Trial Outcomes & Findings for Special Investigation (All Cases) of LipaCreon in Patients With Pancreatic Exocrine Insufficiency Due to Cystic Fibrosis (NCT NCT01427712)

NCT ID: NCT01427712

Last Updated: 2022-06-10

Results Overview

An adverse event (AE) was defined as any unfavourable or unintended disease, or symptom or sign of such a disease, or abnormal laboratory finding that occurred in a patient who received Lipacreon, whether or not considered related to the medicinal product. Also, an AE for which the relationship with Lipacreon could not be ruled out was regarded as an adverse drug reaction (ADR). 1. Related : There is a temporal relationship between the use of the medicinal product and the onset of an AE, or a relapse with readministration,where other factors are less likely to be involved. 2. Relationship cannot be ruled out : There are other potential factors although there is a temporal relationship between the use of the medicinal product and the onset of an AE

Recruitment status

COMPLETED

Target enrollment

24 participants

Primary outcome timeframe

From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).

Results posted on

2022-06-10

Participant Flow

For this survey, the contract for the conduct of the survey was concluded with 21 departments of 21 facilities during the period from August 2011 to March 2018. Among these, 24 patients were registered at 21 departments of 21 facilities (patient registration period: August 2011 to March 2017).

Participant milestones

Participant milestones
Measure
LipaCreon
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Overall Study
STARTED
24
Overall Study
Collected CRFs
21
Overall Study
Safety Analysis Set
21
Overall Study
COMPLETED
17
Overall Study
NOT COMPLETED
7

Reasons for withdrawal

Reasons for withdrawal
Measure
LipaCreon
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Overall Study
Transfer to a different hospital
2
Overall Study
Lost to Follow-up
1
Overall Study
Aggravation of cystic fibrosis
3
Overall Study
Failure to visit
1

Baseline Characteristics

Special Investigation (All Cases) of LipaCreon in Patients With Pancreatic Exocrine Insufficiency Due to Cystic Fibrosis

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Age, Continuous
8.7 years
STANDARD_DEVIATION 9.4 • n=5 Participants
Age, Customized
< 6 years
12 Participants
n=5 Participants
Age, Customized
>= 6 years and < 12 years
4 Participants
n=5 Participants
Age, Customized
>= 12 years and < 18 years
0 Participants
n=5 Participants
Age, Customized
>= 18 years
5 Participants
n=5 Participants
Sex: Female, Male
Female
11 Participants
n=5 Participants
Sex: Female, Male
Male
10 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
21 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
0 Participants
n=5 Participants
Race (NIH/OMB)
White
0 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Region of Enrollment
Japan
21 participants
n=5 Participants
Body Mass Index (BMI)
< 18.5 kg/m^2
16 Participants
n=5 Participants
Body Mass Index (BMI)
>= 18.5 kg/m^2 and < 25 kg/m^2
2 Participants
n=5 Participants
Body Mass Index (BMI)
>= 25 kg/m^2
0 Participants
n=5 Participants
Body Mass Index (BMI)
unknown
3 Participants
n=5 Participants

PRIMARY outcome

Timeframe: From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

An adverse event (AE) was defined as any unfavourable or unintended disease, or symptom or sign of such a disease, or abnormal laboratory finding that occurred in a patient who received Lipacreon, whether or not considered related to the medicinal product. Also, an AE for which the relationship with Lipacreon could not be ruled out was regarded as an adverse drug reaction (ADR). 1. Related : There is a temporal relationship between the use of the medicinal product and the onset of an AE, or a relapse with readministration,where other factors are less likely to be involved. 2. Relationship cannot be ruled out : There are other potential factors although there is a temporal relationship between the use of the medicinal product and the onset of an AE

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Number of Patients With Adverse Drug Reaction
1 participants

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following nutritional endpoints were measured prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •BMI (height \[only prior to the start of Lipacreon treatment\] and weight)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Nutritional Endpoints - BMI
Baseline
15.093 kg/m^2
Standard Deviation 1.955
Nutritional Endpoints - BMI
4 weeks
15.583 kg/m^2
Standard Deviation 1.511
Nutritional Endpoints - BMI
8 weeks
15.649 kg/m^2
Standard Deviation 1.667
Nutritional Endpoints - BMI
24 weeks
15.604 kg/m^2
Standard Deviation 1.350
Nutritional Endpoints - BMI
52 weeks
15.698 kg/m^2
Standard Deviation 1.239
Nutritional Endpoints - BMI
2 years
15.766 kg/m^2
Standard Deviation 1.438
Nutritional Endpoints - BMI
3 years
15.152 kg/m^2
Standard Deviation 1.241
Nutritional Endpoints - BMI
4 years
15.479 kg/m^2
Standard Deviation 1.757
Nutritional Endpoints - BMI
5 years
15.584 kg/m^2
Standard Deviation 2.608
Nutritional Endpoints - BMI
6 years
15.819 kg/m^2
Standard Deviation 2.467
Nutritional Endpoints - BMI
7 years
11.806 kg/m^2

