Mucopolysaccharidosis (MPS) VI Clinical Surveillance Program (CSP)

NCT ID: NCT00214773

Last Updated: 2021-04-05

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Total Enrollment

237 participants

Study Classification

OBSERVATIONAL

Study Start Date

2005-07-31

Study Completion Date

2020-05-01

Brief Summary

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The objectives of this program are: to further characterize the natural progression of MPS VI disease; to generate and disseminate information on the care and management of MPS VI patients to clinical and medical professionals; to provide a resource to physicians and patients by providing information for optimizing patient care based on aggregate data; to characterize the clinical response to long-term Naglazyme® (galsulfase) treatment; to further characterize the long-term safety of Naglazyme® treatment.

Detailed Description

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Conditions

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Mucopolysaccharidosis VI (MPS VI, Maroteaux-Lamy Syndrome)

Study Design

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Observational Model Type

COHORT

Study Time Perspective

PROSPECTIVE

Study Groups

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Observational

No intervention. This is an observational program.

No interventions assigned to this group

Eligibility Criteria

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Inclusion Criteria

All patients must meet the following criteria to qualify for enrollment in the CSP:

* Patient or patient's parent or legal guardian, if child is under 18 year old or is unable to consent, has provided a signed Patient Information and Authorization Form.
* Patient has laboratory results confirming a diagnosis of MPS VI disease based on detection of deficient ARSB activity (on fibroblasts, leucocytes or dried blood spots)and/or abnormality on the ARSB gene.
* Patient is willing to undergo general assessments to establish baseline data or permits physician to enter assessment data recorded prior to CSP entry if available in the patient's medical records. General assessments include: urinary GAG level, urinary protein level, serum sample for antibody levels, height, weight, and patient history.
Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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BioMarin Pharmaceutical

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Julie Johnson

Role: STUDY_DIRECTOR

BioMarin Pharmaceutical

Locations

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University of California, Irvine

Irvine, California, United States

Site Status

Children's Hospital of Los Angeles

Los Angeles, California, United States

Site Status

Children's Hospital and Research Center Oakland

Oakland, California, United States

Site Status

Emory University

Decatur, Georgia, United States

Site Status

Ann and Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, United States

Site Status

Indiana University School of Medicine

Indianapolis, Indiana, United States

Site Status

Baton Rouge Clinic

Baton Rouge, Louisiana, United States

Site Status

Tulane University Medical Center

New Orleans, Louisiana, United States

Site Status

Johns Hopkins Univeristy School of Medicine

Baltimore, Maryland, United States

Site Status

Children's Health Care

Minneapolis, Minnesota, United States

Site Status

University of Minnesota - Fairview University Medical Center

Minneapolis, Minnesota, United States

Site Status

Children's Mercy Hospital

Kansas City, Missouri, United States

Site Status

St. Joseph's Healthcare

Paterson, New Jersey, United States

Site Status

New York University

New York, New York, United States

Site Status

Fullerton Genetic Center

Asheville, North Carolina, United States

Site Status

Carolinas Medical Center

Charlotte, North Carolina, United States

Site Status

Oregon Health and Science University

Portland, Oregon, United States

Site Status

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

Children's Hospital of Pittsburgh

Pittsburgh, Pennsylvania, United States

Site Status

Sioux Valey Children's Speciality Clinics

Sioux Falls, South Dakota, United States

Site Status

University of Utah Medical Center

Salt Lake City, Utah, United States

Site Status

Children's Hospital of the King's Daughters

Norfolk, Virginia, United States

Site Status

Seattle Children's Hospital

Seattle, Washington, United States

Site Status

Westmead Hospital

Wentworthville, New South Wales, Australia

Site Status

Royal Children's Hospital, Brisbane

Brisbane, Queensland, Australia

Site Status

Women and Children's Hospital

Adelaide, South Australia, Australia

Site Status

Royal Children's Hospital

Parkville, Victoria, Australia

Site Status

Princess Margaret Hospital for Children

Subiaco, Western Australia, Australia

Site Status

LKH-Universitätsklinik Graz, Kinderklinik

Graz, Styria, Austria

Site Status

Institute of Pathology and Genetics, Metabolic Unit

Charleroi, Wallonia, Belgium

Site Status

Hôpital Femme Mère Enfant

Bron, Auvergne-Rhône-Alpes, France

Site Status

Hopital Necker - Enfants Malades

Paris, , France

Site Status

Oberarzt Pädiatrie

Hanover, Lower Saxony, Germany

Site Status

Universitatsklinikum Freiburg, Klinik II

Kammin, Mecklenburg-Vorpommern, Germany

Site Status

Universitätsmedizin

Mainz, Rheinland-Pfalz RP, Germany

Site Status

Charité-Universitätsmedizin Berlin

Berlin, , Germany

Site Status

Universitätsklinikum Hamburg Eppendorf

Hamburg, , Germany

Site Status

MidWestern Regional Hospital

Limerick, , Ireland

Site Status

Azienda Ospedaliero Universitaria

Cibali, Catania, Italy

Site Status

Department of Woman's and Child's Health

Padua, Veneto, Italy

Site Status

Università Milano Bicocca, Resp. Centro "Fondazione Mariani"

Monza, , Italy

Site Status

Vilnius University Hospital, Santariskiu Klinikos

Vilnius, , Lithuania

Site Status

Rotterdam University Hospital - Sophia's Children's Hospital

Rotterdam, , Netherlands

Site Status

Hospital de Sao Joao, Unidae de Doencas Metabolicas

Porto, , Portugal

Site Status

Astrid Lindgrens Children's Hospital

Stockholm, , Sweden

Site Status

Queen Elizabeth Hospital, University Hospitals Birmingham NHS

Birmingham, , United Kingdom

Site Status

Birmingham Children's Hospital, Steelhouse

Birmingham, , United Kingdom

Site Status

Great Ormond Street Hospital For Children, NHS Foundation Trust

London, , United Kingdom

Site Status

St Mary's Hospital, Willink Biochemical Genetics Unit

Manchester, , United Kingdom

Site Status

Salford Royal Hospital NHS Trust

Salford, , United Kingdom

Site Status

Countries

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United States Australia Austria Belgium France Germany Ireland Italy Lithuania Netherlands Portugal Sweden United Kingdom

References

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Solanki GA, Sun PP, Martin KW, Hendriksz CJ, Lampe C, Guffon N, Hung A, Sisic Z, Shediac R, Harmatz PR; CSP Study Group. Cervical cord compression in mucopolysaccharidosis VI (MPS VI): Findings from the MPS VI Clinical Surveillance Program (CSP). Mol Genet Metab. 2016 Aug;118(4):310-8. doi: 10.1016/j.ymgme.2016.06.001. Epub 2016 Jun 3.

Reference Type DERIVED
PMID: 27339555 (View on PubMed)

Related Links

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http://www.BRMN.com

BioMarin Pharmaceutical Inc Website

Other Identifiers

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MPSVI CSP

Identifier Type: -

Identifier Source: org_study_id

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