Observation, Combination Chemotherapy, Radiation Therapy, and/or Autologous Stem Cell Transplant in Treating Young Patients With Neuroblastoma

NCT ID: NCT00410631

Last Updated: 2013-08-07

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

UNKNOWN

Clinical Phase

PHASE3

Total Enrollment

642 participants

Study Classification

INTERVENTIONAL

Study Start Date

2004-10-31

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

RATIONALE: Drugs used in chemotherapy work in different ways to stop the growth of tumor cells, either by killing the cells or by stopping them from dividing. Giving combination chemotherapy may kill more tumor cells. Radiation therapy uses high-energy x-rays to kill tumor cells. An autologous stem cell transplant may be able to replace blood-forming cells that were destroyed by chemotherapy and radiation therapy. This may allow more chemotherapy to be given so that more tumor cells are killed. Sometimes, after surgery, the tumor may not need more treatment until it progresses. In this case, observation may be sufficient. It is not yet known whether observation is more effective than combination chemotherapy, radiation therapy, and/or autologous stem cell transplant in treating neuroblastoma.

PURPOSE: This randomized phase III and phase IV trial is studying observation, combination chemotherapy, radiation therapy, and/or autologous stem cell transplant to compare how well they work in treating young patients with neuroblastoma.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

OBJECTIVES:

Primary

* Determine the event-free survival (EFS) of younger patients with newly diagnosed neuroblastoma categorized in the low-risk group (LRG) who undergo observation only or receive combination chemotherapy.
* Compare the EFS rate in patients with neuroblastoma categorized in the medium-risk group (MRG) treated with combination induction therapy, maintenance therapy, and consolidation therapy with that of a historical control group.
* Compare the EFS in patients with neuroblastoma categorized in the high-risk group (HRG) treated with standard vs experimental induction therapy followed by autologous stem cell transplantation and consolidation therapy.

Secondary

* Determine the locoregional EFS of patients in the LRG, MRG, or HRG.
* Determine the overall survival of these patients.
* Determine the extent of initial surgery, the extent or impact of best surgery, and surgery-related complications in these patients.
* Determine the time to transition to stage 4 disease in patients in the LRG or MRG.
* Determine the time to a locoregional event in patients in the LRG or HRG.
* Determine the time from diagnosis to an event in patients in the LRG.
* Determine the time from the beginning of regression to an adverse event in patients in the LRG.
* Determine the time to the beginning of primary tumor regression in patients in the LRG.
* Determine the time to the normalization of tumor markers in patients in the LRG.
* Determine the time to no evidence of disease in patients in the LRG with stage 4S disease.
* Assess the status of the primary tumor at 12 months and the best status of the primary tumor within 12 months in patients in the LRG.
* Determine the need for chemotherapy to control progression and the intensity of therapy required in patients in the LRG.
* Determine the acute and late side effects of external-beam radiotherapy in patients in the MRG or HRG.
* Determine the response to induction therapy in patients in the HRG.
* Assess early response after 2 courses of induction therapy in patients in the HRG.
* Determine the toxicity during induction courses 1 and 2 and the frequency of grade 3 or 4 toxicity during induction therapy in patients in the HRG.
* Assess the efficacy of iodine I 131 metaiodobenzylguanidine (MIBG) therapy, in terms of activity and whole body dose, in patients in the HRG.
* Assess molecular markers (e.g., chromosome 1p, chromosome 11q, neuroblastoma gene chip) in these patients.

OUTLINE: This is a prospective, historically controlled, randomized, open-label, multicenter study. Patients are stratified according to disease risk (low-risk vs medium-risk vs high-risk).