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following nutritional endpoints were measured prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Serum total protein

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Nutritional Endpoints - Serum Total Protein
Baseline
7.282 g/dL
Standard Deviation 1.105
Nutritional Endpoints - Serum Total Protein
4 weeks
6.925 g/dL
Standard Deviation 0.770
Nutritional Endpoints - Serum Total Protein
8 weeks
6.700 g/dL
Standard Deviation 0.441
Nutritional Endpoints - Serum Total Protein
24 weeks
7.350 g/dL
Standard Deviation 1.049
Nutritional Endpoints - Serum Total Protein
52 weeks
7.421 g/dL
Standard Deviation 0.877
Nutritional Endpoints - Serum Total Protein
2 years
7.563 g/dL
Standard Deviation 1.058
Nutritional Endpoints - Serum Total Protein
3 years
8.029 g/dL
Standard Deviation 1.164
Nutritional Endpoints - Serum Total Protein
4 years
8.127 g/dL
Standard Deviation 1.301
Nutritional Endpoints - Serum Total Protein
5 years
7.390 g/dL
Standard Deviation 1.086
Nutritional Endpoints - Serum Total Protein
6 years
7.200 g/dL
Standard Deviation 0.557
Nutritional Endpoints - Serum Total Protein
7 years
6.100 g/dL

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following nutritional endpoints were measured prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Albumin

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Nutrition Endpoints - Albumin
24 weeks
4.130 g/dL
Standard Deviation 0.267
Nutrition Endpoints - Albumin
Baseline
3.872 g/dL
Standard Deviation 0.641
Nutrition Endpoints - Albumin
4 weeks
4.054 g/dL
Standard Deviation 0.657
Nutrition Endpoints - Albumin
8 weeks
4.067 g/dL
Standard Deviation 0.339
Nutrition Endpoints - Albumin
52 weeks
4.232 g/dL
Standard Deviation 0.549
Nutrition Endpoints - Albumin
2 years
4.390 g/dL
Standard Deviation 0.304
Nutrition Endpoints - Albumin
3 years
4.054 g/dL
Standard Deviation 0.323
Nutrition Endpoints - Albumin
4 years
4.040 g/dL
Standard Deviation 0.844
Nutrition Endpoints - Albumin
5 years
3.613 g/dL
Standard Deviation 0.931
Nutrition Endpoints - Albumin
6 years
4.233 g/dL
Standard Deviation 0.115
Nutrition Endpoints - Albumin
7 years
3.700 g/dL

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following nutritional endpoints were measured prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Total cholesterol

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Nutrition Endpoints - Total Cholesterol
Baseline
124.94 mg/dL
Standard Deviation 31.04
Nutrition Endpoints - Total Cholesterol
4 weeks
126.10 mg/dL
Standard Deviation 34.94
Nutrition Endpoints - Total Cholesterol
8 weeks
128.00 mg/dL
Standard Deviation 35.96
Nutrition Endpoints - Total Cholesterol
24 weeks
139.13 mg/dL
Standard Deviation 40.88
Nutrition Endpoints - Total Cholesterol
52 weeks
123.11 mg/dL
Standard Deviation 29.40
Nutrition Endpoints - Total Cholesterol
2 years
148.17 mg/dL
Standard Deviation 26.12
Nutrition Endpoints - Total Cholesterol
3 years
139.00 mg/dL
Standard Deviation 39.72
Nutrition Endpoints - Total Cholesterol
4 years
136.50 mg/dL
Standard Deviation 30.88
Nutrition Endpoints - Total Cholesterol
5 years
114.00 mg/dL
Standard Deviation 62.23
Nutrition Endpoints - Total Cholesterol
6 years
157.50 mg/dL
Standard Deviation 57.28
Nutrition Endpoints - Total Cholesterol
7 years
167.00 mg/dL

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following nutritional endpoints were measured prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Triglycerides

