Abatacept for GVHD Prophylaxis After Hematopoietic Stem Cell Transplantation for Pediatric Sickle Cell Disease

NCT ID: NCT02867800

Last Updated: 2024-06-13

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

COMPLETED

Clinical Phase

PHASE1

Total Enrollment

24 participants

Study Classification

INTERVENTIONAL

Study Start Date

2016-07-31

Study Completion Date

2023-12-30

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

To assess the tolerability of the costimulation blocking agent abatacept (CTLA4-Ig) when added to the standard graft versus host disease (GVHD) prophylaxis regimen of a calcineurin inhibitor and methotrexate in patients receiving early alemtuzumab followed by fludarabine, thiotepa, melphalan, and alemtuzumab for conditioning.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Outcomes of hematopoietic stem cell transplantation (HSCT) for children and adolescents with sickle cell disease (SCD) have improved. Graft versus host disease (GVHD), however, remains a barrier to success. GVHD accounts for most of the transplant related mortality and much of the morbidity in this setting-in part through the injury it directly causes and in part through the deleterious effects of steroids and the other immunosuppressive agents used to prevent and treat it. The results of pre-clinical studies and a phase I clinical study in patients with hematologic malignancies suggest that the costimulation blocking agent CTLA4-Ig may hold promise an agent for GVHD prophylaxis. In the present trial, the investigators are assessing the tolerability of adding abatacept to standard GVHD prophylaxis-a calcineurin inhibitor and methotrexate-in pediatric SCD patients receiving early alemtuzumab (completed by day -18) followed by fludarabine, thiotepa, and melphalan for conditioning. This trial will provide the foundation for subsequent trials designed to test the long-term hypothesis that abatacept is a safe, steroid-sparing effective adjunct to standard GVHD prophylaxis in this setting.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Sickle Cell Disease Graft Versus Host Disease

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Standard GVHD Prophylaxis + Abatacept

Subjects will receive

* premedication (Diphenhydramine, Acetaminophen, Methylprednisolone; and Meperidine as needed)
* immunosuppression (Alemtuzumab, or Thymoglobulin)
* conditioning regimen (Fludarabine, Thiotepa, and Melphalan)
* GVHD prophylaxis: calcineurin inhibitor (Cyclosporine,Tacrolimus, Sirolimus or Mycophenolate Mofetil with permission of the sponsor) and Methotrexate plus Abatacept on days -1, +5, +14 and +28, and a marrow infusion on day 0.

Group Type EXPERIMENTAL

Diphenhydramine

Intervention Type DRUG

(Standard of Care) Premedication

Diphenhydramine: 1 mg/kg IV or PO q 8 hours (maximum=50 mg)

Acetaminophen

Intervention Type DRUG

(Standard of Care) Premedication

Acetaminophen: 10-15 mg/kg PO q 6 hours (maximum=1000 mg)

Methylprednisolone

Intervention Type DRUG

(Standard of Care) Premedication

Methylprednisolone: 0.25-0.5 mg/kg IV q 6 hours

Meperidine

Intervention Type DRUG

(Standard of Care) Premedication

Use as needed (PRN) Meperidine: 0.5 mg/kg IV q 4-6 hours (for rigors)

Alemtuzumab

Intervention Type DRUG

(Standard of Care) Immunosuppression

Alemtuzumab:

A test dose of alemtuzumab, 3 mg, should be administered IV over 2 hours the first day. If the test dose is tolerated, administration of three treatment doses should begin within 24 hours. The three treatment doses should be administered on consecutive days. 10 mg/m2 should be given the first day, 15 mg/m2 the second and 20 mg/m2 the third.

Thymoglobulin

Intervention Type DRUG

(Standard of Care) Immunosuppression

Thymoglobulin: A 4 mg/kg dose of anti-thymocyte globulin should be administered in place of each alemtuzumab dose not completed.

Fludarabine

Intervention Type DRUG

(Standard Conditioning Regimen)

Fludarabine should be administered 30 mg/m2 IV daily for five days. It should be infused over 30 to 60 minutes.

Melphalan

Intervention Type DRUG

(Standard Conditioning Regimen)

Melphalan should be administered 140 mg/m2 IV 3 days before marrow infusion. It should be infused within 60 minutes of preparation and over a maximum of 30 minutes. It should be infused immediately after the fludarabine infusion is complete.