* Low-risk group: Patients undergo complete staging 3 months after initial surgery. Patients with no progression are observed for 12 months (for patients over 1 year of age) or until the end of the second year of life (for patients 1 year of age or younger). Patients with localized progression or threatening symptoms undergo N4 chemotherapy comprising doxorubicin hydrochloride IV over 30 minutes and vincristine IV on days 1, 3, and 5 and cyclophosphamide IV over 30 minutes on days 1-7. Treatment repeats every 21 days for up to 4 courses. Patients are reassessed after each course of N4 chemotherapy. Patients achieving stable disease or tumor regression at any point discontinue N4 chemotherapy and undergo observation. Patients with persistent progressive disease after 4 courses of N4 chemotherapy proceed to treatment as in the medium-risk group. Patients who progress to stage 4 disease after initial surgery proceed to treatment as in the medium-risk group (for patients 1 year of age or younger and no indication of stage 4S disease) or high-risk group (for patients over 1 year of age).
* Medium-risk group: Patients receive induction therapy followed by maintenance therapy and consolidation therapy.

* Induction therapy: Patients\* receive N5 chemotherapy comprising cisplatin IV continuously over 96 hours and etoposide phosphate IV continuously over 96 hours on days 1-4, vindesine IV over 1 hour on day 1, and filgrastim (G-CSF) subcutaneously (SC) beginning on day 9 and continuing until blood counts recover. Patients then receive N6 chemotherapy comprising vincristine IV over 1 hour on days 1 and 8, dacarbazine IV over 1 hour and ifosfamide IV continuously over 120 hours on days 1-5, doxorubicin hydrochloride IV over 4 hours on days 6 and 7, and G-CSF beginning on day 10 and continuing until blood counts recover. Treatment repeats every 21 days alternating between N5 and N6 chemotherapy for up to 6 total courses (3 courses of N5 and N6 each). Patients then proceed to maintenance therapy.

NOTE: \*Patients under 6 months of age receive up to 4 courses of N4 chemotherapy (as in the low-risk group) instead of N5/N6 chemotherapy until they reach 6 months of age.

Patients with active residual tumor after induction chemotherapy undergo external-beam radiotherapy (EBRT) for up to 25 fractions concurrently with maintenance chemotherapy. Secondary surgery for resection of the primary tumor is attempted after course 4 or 6 of the induction therapy and before EBRT.

* Maintenance therapy: Patients receive N7 chemotherapy comprising cyclophosphamide orally or IV over 1 hour on days 1-8. Treatment repeats every 21 days for up to 4 courses in the absence of disease progression or unacceptable toxicity.
* Consolidation therapy: Beginning 21 days after completion of maintenance therapy, patients receive oral isotretinoin 2-3 times daily on days 1-14. Treatment repeats every 28 days for up to 6 courses in the absence of unacceptable toxicity. Patients then receive 3 additional courses after 3-months of rest.

* High-risk group: Patients receive induction therapy followed by autologous stem cell transplantation (ASCT) and consolidation therapy.
* Induction therapy: Patients 1 year of age and over are randomized to 1 of 2 treatment arms. Patients under 1 year of age do not undergo randomization; instead they are assigned to arm I.

* Arm I (standard): Patients\* receive N5 and N6 chemotherapy as in induction therapy for the medium-risk group.
* Arm II (experimental): Patients receive N8 chemotherapy comprising topotecan hydrochloride IV continuously over 168 hours and cyclophosphamide IV over 1 hour on days 1-7, etoposide IV over 1 hour on days 8-10, and G-CSF SC beginning on day 12 and continuing until blood counts recover. Treatment repeats every 21 days for 2 courses. Patients then receive N5 and N6 chemotherapy as in induction therapy for the medium-risk group.

In both arms, patients with active residual primary tumor after 6 courses of induction therapy undergo iodine I 131 metaiodobenzylguanidine (MIBG)\*\* radiotherapy (before ASCT). Patients also undergo EBRT for up to 25 fractions after ASCT. Secondary surgery for resection of the primary tumor is attempted after course 4 or 6 of induction therapy and before radiotherapy.

NOTE: \*Patients under 6 months of age receive up to 4 courses of N4 chemotherapy (as in the low-risk group) instead of N5/N6 chemotherapy until they reach 6 months of age.

NOTE: \*\*Patients with MIBG-negative disease undergo EBRT only.

