A Study to Assess the Safety and Tolerability of Lucerastat in Subjects With Fabry Disease

NCT ID: NCT02930655

Last Updated: 2018-07-10

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE1

Total Enrollment

14 participants

Study Classification

INTERVENTIONAL

Study Start Date

2015-02-01

Study Completion Date

2016-02-01

Brief Summary

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The primary purpose of this study was to assess the safety and tolerability of lucerastat in adults with Fabry Disease receiving Enzyme Replacement Therapy (ERT).

The secondary objectives were to investigate the effects of lucerastat on plasma and urine levels of biomarkers, to assess its effects on renal and cardiac functions and to determine the pharmacokinetic profile of lucerastat at steady-state.

Detailed Description

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Conditions

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Fabry Disease

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Lucerastat group

Ten subjects with Fabry Disease received 1000 mg of oral lucerastat twice daily for 12 weeks in addition to their standard of care treatment (enzyme replace therapy).

Group Type EXPERIMENTAL

Lucerastat

Intervention Type DRUG

Hard gelatin capsules for oral administration formulated at a strength of 250 mg, and administered as 4 capsules in the morning and 4 capsules in the evening.

Enzyme replacement therapy (ERT)

Intervention Type DRUG

All the subjects received an ERT as background therapy for at least 24 months prior to the screening visit and they had to continue receiving this treatment during the conduct of the study.

Control group

Four subjects with Fabry Disease under enzyme replace therapy (ERT) as standard of care treatment were included as a control group.

Group Type EXPERIMENTAL

Enzyme replacement therapy (ERT)

Intervention Type DRUG

All the subjects received an ERT as background therapy for at least 24 months prior to the screening visit and they had to continue receiving this treatment during the conduct of the study.

Interventions

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Lucerastat

Hard gelatin capsules for oral administration formulated at a strength of 250 mg, and administered as 4 capsules in the morning and 4 capsules in the evening.

Intervention Type DRUG

Enzyme replacement therapy (ERT)

All the subjects received an ERT as background therapy for at least 24 months prior to the screening visit and they had to continue receiving this treatment during the conduct of the study.

Intervention Type DRUG

Other Intervention Names

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ACT-434964 Fabrazyme Replagal

Eligibility Criteria

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Inclusion Criteria

* Signed informed consent form
* Male and female adult subjects with a diagnosis of Fabry Disease (FD) based on historical assessments (residual α-GAL A activity level below lower limit of normal for males and presence of a galactosidase alpha mutation for females) and a history of clinical symptoms of FD
* On ERT for at least 24 months without any change in dose within the last 6 months prior to screening

Exclusion Criteria

* Severe renal function impairment
* Severe residual neurologic deficit
* Clinically significant unstable cardiac disease
* Any circumstances or conditions, which, in the opinion of the investigator, may have affected full participation in the study or compliance with the protocol
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Idorsia Pharmaceuticals Ltd.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Nicolas Guérard

Role: STUDY_DIRECTOR

Actelion

Locations

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Investigator Site

Würzburg, , Germany

Site Status

Countries

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Germany

References

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Guerard N, Morand O, Dingemanse J. Lucerastat, an iminosugar with potential as substrate reduction therapy for glycolipid storage disorders: safety, tolerability, and pharmacokinetics in healthy subjects. Orphanet J Rare Dis. 2017 Jan 14;12(1):9. doi: 10.1186/s13023-017-0565-9.

Reference Type DERIVED
PMID: 28088251 (View on PubMed)

Other Identifiers

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AC-069-104

Identifier Type: -

Identifier Source: org_study_id

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