A Phase 1/2 Trial of SP-101 for the Treatment of Cystic Fibrosis (CF)

NCT ID: NCT06526923

Last Updated: 2024-11-25

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

15 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-09-16

Study Completion Date

2026-12-31

Brief Summary

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This is a Phase 1/2 multicenter, open-label, single dose trial of SP-101 investigational gene therapy in adults with CF who are ineligible for or intolerant to CFTR modulator therapy.

Detailed Description

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This multi-center study is a first-in-human, single ascending dose, Phase 1/2 trial to evaluate the safety, pharmacokinetics, and pharmacodynamics of various dose levels in people with CF who are ineligible or intolerant to CFTR modulator therapy.

Conditions

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Cystic Fibrosis

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

SEQUENTIAL

Single ascending dose
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Cohort 1

Single inhalational administration of SP-101 and doxorubicin Dose 1

Group Type EXPERIMENTAL

SP-101 and doxorubicin Cohort 1

Intervention Type COMBINATION_PRODUCT

Single inhaled dose of SP-101 and doxorubicin Dose 1

Cohort 2

Single inhalational administration of SP-101 and doxorubicin Dose 2

Group Type EXPERIMENTAL

SP-101 and doxorubicin Cohort 2

Intervention Type COMBINATION_PRODUCT

Single inhaled dose of SP-101 and doxorubicin Dose 2

Dose Expansion

Single inhalational administration of SP-101 and doxorubicin Selected Dose

Group Type EXPERIMENTAL

SP-101 and doxorubicin Cohort 1

Intervention Type COMBINATION_PRODUCT

Single inhaled dose of SP-101 and doxorubicin Dose 1

SP-101 and doxorubicin Cohort 2

Intervention Type COMBINATION_PRODUCT

Single inhaled dose of SP-101 and doxorubicin Dose 2

Interventions

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SP-101 and doxorubicin Cohort 1

Single inhaled dose of SP-101 and doxorubicin Dose 1

Intervention Type COMBINATION_PRODUCT

SP-101 and doxorubicin Cohort 2

Single inhaled dose of SP-101 and doxorubicin Dose 2

Intervention Type COMBINATION_PRODUCT

Other Intervention Names

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SP-101 doxorubicin SP-101 doxorubicin

Eligibility Criteria

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Inclusion Criteria

1. Males or females, age 18 to 65 years at Screening Visit, inclusive
2. Diagnosis of CF
3. ppFEV1 value between 50-100% (inclusive)
4. Resting oxygen saturation ≥94% on room air by pulse oximetry 5 . Clinically stable CF disease as assessed by the Investigator and not requiring any new class of interventional treatment within the last 3 months prior to Screening

Exclusion Criteria

1. Any change in established pulmonary treatment (including antibiotics) within 28 days prior to Screening Visit. However, inhaled beta-agonists can be included within 2 weeks prior to Screening Visit.
2. Clinically significant episode of hemoptysis (\>50 mL or ¼ cup or 10 teaspoons per day) within 12 weeks prior to dosing with study drug on Day 1
3. Lung infection with Mycobacterium abscessus associated with a more rapid decline in pulmonary status
4. Currently receiving treatment for active lung infection with Burkholderia cenocepacia or Burkholderia dolosa
5. History of solid organ or hematological transplantation
6. History of clinically significant cirrhosis with or without portal hypertension
7. History of pulmonary hypertension
8. History of cardiotoxicity, a history of known coronary artery disease, and/or existing cardiomyopathy
9. Current active fungal infection (not just a positive culture), acute blood, lung, or bladder infection, clinically significant hepatic or renal dysfunction, and/or viral infection (including human immunodeficiency virus or hepatitis virus B or C) requiring the initiation of new therapy within 30 days prior to Screening
10. History of allergic bronchopulmonary aspergillosis (ABPA)
11. Uncontrolled diabetes mellitus, as evidenced by hemoglobin A1c \>9% at Screening
12. Clinically significant laboratory abnormalities at Screening
13. Subjects with any medical condition or abnormal laboratory result that, in the opinion of the Investigator, will interfere with the safe completion of the study
14. Subjects who received any investigational products within 30 days (or 5 therapeutic half-lives, whichever is longer) prior to Screening
15. Subjects who have previously received any gene therapy agent
16. Subjects with known sensitivity to SP-101, doxorubicin or its excipients
Minimum Eligible Age

18 Years

Maximum Eligible Age

65 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Spirovant Sciences, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Jessica Lee, MPH

Role: STUDY_DIRECTOR

Spirovant Sciences

Locations

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University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status RECRUITING

Boston Children's Hospital, Brigham & Women's Hospital

Boston, Massachusetts, United States

Site Status RECRUITING

Columbia University

New York, New York, United States

Site Status RECRUITING

Hospital at University of Pennsylvania

Philadelphia, Pennsylvania, United States

Site Status RECRUITING

Countries

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United States

Central Contacts

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Spirovant.ClinicalTrials

Role: CONTACT

(267) 805-6747

Facility Contacts

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Taryn McNickle

Role: primary

Monica Ulles

Role: primary

Barbara Djan

Role: primary

Melissa Molter

Role: primary

References

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Excoffon KJDA, Smith MD, Falese L, Schulingkamp R, Lin S, Mahankali M, Narayan PKL, Glatfelter MR, Limberis MP, Yuen E, Kolbeck R. Inhalation of SP-101 Followed by Inhaled Doxorubicin Results in Robust and Durable hCFTRDeltaR Transgene Expression in the Airways of Wild-Type and Cystic Fibrosis Ferrets. Hum Gene Ther. 2024 Sep;35(17-18):710-725. doi: 10.1089/hum.2024.064. Epub 2024 Sep 4.

Reference Type RESULT
PMID: 39155828 (View on PubMed)

Excoffon KJDA, Lin S, Narayan PKL, Sitaraman S, Jimah AM, Fallon TT, James ML, Glatfelter MR, Limberis MP, Smith MD, Guffanti G, Kolbeck R. SP-101, A Novel Adeno-Associated Virus Gene Therapy for the Treatment of Cystic Fibrosis, Mediates Functional Correction of Primary Human Airway Epithelia From Donors with Cystic Fibrosis. Hum Gene Ther. 2024 Sep;35(17-18):695-709. doi: 10.1089/hum.2024.063. Epub 2024 Aug 29.

Reference Type RESULT
PMID: 39155805 (View on PubMed)

Other Identifiers

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CFAAV-001

Identifier Type: -

Identifier Source: org_study_id

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