* Conditioning followed by ASCT: Patients receive melphalan IV over 30 minutes on days -8 to -5, etoposide phosphate IV over 4 hours on day -4, and carboplatin IV over 1 hour on days -4 to -2. Patients undergo ASCT on day 0. Patients receive G-CSF SC beginning on day 2 and continuing until blood counts recover.
* Consolidation therapy: Beginning 30 days after ASCT, patients receive isotretinoin\* as in consolidation therapy for the medium-risk group.

NOTE: \*Isotretinoin is discontinued during EBRT and restarted 1 week after completion of EBRT.

After completion of study treatment, patients are followed periodically.

PROJECTED ACCRUAL: A total of 642 patients will be accrued for this study.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Neuroblastoma

Keywords

Explore important study keywords that can help with search, categorization, and topic discovery.

localized resectable neuroblastoma localized unresectable neuroblastoma regional neuroblastoma stage 4S neuroblastoma disseminated neuroblastoma recurrent neuroblastoma

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

RANDOMIZED

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

filgrastim

Intervention Type BIOLOGICAL

carboplatin

Intervention Type DRUG

cisplatin

Intervention Type DRUG

cyclophosphamide

Intervention Type DRUG

dacarbazine

Intervention Type DRUG

doxorubicin hydrochloride

Intervention Type DRUG

etoposide phosphate

Intervention Type DRUG

ifosfamide

Intervention Type DRUG

isotretinoin

Intervention Type DRUG

melphalan

Intervention Type DRUG

topotecan hydrochloride

Intervention Type DRUG

vincristine sulfate

Intervention Type DRUG

vindesine

Intervention Type DRUG

autologous hematopoietic stem cell transplantation

Intervention Type PROCEDURE

conventional surgery

Intervention Type PROCEDURE

peripheral blood stem cell transplantation

Intervention Type PROCEDURE

iobenguane I 131

Intervention Type RADIATION

radiation therapy

Intervention Type RADIATION

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

DISEASE CHARACTERISTICS:

* Diagnosis of neuroblastoma by histology using tumor tissue or as evidenced by the presence of distinct neuroblastoma cells in the bone marrow AND elevated catecholamine metabolites (i.e., homovanillic acid \[HVA\] and vanillylmandelic acid \[VMA\]) in blood or urine

* Newly diagnosed disease (for patients in the low-risk group)
* Diagnosis from tumor tissue (for patients in the medium-risk group)
* Meets criteria for 1 of the following risk groups:

* Low-risk group

* No MYCN amplification AND meets 1 of the following criteria:

* Stage 1 disease
* Stage 2 disease with no chromosome 1p deletion or imbalance
* Stage 3 disease with no chromosome 1p deletion or imbalance (for patients \< 2 years of age)
* Stage 4S disease (for patients \< 1 year of age)
* Medium-risk group

* No MYCN amplification AND meets 1 of the following criteria:

* Stage 2 disease with chromosome 1p deletion or imbalance
* Stage 3 disease with chromosome 1p deletion or imbalance

* Any chromosome 1p status (for patients ≥ 2 years of age)
* Stage 4 disease (for patients \< 1 year of age)
* High-risk group, meeting 1 of the following criteria:

* Any stage disease with MYCN amplification

* Any MYCN status (for patients ≥ 1 year of age)

PATIENT CHARACTERISTICS:

* Not pregnant or nursing
* Negative pregnancy test
* Fertile patients must use effective contraception

PRIOR CONCURRENT THERAPY:

* No prior nephrectomy or other mutilating surgery as initial surgery (for patients in the low-risk group)
* No other concurrent anticancer therapy
Maximum Eligible Age

21 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

German Society for Pediatric Oncology and Hematology GPOH gGmbH

OTHER

Sponsor Role lead

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Frank Berthold, MD

Role: STUDY_CHAIR

Children's Hospital Medical Center, Cincinnati

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Kinderklinik - Universitaetsklinikum Aachen

