Study of BMN 349 Single Dose in PiZZ and PiMZ/MASH Adult Participants

NCT ID: NCT06738017

Last Updated: 2025-09-08

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1

Total Enrollment

12 participants

Study Classification

INTERVENTIONAL

Study Start Date

2025-02-21

Study Completion Date

2025-09-30

Brief Summary

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The goal of this clinical trial is to assess the safety and tolerability of a single oral dose of BMN 349 in participants with PiZZ or PiMZ/MASH.

Primary outcome measures include incidence of any adverse events (including serious adverse events, dose limit toxicities, and adverse events of special interest), incidence of any laboratory test abnormalities, incidence of lung function test abnormalities and 12-lead ECG parameters.

Participants will receive a single dose of either BMN 349 or placebo and then monitored for safety and tolerability.

Detailed Description

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Conditions

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Alpha 1-Antitrypsin Deficiency

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

TRIPLE

Participants Caregivers Investigators

Study Groups

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Group A (PiZZ)

5:1 (349:Placebo)

Group Type OTHER

BMN 349

Intervention Type DRUG

250mg oral tablet

Placebo

Intervention Type DRUG

250mg oral tablet

Group B (PiMZ)

5:1 (349:Placebo)

Group Type OTHER

BMN 349

Intervention Type DRUG

250mg oral tablet

Placebo

Intervention Type DRUG

250mg oral tablet

Interventions

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BMN 349

250mg oral tablet

Intervention Type DRUG

Placebo

250mg oral tablet

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Participants must have confirmation of PiZZ or PiMZ genotype
* Females and males, of any race, 18 to 75 years of age
* Nonsmokers, defined as not using tobacco or nicotine-containing products for at least 6 months prior to Screening

Exclusion Criteria

* International normalized ratio (INR) \> 1.2
* Alanine aminotransferase (ALT) and aspartate aminotransferase (AST) levels \> 125 U/L
* Current or recent use of AAT augmentation therapy
* Participants with recent (last 3 months) diagnosis of pneumonia
Minimum Eligible Age

18 Years

Maximum Eligible Age

75 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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BioMarin Pharmaceutical

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Medical Director, MD

Role: STUDY_DIRECTOR

BioMarin Pharmaceutical

Locations

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University of California, San Diego

San Diego, California, United States

Site Status RECRUITING

Saint Louis University

St Louis, Missouri, United States

Site Status RECRUITING

Medpace Clinical Pharmacology Unit

Cincinnati, Ohio, United States

Site Status RECRUITING

The Medical University of South Carolina

Charleston, South Carolina, United States

Site Status RECRUITING

NHS Lothian

Edinburgh, UK, United Kingdom

Site Status RECRUITING

Royal Free London NHS Foundation Trust

London, UK, United Kingdom

Site Status RECRUITING

Nottingham University Hospitals

Nottingham, UK, United Kingdom

Site Status NOT_YET_RECRUITING

University Hospital Southampton NHS Foundation Trust

Southampton, UK, United Kingdom

Site Status RECRUITING

Countries

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United States United Kingdom

Central Contacts

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Trial Specialist

Role: CONTACT

1-800-983-4587

Facility Contacts

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Egbert Madamba

Role: primary

858-246-2227

Jeffery Teckman Principal Investigator, MD

Role: primary

314-577-5647

Tina M Ramey

Role: primary

513-579-9911 ext. 12576

Kristin Neff Primary CRC

Role: primary

843-792-1219

Ellyse Kilarski

Role: primary

+44 (0131) 242 1289

Role: primary

Stephen Ryder, MD

Role: primary

+44(0)115 9249924

AATD Research Team

Role: primary

023 8120 4479

Other Identifiers

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349-102

Identifier Type: -

Identifier Source: org_study_id

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