In the opinion of the Investigator and/or the Sponsor, it is not in the participant's best interest to participate in the study.
Minimum Eligible Age

18 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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NightstaRx Ltd, a Biogen Company

OTHER

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Medical Director

Role: STUDY_DIRECTOR

Biogen

Locations

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UCLA - Jules Stein Eye Institute

Los Angeles, California, United States

Site Status

Vitreo Retinal Associates PA - The Millennium Center

Gainesville, Florida, United States

Site Status

University of Miami

Miami, Florida, United States

Site Status

Johns Hopkins Hospital

Baltimore, Maryland, United States

Site Status

MEEI Massachusets Eye and Ear Infirmary

Boston, Massachusetts, United States

Site Status

Columbia University Medical Center

New York, New York, United States

Site Status

Cincinnati Eye Institute - Blue Ash

Cincinnati, Ohio, United States

Site Status

OHSU - Casey Eye Institute

Portland, Oregon, United States

Site Status

Retina Foundation of the Southwest

Dallas, Texas, United States

Site Status

University of Wisconsin School of Medicine

Madison, Wisconsin, United States

Site Status

Instituto Genetica Ocular

São Paulo, , Brazil

Site Status

The Northern Alberta Clinical Trials and Research Centre

Edmonton, Alberta, Canada

Site Status

The University of British Columbia - Eye Care Centre

Vancouver, British Columbia, Canada

Site Status

McGill University Health Centre

Montreal, Quebec, Canada

Site Status

Rigshospitalet-Glostrup, Oejenafdelingen

Glostrup Municipality, , Denmark

Site Status

Helsinki University Central Hospital (HUCH)

Helsinki, , Finland

Site Status

CHU Montpellier - Saint Eloi

Montpellier, , France

Site Status

Centre Hospitalier National d Ophtalmologie (CHNO) des Quinze-Vingts

Paris, , France

Site Status

Universitäts-Augenklinik Bonn

Bonn, , Germany

Site Status

Universitats Klinikum Tubingen - Institute for Ophthalmic Research

Tübingen, , Germany

Site Status

Radboudumc

Nijmegen, , Netherlands

Site Status

Moorfields Eye Hospital

London, , United Kingdom

Site Status

Manchester Royal Eye Hopsital

Manchester, , United Kingdom

Site Status

John Radcliffe Hospital

Oxford, , United Kingdom

Site Status

Southampton General Hospital

Southampton, , United Kingdom

Site Status

Countries

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United States Brazil Canada Denmark Finland France Germany Netherlands United Kingdom

Other Identifiers

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2017-003104-42

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

273CH201

Identifier Type: -

Identifier Source: org_study_id

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