Efficacy and Safety Study of WTX101 (ALXN1840) in Adult Wilson Disease Patients

NCT ID: NCT02273596

Last Updated: 2021-09-29

Study Results

Results available

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

29 participants

Study Classification

INTERVENTIONAL

Study Start Date

2014-11-24

Study Completion Date

2018-11-07

Brief Summary

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The main purpose of the study was to evaluate the efficacy of ALXN1840 (formerly WTX101) for 24 weeks on non-ceruloplasmin-bound copper (NCC) concentrations adjusted for molybdenum plasma concentration in participants newly diagnosed with Wilson Disease (WD) who were aged 18 and older and who had NCC concentrations within or above the reference range at the time of enrollment in the study. The study consisted of a 24-week Treatment Period, followed by a planned 36-month Extension Period.

Detailed Description

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Conditions

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Wilson Disease

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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ALXN1840

Treatment Period: ALXN1840 at individualized doses ranging from 15 to 60 milligram (mg) per day. Dose increases or dose reductions were dependent on the individual NCC concentrations adjusted for Mo plasma concentration. ALXN1840 may have been administered every other day, once daily, or twice daily, depending on individualized dosing regimen, for 24 weeks.

Extension Period: Participants continued the same ALXN1840 daily dose maintained at Week 24 of the Treatment Period and the same dosing regimen. During the Extension Period, no up-titration was made unless NCC concentrations adjusted for Mo plasma concentration did not remain stable within (or below) the reference range. ALXN1840 could have been received for up to 36 months in the Extension Period.

Group Type EXPERIMENTAL

ALXN1840

Intervention Type DRUG

Individualized oral doses of ALXN1840.

Interventions

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ALXN1840

Individualized oral doses of ALXN1840.

Intervention Type DRUG

Other Intervention Names

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WTX101

Eligibility Criteria

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Inclusion Criteria

* Able to understand and willing to comply with study procedures, restrictions, and requirements, as judged by the Investigator.
* Newly established diagnosis of WD by Leipzig-Score ≥ 4 documented by testing as outlined in 2012 European Association for the Study of the Liver Wilson Disease Clinical Practice Guidelines.
* NCC levels within or above the normal reference range (0.8 to 2.3 micromole).
* Willing to undergo 48 hour washout from current WD treatment

Exclusion Criteria

* Treatment for greater than 24 months for WD with chelation therapy (for example, penicillamine, trientine hydrochloride) or zinc therapy.
* Decompensated hepatic cirrhosis.
* Model for End-Stage Liver Disease score \> 11.
* Modified Nazer score \> 6.
* Gastrointestinal bleed within past 6 months.
* Alanine aminotransferase \> 5 x upper limit of normal.
* Marked neurological disease requiring either nasogastric feeding or intensive in-patient medical care.
* Severe anemia with a hemoglobin \< 9 grams/deciliter.
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Alexion Pharmaceuticals, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Eugene Swenson, MD, PhD

Role: STUDY_DIRECTOR

Alexion Pharmaceuticals, Inc.

Locations

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Clinical Trial Site

Los Angeles, California, United States

Site Status

Clinical Trial Site

New Haven, Connecticut, United States

Site Status

Clinical Trial Site

Chicago, Illinois, United States

Site Status

Clinical Trial Site

Ann Arbor, Michigan, United States

Site Status

Clinical Trial Site

Vienna, , Austria

Site Status

Clinical Trial Site

Heidelberg, , Germany

Site Status

Clinical Trial Site

Warsaw, , Poland

Site Status

Clinical Trial Site

Guildford, Surrey, United Kingdom

Site Status

Clinical Trial Site

Birmingham, , United Kingdom

Site Status

Countries

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United States Austria Germany Poland United Kingdom

References

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Weiss KH, Askari FK, Czlonkowska A, Ferenci P, Bronstein JM, Bega D, Ala A, Nicholl D, Flint S, Olsson L, Plitz T, Bjartmar C, Schilsky ML. Bis-choline tetrathiomolybdate in patients with Wilson's disease: an open-label, multicentre, phase 2 study. Lancet Gastroenterol Hepatol. 2017 Dec;2(12):869-876. doi: 10.1016/S2468-1253(17)30293-5. Epub 2017 Oct 5.

Reference Type RESULT
PMID: 28988934 (View on PubMed)

Other Identifiers

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WTX101-201

Identifier Type: -

Identifier Source: org_study_id

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