Thiotepa

Intervention Type DRUG

(Standard Conditioning Regimen)

Thiotepa should be administered 8 mg/kg IV 3 days before marrow infusion. It should be infused immediately after the fludarabine infusion is complete. The thiotepa should be infused over one hour.

Cyclosporine

Intervention Type DRUG

(Standard GVHD Prophylaxis) Calcineurin inhibitor

Cyclosporine: Administration will commence no later than at least 36 hours before marrow infusion; Cyclosporine doses will be adjusted to maintain a level of 150-300 ng/ml.

Tacrolimus

Intervention Type DRUG

(Standard GVHD Prophylaxis) Calcineurin inhibitor

Tacrolimus: Administration will commence no later than at least 36 hours before marrow infusion; Tacrolimus doses will be adjusted to maintain a level of 8-15 ng/ml.

Methotrexate

Intervention Type DRUG

(Standard GVHD Prophylaxis)

Methotrexate will be given at a dose of 15 mg/m2 IV on day 1 and a dose of 10 mg/m2 IV on days 3, 6 and 11. Dosing shall be based on actual weight.

Abatacept

Intervention Type DRUG

(Investigational)

Abatacept will be administered intravenously at a dose of 10 mg/kg based on actual weight with a maximum of 750 mg. In cases where the calculated dose is less than or equal to 110% of a simple multiple of a 250 mg vial: 250 mg (275mg), 500 mg (550 mg) or 750 mg (825 mg), the dose may be rounded down to the nearest multiple. No rounding up of the abatacept dose is permitted.

Marrow infusion

Intervention Type PROCEDURE

(Standard)

A procedure that infuses healthy cells, called stem cells, into your body to replace damaged or diseased bone marrow. A bone marrow transplant may also be used to treat certain types of cancer

Sirolimus

Intervention Type DRUG

(Standard GVHD Prophylaxis)

Calcineurin inhibitor (cyclosporine or tacrolimus or with permission of the sponsor: sirolimus or mycophenolate mofetil (MMF)) administration will commence no later than day -2 (at least 36 hours before the stem cell infusion); cyclosporine doses will be adjusted to maintain a level of 150-300 ng/ml. This range assumes monitoring by mass spectrometry. If an immunoassay is used instead, the equivalent range for that immunoassay should be used.

Mycophenolate Mofetil

Intervention Type DRUG

(Standard GVHD Prophylaxis)

Calcineurin inhibitor (cyclosporine or tacrolimus or with permission of the sponsor: sirolimus or mycophenolate mofetil (MMF)) administration will commence no later than day -2 (at least 36 hours before the stem cell infusion); cyclosporine doses will be adjusted to maintain a level of 150-300 ng/ml. This range assumes monitoring by mass spectrometry. If an immunoassay is used instead, the equivalent range for that immunoassay should be used.

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

Diphenhydramine

(Standard of Care) Premedication

Diphenhydramine: 1 mg/kg IV or PO q 8 hours (maximum=50 mg)

Intervention Type DRUG

Acetaminophen

(Standard of Care) Premedication

Acetaminophen: 10-15 mg/kg PO q 6 hours (maximum=1000 mg)

Intervention Type DRUG

Methylprednisolone

(Standard of Care) Premedication

Methylprednisolone: 0.25-0.5 mg/kg IV q 6 hours

Intervention Type DRUG

Meperidine

(Standard of Care) Premedication

Use as needed (PRN) Meperidine: 0.5 mg/kg IV q 4-6 hours (for rigors)

Intervention Type DRUG

Alemtuzumab

(Standard of Care) Immunosuppression

Alemtuzumab:

A test dose of alemtuzumab, 3 mg, should be administered IV over 2 hours the first day. If the test dose is tolerated, administration of three treatment doses should begin within 24 hours. The three treatment doses should be administered on consecutive days. 10 mg/m2 should be given the first day, 15 mg/m2 the second and 20 mg/m2 the third.

Intervention Type DRUG

Thymoglobulin

(Standard of Care) Immunosuppression

Thymoglobulin: A 4 mg/kg dose of anti-thymocyte globulin should be administered in place of each alemtuzumab dose not completed.

Intervention Type DRUG

Fludarabine

(Standard Conditioning Regimen)

Fludarabine should be administered 30 mg/m2 IV daily for five days. It should be infused over 30 to 60 minutes.

Intervention Type DRUG

Melphalan

(Standard Conditioning Regimen)

Melphalan should be administered 140 mg/m2 IV 3 days before marrow infusion. It should be infused within 60 minutes of preparation and over a maximum of 30 minutes. It should be infused immediately after the fludarabine infusion is complete.

