A Retrospective and Prospective Natural History of Genetic Vasculopathies

NCT ID: NCT06552052

Last Updated: 2025-05-08

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

RECRUITING

Total Enrollment

50 participants

Study Classification

OBSERVATIONAL

Study Start Date

2024-05-08

Study Completion Date

2028-07-31

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

This study will combine retrospective review of medical records from patients with ACTA2 and ongoing collection of clinical data using standardized instruments and intervals on an observational basis from patients with ACTA2.

Patients in cohorts 1-3 will be asked to attend clinic visits in person per the schedule of events. At minimum, the medical records of patients with ACTA2 will be reviewed to record data on aspects of the disease, including disease characteristics and developmental milestones. The study is planned to enroll a total of 100 patients: 7 in cohort 1, 7 in cohort 2, and the remaining in cohorts 3 and 4.

This study is planned to study patients for at least 3 years with the option to continue as long as possible for assessment of disease progression. During their continued study participation, as patients age, they may move into the next cohort. Beyond 3 years the duration of the study with be determined by availability of funding from sponsors.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Multisystemic Smooth Muscle Dysfunction Syndrome ACTA2

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Observational Model Type

COHORT

Study Time Perspective

PROSPECTIVE

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Cohort 1 (29 days - 6 years of age)

1. Patient is between the ages of 29 days - 6 years old
2. Confirmed ACTA2 pathogenic variant
3. Available medical records since birth that permit documentation of disease characteristics and developmental milestone
4. Have two parents and/or legal guardians who are English speaking and are able to read, understand, and sign the informed consent
5. Able to tolerate travel to study site

No interventions assigned to this group

Cohort 2 (7 - 18 years of age)

1. Patient is between the ages of 7 - 18 years old
2. Confirmed ACTA2 pathogenic variant
3. Available medical records since birth that permit documentation of disease characteristics and developmental milestone
4. Have two parents and/or legal guardians who are English speaking and are able to read, understand, and sign the informed consent
5. Able to tolerate travel to study site

No interventions assigned to this group

Cohort 3 (19 - 99 years of age)

1. Patient is between the ages of 19 - 100 years old
2. Confirmed ACTA2 pathogenic variant
3. Available medical records since birth that permit documentation of disease characteristics and developmental milestone
4. Patient, parent and/or legal guardian is English speaking is able to read, understand, and sign the informed consent
5. Able to tolerate travel to study site

No interventions assigned to this group

Cohort 4 (Retrospective - All Ages)

1. Patient of any age, alive or deceased
2. Confirmed ACTA2 pathogenic variant
3. Available medical records since birth that permit documentation of disease characteristics and developmental milestone
4. Patient, parent and/or legal guardian is English speaking and able to read, understand, and sign the informed consent

No interventions assigned to this group

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

* Confirmed ACTA2 pathogenic variant
* Available medical records since birth that permit documentation of disease characteristics and developmental milestone
* Have two parents and/or legal guardians who are English speaking and are able to read, understand, and sign the informed consent
* Able to tolerate travel to study site

* Patient is currently pregnant
Minimum Eligible Age

29 Days

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Massachusetts General Hospital

OTHER

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Patricia Musolino, MD PhD

Dr. Patricia L. Musolino, MD PhD, Principle Investigator

Responsibility Role PRINCIPAL_INVESTIGATOR

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Massachusetts General Hospital

Boston, Massachusetts, United States

Site Status RECRUITING

Countries

Review the countries where the study has at least one active or historical site.

United States

Central Contacts

Reach out to these primary contacts for questions about participation or study logistics.

Anna V Lynch, BA

Role: CONTACT

617-949-6960

Diana Tambala, MD

Role: CONTACT

Facility Contacts

Find local site contact details for specific facilities participating in the trial.

Anna V Lynch, BA

Role: primary

617-949-6960

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

2023P000821

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

GNAO1 Natural History Study
NCT04950946 UNKNOWN
Neurogenetics Patient Registry
NCT02995538 RECRUITING