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Nutrition Endpoints - Triglycerides
Baseline
81.6 mg/dL
Standard Deviation 41.4
Nutrition Endpoints - Triglycerides
4 weeks
126.1 mg/dL
Standard Deviation 115.2
Nutrition Endpoints - Triglycerides
8 weeks
73.2 mg/dL
Standard Deviation 35.4
Nutrition Endpoints - Triglycerides
24 weeks
80.5 mg/dL
Standard Deviation 39.6
Nutrition Endpoints - Triglycerides
52 weeks
117.1 mg/dL
Standard Deviation 51.1
Nutrition Endpoints - Triglycerides
2 years
83.6 mg/dL
Standard Deviation 69.9
Nutrition Endpoints - Triglycerides
3 years
89.8 mg/dL
Standard Deviation 34.8
Nutrition Endpoints - Triglycerides
4 years
100.0 mg/dL
Standard Deviation 49.2
Nutrition Endpoints - Triglycerides
5 years
89.0 mg/dL
Standard Deviation 28.3
Nutrition Endpoints - Triglycerides
6 years
124.5 mg/dL
Standard Deviation 38.9
Nutrition Endpoints - Triglycerides
7 years
160.0 mg/dL

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following nutritional endpoints were measured prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Haemoglobin

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Nutrition Endpoints - Haemoglobin
Baseline
12.02 g/dL
Standard Deviation 1.84
Nutrition Endpoints - Haemoglobin
4 weeks
12.38 g/dL
Standard Deviation 1.65
Nutrition Endpoints - Haemoglobin
8 weeks
12.07 g/dL
Standard Deviation 1.94
Nutrition Endpoints - Haemoglobin
24 weeks
12.82 g/dL
Standard Deviation 1.65
Nutrition Endpoints - Haemoglobin
52 weeks
12.89 g/dL
Standard Deviation 1.88
Nutrition Endpoints - Haemoglobin
2 years
13.41 g/dL
Standard Deviation 1.18
Nutrition Endpoints - Haemoglobin
3 years
13.18 g/dL
Standard Deviation 0.81
Nutrition Endpoints - Haemoglobin
4 years
13.38 g/dL
Standard Deviation 2.25
Nutrition Endpoints - Haemoglobin
5 years
11.65 g/dL
Standard Deviation 2.11
Nutrition Endpoints - Haemoglobin
6 years
12.50 g/dL
Standard Deviation 3.22
Nutrition Endpoints - Haemoglobin
7 years
12.20 g/dL

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following symptoms were assessed as those related to exocrine pancreatic insufficiency prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Steatorrhoea (Yes/No)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
Baseline, Yes
14 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
Baseline, No
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
4 weeks, Yes
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
4 weeks, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
8 weeks, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
8 weeks, No
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
24 weeks, Yes
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
24 weeks, No
10 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
52 weeks, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
52 weeks, No
9 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
2 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
2 years, No
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
3 years, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
3 Years, No
6 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
4 years, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
4 years, No
6 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
5 years, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
5 years, No
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
6 years, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
6 years, No
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
7 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Steatorrhoea
7 years, No
1 participants

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following symptoms were assessed as those related to exocrine pancreatic insufficiency prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Frequency of bowel movements (times/day)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
Baseline
2.40 times/day
Standard Deviation 1.76
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
4 weeks
1.90 times/day
Standard Deviation 0.74
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
8 weeks
1.86 times/day
Standard Deviation 0.69
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
24 weeks
1.83 times/day
Standard Deviation 0.83
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
52 weeks
1.82 times/day
Standard Deviation 0.75
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
2 years
1.75 times/day
Standard Deviation 1.16
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
3 years
1.63 times/day
Standard Deviation 0.74
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
4 years
2.29 times/day
Standard Deviation 1.11
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
5 years
1.60 times/day
Standard Deviation 0.89
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
6 years
1.33 times/day
Standard Deviation 0.58
Symptoms Related to Exocrine Pancreatic Insufficiency - Frequency of Bowel Movements
7 years
1.00 times/day

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following symptoms were assessed as those related to exocrine pancreatic insufficiency prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Diarrhoea (Yes/No)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
8 weeks, No
10 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
24 weeks, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
Baseline, Yes
6 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
Baseline, No
13 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
4 weeks, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
4 weeks, No
12 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
8 weeks, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
24 weeks, No
16 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
52 weeks, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
52 weeks, No
12 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
2 years, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
2 years, No
10 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
3 years, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
3 Years, No
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
4 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
4 years, No
9 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
5 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
5 years, No
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
6 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
6 years, No
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
7 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Diarrhoea
7 years, No
1 participants

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following symptoms were assessed as those related to exocrine pancreatic insufficiency prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Foul stool odour (Yes/No)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
Baseline, Yes
6 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
Baseline, No
13 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
4 weeks, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
4 weeks, No
12 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
8 weeks, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
8 weeks, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
24 weeks, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
24 weeks, No
13 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
52 weeks, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
52 weeks, No
9 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
2 years, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
2 years, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
3 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
3 Years, No
5 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
4 years, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
4 years, No
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
5 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
5 years, No
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
6 years, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
6 years, No
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
7 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Foul Stool Odour
7 years, No
1 participants