Intervention Type DRUG

Thiotepa

(Standard Conditioning Regimen)

Thiotepa should be administered 8 mg/kg IV 3 days before marrow infusion. It should be infused immediately after the fludarabine infusion is complete. The thiotepa should be infused over one hour.

Intervention Type DRUG

Cyclosporine

(Standard GVHD Prophylaxis) Calcineurin inhibitor

Cyclosporine: Administration will commence no later than at least 36 hours before marrow infusion; Cyclosporine doses will be adjusted to maintain a level of 150-300 ng/ml.

Intervention Type DRUG

Tacrolimus

(Standard GVHD Prophylaxis) Calcineurin inhibitor

Tacrolimus: Administration will commence no later than at least 36 hours before marrow infusion; Tacrolimus doses will be adjusted to maintain a level of 8-15 ng/ml.

Intervention Type DRUG

Methotrexate

(Standard GVHD Prophylaxis)

Methotrexate will be given at a dose of 15 mg/m2 IV on day 1 and a dose of 10 mg/m2 IV on days 3, 6 and 11. Dosing shall be based on actual weight.

Intervention Type DRUG

Abatacept

(Investigational)

Abatacept will be administered intravenously at a dose of 10 mg/kg based on actual weight with a maximum of 750 mg. In cases where the calculated dose is less than or equal to 110% of a simple multiple of a 250 mg vial: 250 mg (275mg), 500 mg (550 mg) or 750 mg (825 mg), the dose may be rounded down to the nearest multiple. No rounding up of the abatacept dose is permitted.

Intervention Type DRUG

Marrow infusion

(Standard)

A procedure that infuses healthy cells, called stem cells, into your body to replace damaged or diseased bone marrow. A bone marrow transplant may also be used to treat certain types of cancer

Intervention Type PROCEDURE

Sirolimus

(Standard GVHD Prophylaxis)

Calcineurin inhibitor (cyclosporine or tacrolimus or with permission of the sponsor: sirolimus or mycophenolate mofetil (MMF)) administration will commence no later than day -2 (at least 36 hours before the stem cell infusion); cyclosporine doses will be adjusted to maintain a level of 150-300 ng/ml. This range assumes monitoring by mass spectrometry. If an immunoassay is used instead, the equivalent range for that immunoassay should be used.

Intervention Type DRUG

Mycophenolate Mofetil

(Standard GVHD Prophylaxis)

Calcineurin inhibitor (cyclosporine or tacrolimus or with permission of the sponsor: sirolimus or mycophenolate mofetil (MMF)) administration will commence no later than day -2 (at least 36 hours before the stem cell infusion); cyclosporine doses will be adjusted to maintain a level of 150-300 ng/ml. This range assumes monitoring by mass spectrometry. If an immunoassay is used instead, the equivalent range for that immunoassay should be used.

Intervention Type DRUG

Other Intervention Names

Discover alternative or legacy names that may be used to describe the listed interventions across different sources.

Benadryl Tylenol Medrol Demerol Lemtrada Genzyme Fludara Alkeran Thioplex Neoral Protopic Trexall CTLA4-Ig Orencia stem cell transplant Rapamune MMF

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

1. Patients with hemoglobin (Hgb) SS or SB0 thalassemia between the ages of 3 and 20.99 years who are at least 10 kg getting an human leukocyte antigen (HLA) matched bone marrow transplant, will be eligible if they are at increased risk for graft versus host disease (GVHD) and have severe SCD.

(a) Patients falling into one of the following three groups will be considered to be at increased risk for GVHD:

(i) Are between 10 and 20.99 years and receiving their transplant from an HLA matched related donor.

(ii) Are between 3 and 9.99 years and receiving their transplant from an HLA matched related donor who is at least 10 years.

(iii) Are between 3 and 20.99 years and receiving their transplant from an HLA matched unrelated donor. Donors must be matched at the A, B, C and DRB1 loci at the allele level.

(b) Patients who meet one of the following criteria will qualify as having severe SCD:

(i) Previous clinical stroke, as evidenced by a neurological deficit lasting longer than 24 hours, which is accompanied by radiographic evidence of ischemic brain injury and cerebral vasculopathy.