Aachen, , Germany

Site Status RECRUITING

Klinikum Augsburg

Augsburg, , Germany

Site Status RECRUITING

Klinikum am Bamberg

Bamberg, , Germany

Site Status RECRUITING

Klinikum Bayreuth

Bayreuth, , Germany

Site Status RECRUITING

Helios Klinikum Berlin

Berlin, , Germany

Site Status RECRUITING

Charite University Hospital - Campus Virchow Klinikum

Berlin, , Germany

Site Status RECRUITING

Evangelisches Krankenhauus Bielfeld

Biefeld, , Germany

Site Status RECRUITING

Kinderklinik der Universitaet Bonn

Bonn, , Germany

Site Status RECRUITING

Staedtisches Klinikum - Howedestrase

Braunschweig, , Germany

Site Status RECRUITING

Klinikum Bremen-Mitte

Bremen, , Germany

Site Status RECRUITING

Allgemeinen Krankenhaus Celle Kinderklinik

Celle, , Germany

Site Status RECRUITING

Klinikum Chemnitz gGmbH

Chemnitz, , Germany

Site Status RECRUITING

Klinikum Coburg

Coburg, , Germany

Site Status RECRUITING

Kliniken der Stadt Koeln gGmbH - Kinderkrankenhaus Riehl

Cologne, , Germany

Site Status RECRUITING

Children's Hospital

Cologne, , Germany

Site Status RECRUITING

Carl - Thiem - Klinkum Cottbus

Cottbus, , Germany

Site Status RECRUITING

Vestische Kinderklinik

Datteln, , Germany

Site Status RECRUITING

Klinikum Lippe - Detmold

Detmold, , Germany

Site Status RECRUITING

Klinikum Dortmund

Dortmund, , Germany

Site Status RECRUITING

Universitatsklinikum Carl Gustav Carus

Dresden, , Germany

Site Status RECRUITING

Klinikum Duisburg

Duisburg, , Germany

Site Status RECRUITING

Universitaets - Frauenklinik, Duesseldorf

Düsseldorf, , Germany

Site Status RECRUITING

Helios Klinikum Erfurt

Erfurt, , Germany

Site Status RECRUITING

Universitaets - Kinderklinik

Erlangen, , Germany

Site Status RECRUITING

Universitaetsklinikum Essen

Essen, , Germany

Site Status RECRUITING

Klinikum der J.W. Goethe Universitaet

Frankfurt, , Germany

Site Status RECRUITING

Universitaetskinderklinik - Universitaetsklinikum Freiburg

Freiburg im Breisgau, , Germany

Site Status RECRUITING

Kinderklinik

Giessen, , Germany

Site Status RECRUITING

Universitaetsklinikum Goettingen

Göttingen, , Germany

Site Status RECRUITING

Universitats - Kinderklinik

Greiswald, , Germany

Site Status RECRUITING

Universitaetsklinikum Halle

Halle, , Germany

Site Status RECRUITING

Krankenhaus St. Elisabeth und St. Barbara

Halle, , Germany

Site Status RECRUITING

University Medical Center Hamburg - Eppendorf

Hamburg, , Germany

Site Status RECRUITING

Kinderkrankenhaus auf der Bult

Hanover, , Germany

Site Status RECRUITING

Medizinische Hochschule Hannover

Hanover, , Germany

Site Status RECRUITING

Universitaets-Kinderklinik Heidelberg

Heidelberg, , Germany

Site Status RECRUITING

SLK - Kliniken Heilbronn GmbH - Klinikum am Gesundbrunnen

Heilbronn, , Germany

Site Status RECRUITING

Gemeinschaftskrankenhaus

Herdecke, , Germany

Site Status RECRUITING

Universitaetsklinikum des Saarlandes

Homburg, , Germany

Site Status RECRUITING

Universitaets - Kinderklinik

Jena, , Germany

Site Status RECRUITING

Universitaets - Kinderklinik

Jena, , Germany

Site Status RECRUITING

Staedtisches Klinikum Karlsruhe gGmbH

Karlsruhe, , Germany

Site Status RECRUITING