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following symptoms were assessed as those related to exocrine pancreatic insufficiency prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Inappetence (Yes/No)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
Baseline, Yes
7 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
Baseline, No
13 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
4 weeks, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
4 weeks, No
13 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
8 weeks, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
8 weeks, No
10 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
24 weeks, Yes
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
24 weeks, No
12 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
52 weeks, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
52 weeks, No
11 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
2 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
2 years, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
3 years, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
3 Years, No
6 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
4 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
4 years, No
6 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
5 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
5 years, No
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
6 years, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
6 years, No
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
7 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Inappetence
7 years, No
1 participants

SECONDARY outcome

Timeframe: Baseline, 4 weeks, 8 weeks, 24 weeks, 52 weeks, 2 years, 3 years, 4 years, 5 years, 6 years, and 7 years

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients.

The following symptoms were assessed as those related to exocrine pancreatic insufficiency prior to the start of Lipacreon treatment, at 4, 8, and 24 weeks after the start of treatment, at the completion of the 52-week observation period, at 1-year intervals during the follow-up period, and at the completion of follow-up in March 2018. •Abdominal distension (Yes/No)

Outcome measures

Outcome measures
Measure
LipaCreon
n=21 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
Baseline, Yes
5 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
Baseline, No
15 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
4 weeks, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
4 weeks, No
12 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
8 weeks, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
8 weeks, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
24 weeks, Yes
2 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
24 weeks, No
14 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
52 weeks, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
52 weeks, No
12 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
2 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
2 years, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
3 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
3 Years, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
4 years, Yes
1 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
4 years, No
8 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
5 years, Yes
3 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
5 years, No
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
6 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
6 years, No
4 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
7 years, Yes
0 participants
Symptoms Related to Exocrine Pancreatic Insufficiency - Abdominal Distension
7 years, No
1 participants

SECONDARY outcome

Timeframe: At 24 weeks

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients. Of these 21 patients, 17 patients were obtained with data on Degree of General Improvement at 24 weeks.

Degree of general improvement was assessed at 24 weeks after the start of Lipacreon treatment and at the completion of the 52-week observation period, using the following 4 grades: Improved, unchanged, exacerbated, unassessable

Outcome measures

Outcome measures
Measure
LipaCreon
n=17 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Degree of General Improvement
Improved
10 Participants
Degree of General Improvement
Unchanged
7 Participants
Degree of General Improvement
Exacerbated
0 Participants
Degree of General Improvement
Unassessable
0 Participants

SECONDARY outcome

Timeframe: At 52 weeks

Population: Among the 21 patients from whom the survey forms were collected, no patient was excluded from the safety analysis or efficacy analysis, and both the safety analysis set and the efficacy analysis set included 21 patients. Of these 21 patients, 14 patients were obtained with data on Degree of General Improvement at 52 weeks.

Degree of general improvement was assessed at 24 weeks after the start of Lipacreon treatment and at the completion of the 52-week observation period, using the following 4 grades: Improved, unchanged, exacerbated, unassessable

Outcome measures

Outcome measures
Measure
LipaCreon
n=14 Participants
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Degree of General Improvement
Improved
9 Participants
Degree of General Improvement
Unchanged
5 Participants
Degree of General Improvement
Exacerbated
0 Participants
Degree of General Improvement
Unassessable
0 Participants

Adverse Events

LipaCreon

Serious events: 4 serious events
Other events: 4 other events
Deaths: 3 deaths

Serious adverse events

Serious adverse events
Measure
LipaCreon
n=21 participants at risk
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Infections and infestations
Pharyngitis
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Infections and infestations
Pneumonia
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Infections and infestations
Enteritis infectious
4.8%
1/21 • Number of events 2 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Metabolism and nutrition disorders
Dehydration
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Metabolism and nutrition disorders
Hyperkalaemia
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Gastrointestinal disorders
Haematochezia
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Skin and subcutaneous tissue disorders
Erythema multiforme
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Renal and urinary disorders
Renal impairment
4.8%
1/21 • Number of events 1 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Investigations
C-Reactive Protein Increased
4.8%
1/21 • Number of events 2 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).

Other adverse events

Other adverse events
Measure
LipaCreon
n=21 participants at risk
In general, pancrelipase 600 mg/dose was orally administered immediately after a meal, 3 times a day. Also, the dose was adjusted appropriately according to the patient's condition. Pancrelipase
Infections and infestations
Bronchitis
9.5%
2/21 • Number of events 6 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).
Respiratory, thoracic and mediastinal disorders
Rhinitis allergic
9.5%
2/21 • Number of events 6 • From the start of Lipacreon treatment to the end of the observation period or discontinuation. Approximately 7 years in the study completers (From date of dosage start, up to 7 years).

Additional Information

Medical affairs manager

Medical affairs

Phone: +81-3-5656-0516

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place