Phase III Trial of AMX0035 for Amyotrophic Lateral Sclerosis Treatment

NCT ID: NCT05021536

Last Updated: 2024-08-14

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

664 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-10-28

Study Completion Date

2026-01-01

Brief Summary

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The Phoenix Trial is a randomized double blind placebo controlled Phase III trial to evaluate the safety and efficacy of AMX0035 for treatment of ALS

Detailed Description

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AMX0035 is a combination therapy designed to reduce neuronal death through blockade of key cellular death pathways originating in the mitochondria and endoplasmic reticulum (ER). This clinical trial is designed to demonstrate that treatment is safe, tolerable, and able to slow decline in function as measured by the ALSFRS-R and survival over 48 week. The trial will also assess the effects of AMX0035 on slow vital capacity, quality of life and plasma biomarkers of ALS.

Conditions

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Amyotrophic Lateral Sclerosis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Placebo

Placebo administered by mouth or via feeding tube for 48 weeks: once daily for first 3 weeks and then twice daily for remainder of study if participant tolerating

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type OTHER

Matching Placebo Comparator

AMX0035

Placebo administered by mouth or via feeding tube for 48 weeks: once daily for first 3 weeks and then twice daily for remainder of study if participant tolerating

Group Type EXPERIMENTAL

AMX0035

Intervention Type DRUG

Proprietary formulation of taurursodiol and sodium phenylbutyrate

Interventions

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Placebo

Matching Placebo Comparator

Intervention Type OTHER

AMX0035

Proprietary formulation of taurursodiol and sodium phenylbutyrate

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Male or female, at least 18 years of age
* Diagnosis of ALS (definite or clinically probable)
* Time since onset of first symptom of ALS should be \<24 months prior to randomization;
* If the participant is to be treated with riluzole and/or edaravone during the course of the trial, then treatment with riluzole and/or edaravone was, at the time of the screening visit, started and maintained at a stable regimen for at least 14 days for riluzole and/or for a full treatment cycle for edaravone;
* Capable of providing informed consent
* Capable and willing to follow trial procedures including visits to the trial clinic and visit requirements;
* Women of child bearing potential (e.g. not post-menopausal for at least one year or surgically sterile) must agree to use adequate birth control for the duration of the study and 3 months after last dose of study drug. Women must not be planning to become pregnant for the duration of the study and 3 months after last dose of study drug
* Men must agree to practice contraception for the duration of the study and 3 months after last dose of study drug. Men must not plan to father a child or provide for sperm donation for the duration of the study and 3 months after last dose of study drug

Exclusion Criteria

* Presence of tracheostomy or permanent assisted ventilation(PAV)
* Slow Vital Capacity (SVC) less than 55%
* History of known allergy to phenyl butyrate or bile salts
* Abnormal liver function defined as bilirubin levels and/or aspartate aminotransferase (AST) and/or alanine aminotransferase (ALT) \> 5 times the upper limit of the normal (obtained within 12 weeks from first dose)
* Renal insufficiency as defined by eGFR \<60 mL/min/1.73m\^2 (obtained within 12 weeks from first dose)
* Pregnant women (confirmed by a pregnancy test within 7 days of first dose) or women currently breastfeeding
* Current severe biliary disease which may result in the Investigator medical judgement in biliary obstruction including for example active cholecystitis, primary biliary cirrhosis, sclerosing cholangitis, gallbladder cancer, gangrene of the gallbladder, abscess of the gallbladder
* History of Class III/IV heart failure (per New York Heart Association - NYHA)
* Participant under severe salt restriction where the added salt intake due to treatment would put the participant at risk, in the Investigator clinical judgment
* Presence of unstable psychiatric disease, cognitive impairment, dementia or substance abuse that would impair ability of the participant to provide informed consent, according to Investigator judgment
* Clinically significant unstable medical condition (other than ALS) (e.g., cardiovascular instability, systemic infection, untreated thyroid dysfunction, severe laboratory test anomaly or clinically significant electrocardiogram \[ECG\] changes) that would pose a risk to the participant if he/she were to participate in the trial, according to Investigator judgment
* Previous treatment for ALS with cellular therapies or gene therapies
* Currently enrolled in another trial involving use of an investigational therapy
* Previous treatment with PB or taurursodiol within 30 days from Screening
* Implantation of Diaphragm Pacing System (DPS)
* Currently or previously treated within the last 30 days or planned exposure to any prohibited medications listed in Section 6.8 of the protocol
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Amylyx Pharmaceuticals Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Amylyx Study Director

Role: STUDY_DIRECTOR

Amylyx Pharmaceuticals

Locations

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Barrow Neurological Institute