Kinderkrankenhaus Park Schoenfeld

Kassel, , Germany

Site Status RECRUITING

Klinikum Kassel

Kassel, , Germany

Site Status RECRUITING

University Hospital Schleswig-Holstein - Kiel Campus

Kiel, , Germany

Site Status RECRUITING

Klinikum Kemperhof Koblenz

Koblenz, , Germany

Site Status RECRUITING

Klinikum Krefeld GmbH

Krefeld, , Germany

Site Status RECRUITING

St. Annastift Krankenhaus

Ludwigshafen, , Germany

Site Status RECRUITING

Universitaets - Kinderklinik - Luebeck

Lübeck, , Germany

Site Status RECRUITING

Universitatsklinikum der MA

Magdeburg, , Germany

Site Status RECRUITING

Johannes Gutenberg University

Mainz, , Germany

Site Status RECRUITING

Staedtisches Klinik - Kinderklinik

Mannheim, , Germany

Site Status RECRUITING

Universitaets - Kinderklinik

Marburg, , Germany

Site Status RECRUITING

Klinikum Minden

Minden, , Germany

Site Status RECRUITING

Krankenhaus Muenchen Schwabing

Munich, , Germany

Site Status RECRUITING

Dr. von Haunersches Kinderspital der Universitaet Muenchen

Munich, , Germany

Site Status RECRUITING

Klinikum der Universitaet Muenchen - Grosshadern Campus

Munich, , Germany

Site Status RECRUITING

Staedtisches Krankenhaus Muenchen - Harlaching

Munich, , Germany

Site Status RECRUITING

University of Muenster

Münster, , Germany

Site Status RECRUITING

Klinikum Neubrandenburg

Neubrandenburg, , Germany

Site Status RECRUITING

Kinderklinik Kohlhof

Neunkirchen, , Germany

Site Status RECRUITING

Cnopf'sche Kinderklinik

Nuremberg, , Germany

Site Status RECRUITING

Klinikum Oldenburg

Oldenburg, , Germany

Site Status RECRUITING

Klinik St. Hedwig-Kinderklinik

Regensburg, , Germany

Site Status RECRUITING

Kinderklinik - Universitaetsklinikum Rostock

Rostock, , Germany

Site Status RECRUITING

Johanniter-Kinderklinik

Sankt Augustin, , Germany

Site Status RECRUITING

Kinderklink Siegen Deutsches Rotes Kreuz

Siegen, , Germany

Site Status RECRUITING

Olgahospital

Stuttgart, , Germany

Site Status RECRUITING

Krankenanstalt Mutterhaus der Borromaerinnen

Trier, , Germany

Site Status RECRUITING

Universitaets-Kinderklinik

Tübingen, , Germany

Site Status RECRUITING

Universitaetsklinikum Tuebingen

Tübingen, , Germany

Site Status RECRUITING

Comprehensive Cancer Center Ulm at Universitaetsklinikum Ulm

Ulm, , Germany

Site Status RECRUITING

Reinhard-Nieter-Krankenhaus

Wilhelmshaven, , Germany

Site Status RECRUITING

Helios Kliniken Wuppertal University Hospital

Wuppertal, , Germany

Site Status RECRUITING

Universitaets - Kinderklinik Wuerzburg

Würzburg, , Germany

Site Status RECRUITING

Kantonsspital Aarau

Aarau, , Switzerland

Site Status RECRUITING

Universitaets-Kinderspital beider Basel

Basel, , Switzerland

Site Status RECRUITING

Kinderspital Luzern

Lucerne, , Switzerland

Site Status RECRUITING

Ostschweizer Kinderspital

Sankt Gallen, , Switzerland

Site Status RECRUITING

University Children's Hospital

Zurich, , Switzerland

Site Status RECRUITING

Countries

Review the countries where the study has at least one active or historical site.

Germany Switzerland

Facility Contacts

Find local site contact details for specific facilities participating in the trial.

