Study of Arimoclomol in Inclusion Body Myositis (IBM)

NCT ID: NCT02753530

Last Updated: 2023-05-10

Study Results

Results available

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

152 participants

Study Classification

INTERVENTIONAL

Study Start Date

2017-08-16

Study Completion Date

2021-01-11

Brief Summary

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Funding Source - FDA Office of Orphan Products Development (OOPD). The purpose of this study is to evaluate the safety and efficacy of the study drug, arimoclomol in IBM patients.

Detailed Description

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A Phase 2/3, randomized, double-blind, placebo-controlled, international, 20-month intervention study in patients with IBM.

Conditions

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Inclusion Body Myositis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

DOUBLE

Participants Investigators

Study Groups

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Arimoclomol

248 mg arimoclomol base (equivalent to 400 mg arimoclomol citrate) 3 times daily

Group Type EXPERIMENTAL

Arimoclomol

Intervention Type DRUG

2 capsules (2 x 124 mg arimoclomol base; equivalent to 2 x 200 mg arimoclomol citrate) taken 3 times daily during breakfast, early afternoon, and at bedtime

Placebo

248 mg matching placebo 3 times daily

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type OTHER

2 matched placebo capsules taken 3 times daily during breakfast, early afternoon, and at bedtime

Interventions

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Arimoclomol

2 capsules (2 x 124 mg arimoclomol base; equivalent to 2 x 200 mg arimoclomol citrate) taken 3 times daily during breakfast, early afternoon, and at bedtime

Intervention Type DRUG

Placebo

2 matched placebo capsules taken 3 times daily during breakfast, early afternoon, and at bedtime

Intervention Type OTHER

Eligibility Criteria

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Inclusion Criteria

* Meet any of the European Neuromuscular Centre Inclusion Body Myositis research diagnostic criteria 2011 categories for IBM.
* Demonstrate being able to arise from a chair without support from another person or device.
* Able to ambulate at least 20 ft/6 meters with or without assistive device. Once arisen from the chair, participant may use any walking device, i.e. walker/frame, can, crutches, or braces. They cannot be supported by another person and cannot use furniture or wall for support.
* Age at onset of weakness \>45 years.
* Body weight of \>= 40 kg.
* Able to give informed consent.

Exclusion Criteria

* History of any of the following excludes subject participation in the study: chronic infection particularly HIV or Hepatitis B or C; cancer other than basal cell cancer less than five years prior; or other chronic serious medical illnesses.
* Presence of any of the following on routine blood screening: White blood cells (WBC) \<3000; platelets \< 100,000; hematocrit \<30%; blood urea nitrogen (BUN) \>30 mg/dL; creatinine \>1.5 x upper limit of normal; symptomatic liver disease with serum albumin \<3 g/dL.
* History of most recent creatine kinase \>15x the upper limit of normal without any other explanation besides IBM.
* History of non-compliance with other therapies.
* Use of testosterone except for physiologic replacement doses in case of androgen deficiency. Participants must have documented proof of the androgen deficiency.
* Coexistence of other disease that would be likely to affect outcome measures
* Drug or alcohol abuse within past three months.
* Participation in a recent drug study in the last 30 days prior to the screening visit or use of a biologic agent less than 6 months prior to the screening visit.
* Women who are lactating or unwilling to use adequate method of birth control who are not surgically sterile. Adequate birth control includes use of intrauterine device, abstinence, or oral contraceptives or a double barrier method, e.g condom plus diaphragm will be necessary for both male and female participants.
* Participants taking \>7.5 mg prednisolone or equivalent or participants on Intravenous Immunoglobulin Therapy (IVIg) or other immunosuppressants within the last 3 months.
* Clinically significant renal or hepatic disease, as indicated by clinical laboratory assessment.
Minimum Eligible Age

45 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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University of Kansas Medical Center

OTHER

Sponsor Role collaborator

University College, London

OTHER

Sponsor Role collaborator

ZevraDenmark

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Mazen Dimachkie, MD

Role: PRINCIPAL_INVESTIGATOR

University of Kansas Medical Center

Michael Hanna, MD

Role: PRINCIPAL_INVESTIGATOR

University College, London

Locations

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Phoenix Neurological Associates

Phoenix, Arizona, United States

Site Status

University of California, Irvine

Irvine, California, United States

Site Status

University of Colorado School of Medicine

Aurora, Colorado, United States

Site Status

University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status

Johns Hopkins University

Baltimore, Maryland, United States

Site Status

Brigham and Women's Hospital

Boston, Massachusetts, United States

Site Status

University of Rochester

Rochester, New York, United States

Site Status

The Ohio State University

Columbus, Ohio, United States

Site Status

Nerve and Muscle Center of Texas

Houston, Texas, United States

Site Status

University of Utah

Salt Lake City, Utah, United States

Site Status

University of Virginia

Charlottesville, Virginia, United States

Site Status

University College of London

London, , United Kingdom

Site Status

Countries

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United States United Kingdom

References

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Salam S, Symonds T, Doll H, Rousell S, Randall J, Lloyd-Price L, Hudgens S, Guldberg C, Herbelin L, Barohn RJ, Hanna MG, Dimachkie MM, Machado PM; Members of the Arimoclomol in IBM Investigator Team of the Neuromuscular Study Group. Measurement properties of the Inclusion Body Myositis Functional Rating Scale. J Neurol Neurosurg Psychiatry. 2025 Jan 16;96(2):122-131. doi: 10.1136/jnnp-2024-333617.

Reference Type DERIVED
PMID: 38960586 (View on PubMed)

Machado PM, McDermott MP, Blaettler T, Sundgreen C, Amato AA, Ciafaloni E, Freimer M, Gibson SB, Jones SM, Levine TD, Lloyd TE, Mozaffar T, Shaibani AI, Wicklund M, Rosholm A, Carstensen TD, Bonefeld K, Jorgensen AN, Phonekeo K, Heim AJ, Herbelin L, Barohn RJ, Hanna MG, Dimachkie MM; Arimoclomol in IBM Investigator Team of the Neuromuscular Study Group. Safety and efficacy of arimoclomol for inclusion body myositis: a multicentre, randomised, double-blind, placebo-controlled trial. Lancet Neurol. 2023 Oct;22(10):900-911. doi: 10.1016/S1474-4422(23)00275-2.

Reference Type DERIVED
PMID: 37739573 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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R01FD004809

Identifier Type: FDA

Identifier Source: secondary_id

View Link

STUDY00002461

Identifier Type: -

Identifier Source: org_study_id

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