(ii) Asymptomatic cerebrovascular disease, as evidenced by one the following:
* Progressive silent cerebral infarction, as evidenced by serial MRI scans that demonstrate the development of a succession of lesions (at least two temporally discreet lesions, each measuring at least 3 mm in greatest dimension on the most recent scan) or the enlargement of a single lesion, initially measuring at least 3 mm). Lesions must be visible on T2-weighted MRI sequences.
* Cerebral arteriopathy, as evidenced by abnormal transcranial doppler (TCD) testing (confirmed elevated velocities in any single vessel of time-averaged maximum mean velocities (TAMMV) \> 200 cm/sec for non-imaging TCD) or by significant vasculopathy on magnetic resonance angiogram (MRA) (greater than 50% stenosis of \> 2 arterial segments or complete occlusion of any single arterial segment).

(iii) Frequent ( ≥ 3 per year for preceding 2 years) painful vaso-occlusive episodes (defined as episode lasting ≥ 4 hours and requiring hospitalization or outpatient treatment with parenteral opioids). If patient is on hydroxurea and its use has been associated with a decrease in the frequency of episodes, the frequency should be gauged from the 2 years prior to the start of this drug.

(iv) Recurrent ( ≥ 3 in lifetime) acute chest syndrome events which have necessitated erythrocyte transfusion therapy.

(v) Any combination of ≥ 3 acute chest syndrome episodes and vaso-occlusive pain episodes (defined as above) yearly for 3 years. If patient is on hydroxurea and its use has been associated with a decrease in the frequency of episodes, the frequency should be gauged from the 3 years prior to the start of this drug.
2. All patients and/or their parents or legal guardians must sign a written informed consent. Assent, when appropriate, will be obtained according to institutional guidelines.
3. Must have been evaluated and adequately counseled regarding treatment options for severe SCD by a pediatric hematologist.
4. Because of the elective and non-urgent nature of hematopoietic stem cell transplantation (HSCT) for SCD, it is important that all patients and families be counseled regarding fertility preservation measures available to them. All patients and/or their parents or legal guardians must indicate on the consent and assent forms that they have received this counseling.

Exclusion Criteria

1. Bridging (portal to portal) fibrosis or cirrhosis of the liver.
2. Parenchymal lung disease stemming from SCD or other process defined as a diffusing capacity of the lungs for carbon monoxide (DLCO) (corrected for hemoglobin) or forced vital capacity of less than 45% of predicted. Children unable to perform pulmonary function testing will be excluded if they require daytime oxygen supplementation.
3. Renal dysfunction with an estimated glomerular filtration rate (GFR) \< 50% of predicted normal for age.
4. Cardiac dysfunction with shortening fraction \< 25%.
5. Neurologic impairment other than hemiplegia, defined as full-scale IQ ≤70, quadriplegia or paraplegia, inability to ambulate, or any impairment resulting in decline of Lansky performance score to \< 70%.
6. Clinical stroke within 6 months of anticipated transplant.
7. Karnofsky or Lansky functional performance score \< 70%.
8. Patient is human immunodeficiency virus (HIV) infected.
9. Donor is HIV infected.
10. Donor has Hgb SS, SC or SB0 thalassemia.
11. Patient with unspecified chronic toxicity serious enough to detrimentally affect the patient's capacity to tolerate bone marrow transplantation.
12. Patient or patient's guardian(s) unable to understand the nature and risks inherent in the bone marrow transplant (BMT) process.
13. History of lack of compliance with medical care that would jeopardize transplant course.
14. Donor who for psychological, physiologic, or medical reasons is unable to tolerate a bone marrow harvest or receive general anesthesia.
15. Active viral, bacterial, fungal or protozoal infection.
16. Donor is pregnant.
17. Patient is pregnant.
Minimum Eligible Age

3 Years

Maximum Eligible Age

20 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Monica Bhatia

OTHER

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Monica Bhatia

Associate Professor of Pediatrics at the Columbia University Medical Center

Responsibility Role SPONSOR_INVESTIGATOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Monica Bhatia, MD

Role: STUDY_CHAIR

Columbia University

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Children's National Medical Center

Washington D.C., District of Columbia, United States

Site Status

Children's Healthcare of Atlanta

Atlanta, Georgia, United States

Site Status

Ann & Robert H. Lurie Children's Hospital of Chicago

Chicago, Illinois, United States

Site Status

Floating Hospital for Children at Tufts Medical Center

Boston, Massachusetts, United States

Site Status

Columbia University Irving Medical Center

New York, New York, United States

Site Status

North Carolina Cancer Hospital

Chapel Hill, North Carolina, United States

Site Status

Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

AAAQ2350

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.