R. Mertens, MD, PhD

Role: primary

Astrid Gnekow

Role: primary

Gloeckel, MD

Role: primary

T. Rupprecht

Role: primary

L. Wickmann, MD

Role: primary

Gunter Henze

Role: primary

N. Jorch, MD

Role: primary

Udo Bode, MD

Role: primary

Contact Person

Role: primary

Arnulf Pekrun, MD, PhD

Role: primary

Martin Kirschstein, MD

Role: primary

Krause, MD

Role: primary

Roland Frank, MD

Role: primary

Contact Person

Role: primary

Frank Berthold, MD

Role: primary

D Mobius, MD

Role: primary

W. Andler, MD

Role: primary

Klaus Wesseler, MD

Role: primary

Heidi Olscheswski, MD

Role: primary

M. Suttorp, MD

Role: primary

Ruef, MD

Role: primary

Dilloo, MD

Role: primary

Axel Sauerbrey, MD

Role: primary

W. Holter, MD

Role: primary

Bernhard Kremens, MD

Role: primary

Thomas Klingebiel, MD

Role: primary

Charlotte Niemeyer, MD

Role: primary

Alfred Reiter, MD

Role: primary

Lothar Schweigerer, MD

Role: primary

James F. Beck, MD

Role: primary

Dieter Koerholz, MD

Role: primary

G. Guenther, MD

Role: primary

Rudolf Erttmann, MD

Role: primary

U. Hofmann, MD

Role: primary

Karl Welte, MD

Role: primary

Andreas E. Kulozik, MD, PhD

Role: primary

Full, MD

Role: primary

Christoph Tautz, MD

Role: primary

Norbert Graf

Role: primary

Contact Peron

Role: primary

Felix Zintl, MD

Role: primary

A. Leipold

Role: primary

M. L. Wright, MD

Role: primary

Martina Rodehueser, MD

Role: primary

A. Claviez, MD

Role: primary

M. Rister, MD

Role: primary

S. Volpel, MD

Role: primary

Barbara Selle, MD

Role: primary

Peter P. Bucsky, MD

Role: primary

Uwe Mittler, MD

Role: primary

P. Gutjahr, MD

Role: primary

M. Duerken

Role: primary

H. Christiansen, MD

Role: primary

W Tilmann, MD

Role: primary

Stefan Burdach, MD, PhD

Role: primary

Arndt Borkhardt

Role: primary

Schulz, MD

Role: primary

Contact Person

Role: primary

Contact Person

Role: primary

H. J. Feickert, MD, PhD

Role: primary

Contact Person

Role: primary

W. Scheurlen

Role: primary

Hermann Mueller, MD

Role: primary

Ove Peters

Role: primary

Carl Friedrich Classen, MD, PD

Role: primary

Roswitha Dickerhoff, MD

Role: primary

Rainer Burghard, MD

Role: primary

Stefan Bielack, MD

Role: primary

Wolfgang Rauh, MD

Role: primary

Contact Person

Role: primary

Rupert Handgretinger, MD

Role: primary

Klaus M. Debatin, MD

Role: primary

Liebner, MD

Role: primary

K. Sinha, MD

Role: primary

P. G. Schlegel, MD

Role: primary

R. Angst

Role: primary

Thomas Kuhne, MD

Role: primary

U. Caflisch, MD

Role: primary

Jeanette Greiner, MD

Role: primary

Felix Niggli, MD

Role: primary

References

Explore related publications, articles, or registry entries linked to this study.

Decarolis B, Simon T, Krug B, Leuschner I, Vokuhl C, Kaatsch P, von Schweinitz D, Klingebiel T, Mueller I, Schweigerer L, Berthold F, Hero B. Treatment and outcome of Ganglioneuroma and Ganglioneuroblastoma intermixed. BMC Cancer. 2016 Jul 27;16:542. doi: 10.1186/s12885-016-2513-9.

Reference Type DERIVED
PMID: 27465021 (View on PubMed)

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

CDR0000517312

Identifier Type: REGISTRY

Identifier Source: secondary_id

EU-20661

Identifier Type: -

Identifier Source: secondary_id

GPOH-NB2004

Identifier Type: -

Identifier Source: org_study_id