Phoenix, Arizona, United States

Site Status

University of Southern California

Los Angeles, California, United States

Site Status

University of California Irvine

Orange, California, United States

Site Status

California Pacific Medical Center Research Institute

San Francisco, California, United States

Site Status

University of Colorado

Aurora, Colorado, United States

Site Status

University of Florida

Gainesville, Florida, United States

Site Status

University of South Florida

Tampa, Florida, United States

Site Status

Emory University

Atlanta, Georgia, United States

Site Status

Augusta University Neuroscience Center

Augusta, Georgia, United States

Site Status

Northwestern University

Chicago, Illinois, United States

Site Status

Johns Hopkins University School of Medicine Outpatient Center

Baltimore, Maryland, United States

Site Status

Healey & AMG Center for ALS Research at Massachusetts General Hospital

Boston, Massachusetts, United States

Site Status

University of Massachusetts

Worcester, Massachusetts, United States

Site Status

Hennepin Healthcare Research Institute

Minneapolis, Minnesota, United States

Site Status

Washington University School of Medicine

St Louis, Missouri, United States

Site Status

Somnos Clinical Research

Lincoln, Nebraska, United States

Site Status

Rutgers University

New Brunswick, New Jersey, United States

Site Status

Columbia University

New York, New York, United States

Site Status

University of North Carolina at Chapel Hill

Chapel Hill, North Carolina, United States

Site Status

Wake Forest University Health Sciences

Winston-Salem, North Carolina, United States

Site Status

The Ohio State University

Columbus, Ohio, United States

Site Status

University of Pennsylvania

Philadelphia, Pennsylvania, United States

Site Status

Lewis Katz School of Medicine at Temple University

Philadelphia, Pennsylvania, United States

Site Status

Austin Neuromuscular Center

Austin, Texas, United States

Site Status

Texas Neurology

Dallas, Texas, United States

Site Status

Virginia Commonwealth University

Henrico, Virginia, United States

Site Status

Swedish Neuroscience Institute

Seattle, Washington, United States

Site Status

University of Washington

Seattle, Washington, United States

Site Status

University Hospitals Leuven

Leuven, , Belgium

Site Status

Hospices Civils de Lyon Hôpital Neurologique Pierre Wertheimer Cellule Mutualisée de Recherche Clinique (CMRC)

Bron, , France

Site Status

Hopital Gabriel Montpied Service de Neurologie

Clermont-Ferrand, , France

Site Status

CHRU de Lille - Hôpital Roger Salengro

Lille, , France

Site Status

CHU de Limoges - Hôpital Dupuytren

Limoges, , France

Site Status

Hôpitaux Universitaires de Marseille Timone

Marseille, , France

Site Status

CHU de Montpellier

Montpellier, , France

Site Status

CHU Nice

Nice, , France

Site Status

Hôpital de la Salpêtrière

Paris, , France

Site Status

Le Centre Hospitalier Régional Universitaire de Tours

Tours, , France

Site Status

Charité - Universitätsmedizin Berlin

Berlin, , Germany

Site Status

Uniklinikum Dresden

Dresden, , Germany

Site Status

Hannover Medical School

Hanover, , Germany

Site Status

Jena University Hospital

Jena, , Germany

Site Status

Medizinische Fakultät Mannheim der Universität Heidelberg

Mannheim, , Germany

Site Status

University Medical Center Rostock

Rostock, , Germany

Site Status

Ulm University Medical Centre

Ulm, , Germany

Site Status

Trinity College Dublin/Beaumont Hospital

Dublin, , Ireland

Site Status

Università degli Studi di Bari Aldo Moro

Bari, , Italy

Site Status

Centro Clinico NEMO

Milan, , Italy

Site Status

University of Milan Medical School

Milan, , Italy

Site Status

Azienda Ospedaliero Universitaria Di Modena

Modena, , Italy

Site Status

Università degli Studi della Campania Luigi Vanvitelli

Napoli, , Italy

Site Status

University of Padua

Padua, , Italy

Site Status

University of Torino

Turin, , Italy

Site Status

University Medical Center Utrecht

Utrecht, , Netherlands

Site Status

Centrum Medyczne Linden

Krakow, , Poland

Site Status

City Clinic Warsaw

Warsaw, , Poland

Site Status

Centro Hospitalar Universitário Lisboa-Norte

Lisbon, , Portugal

Site Status

Hospital del Mar

Barcelona, , Spain

Site Status

Hospital Universitari de Bellvitge-IDIBELL

Barcelona, , Spain

Site Status

Hospital San Rafael

Madrid, , Spain

Site Status

Biodonostia Health Research Institute; Hospital Universitario Donostia

San Sebastián, , Spain

Site Status

Hospital Universitario y Politécnico La Fe

Valencia, , Spain

Site Status

Karolinska Institutet

Stockholm, , Sweden

Site Status

Umeå University Hospital

Umeå, , Sweden

Site Status

King's College London

London, , United Kingdom

Site Status

UCL Queen Square Institute of Neurology

London, , United Kingdom

Site Status

University of Plymouth

Plymouth, , United Kingdom

Site Status

Salford Royal Hospital Barnes

Salford, , United Kingdom

Site Status

Sheffield Institute for Translational Neuroscience (SITraN)

Sheffield, , United Kingdom

Site Status

Countries

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United States Belgium France Germany Ireland Italy Netherlands Poland Portugal Spain Sweden United Kingdom

Other Identifiers

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A35-004

Identifier Type: -

Identifier Source: org_study_id

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