Study to Measure Cerebrospinal Fluid Mutant Huntingtin Protein in Participants With Early Manifest Stage I or Stage II Huntington's Disease

NCT ID: NCT03664804

Last Updated: 2025-01-03

Study Results

Results available

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE1

Total Enrollment

95 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-12-05

Study Completion Date

2022-05-07

Brief Summary

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The study is designed as a multi-site, prospective, 15-month longitudinal, cohort study measuring CSF mHTT in participants with early manifest Stage I or Stage II Huntington's Disease (HD).

Detailed Description

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Conditions

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Huntington's Disease

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

OTHER

Blinding Strategy

NONE

Study Groups

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Participants with Early Manifest Stage I or II HD

No study drug was administered in this study

Group Type OTHER

No Study Drug was Administered in this Study

Intervention Type OTHER

No study drug was administered in this study

Interventions

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No Study Drug was Administered in this Study

No study drug was administered in this study

Intervention Type OTHER

Eligibility Criteria

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Inclusion Criteria

* Capacity to consent to participate in the study as assessed using the Evaluation to Sign Consent tool and investigator judgment
* Age 25 to 65 years, inclusive, at the time of signing Informed Consent Form
* Early manifest, Stage I or Stage II HD (defined as TFC of 7-13, inclusive)
* Genetically confirmed disease (CAG repeat length ≥ 36 in huntingtin gene by direct DNA testing)
* Body mass index ≥18 and ≤32 kg/m2; total body weight \>50 kg
* Ability to undergo and tolerate MRI scans
* Ability to tolerate blood draws and lumbar puncture
* Ability and willingness to comply with all aspects of the protocol, including completion of interviews and questionnaires and carrying/wearing of a digital monitoring device
* Stable medical, psychiatric, and neurological status for at least 12 weeks prior to screening and at the time of enrollment
* Signed study companion consent for participation, if a study companion is available
* For women of childbearing potential: agreement to remain abstinent or use acceptable contraceptive methods during the observational period

Exclusion Criteria

* Any condition, including severe chorea, that would prevent either writing or performing pen and paper or smartphone-based tasks
* History of attempted suicide or suicidal ideation with plan (i.e., active suicidal ideation) that required hospital visit and/or change in level of care within 12 months prior to screening
* Current active psychosis, confusional state, or violent behavior
* Any serious medical condition or clinically significant laboratory, vital sign, or electrocardiogram abnormalities at screening that, in the investigator's judgement, precludes the participant's safe participation in and completion of the study
* Pregnant or breastfeeding, or intending to become pregnant during the study
* Positive for hepatitis C virus antibody or hepatitis B surface antigen at screening
* Known HIV infection
* Current or previous use of an antisense oligonucleotide (including small interfering RNA)
* Current use of antipsychotics prescribed for psychosis, cholinesterase inhibitors, memantine, amantadine, or riluzole including use within 12 weeks of enrollment
* Treatment with an investigational drug within 30 days prior to screening or 5 half-lives of the investigational drug, whichever is longer
* Antiplatelet or anticoagulant therapy within the 14 days prior to screening or anticipated use during the study, including, but not limited, to aspirin (unless ≤81mg/day), clopidogrel, dipyridamole, warfarin, dabigatran, rivaroxaban, and apixaban
* History of bleeding diathesis or coagulopathy; platelet count \< lower limit of normal unless stable and assessed by the Investigator and Sponsor Medical Monitor to be not clinically significant
* Malignancy within 5 years prior to screening, except basal or squamous cell carcinoma of the skin or carcinoma in situ of the cervix that has been successfully treated
* History of gene therapy or cell transplantation or any other experimental brain surgery
* Concurrent or planned concurrent participation in any clinical study without approval of the Medical Monitor
* Presence of implanted shunt for the drainage of CSF or an implanted CNS catheter
* Pre-existing structural brain lesion as assessed by MRI scan
Minimum Eligible Age

25 Years

Maximum Eligible Age

65 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Hoffmann-La Roche

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Clinical Trials

Role: STUDY_DIRECTOR

Hoffmann-La Roche

Locations

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CenExel Rocky Mountain Clinical Research, LLC

Englewood, Colorado, United States

Site Status

Georgetown University; Research Division, Psychiatry

Washington D.C., District of Columbia, United States

Site Status

Hereditary Neurological Disease Centre (HNDC)

Wichita, Kansas, United States

Site Status

John Hopkins University School of Medicine

Baltimore, Maryland, United States

Site Status

Columbia University

New York, New York, United States

Site Status

The University of Texas Health Science Center at Houston; McGovern Medical School

Houston, Texas, United States

Site Status

The University of British Columbia; The Centre for Huntington Disease

Vancouver, British Columbia, Canada

Site Status

Centre for Movement Disorders (Neuropharm Consulting Inc.)

Markham, Ontario, Canada

Site Status

Charité - Universitätsmedizin Berlin, Campus Charité Mitte; Klinik für Psychiatrie und Psychotherapi

Berlin, , Germany

Site Status

St. Josef and St. Elisabeth gGmbH ; St. Josef Hospital Bochum; Neurologisches Forschungszentrum

Bochum, , Germany

Site Status

Universitätsklinikum Ulm; Klinik für Neurologie

Ulm, , Germany

Site Status

NIHR Welcome Trust Birmingham CRF - University Hospitals Birmingham; Department of Neuropsychiatry

Birmingham, , United Kingdom

Site Status

Cardiff University School of Medicine; Institute of Psychological Medicine Clinical Neurosciences

Cardiff, , United Kingdom

Site Status

National Hospital For Neurology and Neurosurgery

London, , United Kingdom

Site Status

Central Manchester University Hospitals NHS Foundation Trust; Manchester Centre for Genomic Medicine

Manchester, , United Kingdom

Site Status

Countries

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United States Canada Germany United Kingdom

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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BN40422

Identifier Type: -

Identifier Source: org_study_id

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