Post-Marketing Clinical Study of Ravulizumab in Participants With Clinical aHUS

NCT ID: NCT07308574

Last Updated: 2025-12-29

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

NOT_YET_RECRUITING

Clinical Phase

PHASE4

Total Enrollment

20 participants

Study Classification

INTERVENTIONAL

Study Start Date

2025-12-26

Study Completion Date

2027-06-25

Brief Summary

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The primary objective of this study is to assess the platelet count response to ravulizumab in participants clinically diagnosed as atypical hemolytic ureminc syndrome (aHUS).

Detailed Description

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Conditions

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aHUS Atypical Hemolytic Uremic Syndrome

Keywords

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aHUS atypical hemolytic uremic syndrome ravulizumab

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Ravulizumab

Participants will receive a weight-based loading dose of ravulizumab, followed by a weight-based dose 2 weeks after loading dose administration, then weight-based maintenance doses every 8 weeks via intravenous (IV) infusion.

Group Type EXPERIMENTAL

Ravulizumab

Intervention Type DRUG

Participants will receive ravulizumab via IV infusion.

Interventions

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Ravulizumab

Participants will receive ravulizumab via IV infusion.

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Body weight ≥20 kiligrams (kg)
* Participants clinically diagnosed as aHUS who have any of diseases/conditions listed below (including participants in whom Thrombotic microangiopathy (TMA) has not been improved even after treatment for the pathogenesis of diagnosed secondary TMA and therefore, diagnosis of aHUS was made).
* Infection (except for pneumococcal infection and Siga toxin-producing Escherichia coli infection)
* During pregnancy or postpartum
* Post-renal transplantation
* Hypertensive crisis/malignant hypertension
* Systemic lupus erythematosus and related diseases (e.g. dermatomyositis, mixed connective tissue disease, etc.)
* Participants with the following three signs:
* Thrombocytopenia: Platelet count \<150,000/microliter (μL)
* Microangiopathic haemolytic anaemia: Hb \< 10 grams per deciliter (g/dL) (\*)
* Acute kidney injury: one of the following is fulfilled; 1. ΔsCr ≥ 0.3 milligrams per deciliter (mg/dL) (within 48 hours), 2. 1.5-fold increase from baseline sCr (within 7 days), 3. urinary output ≤ 0.5 mL/kg/hour for ≥ 6 hours.
* No prior treatment with complement inhibitors.
* The investigator plans to provide the participant with 26-week treatment with ravulizumab in accordance with the treatment policy in clinical practice.
* Ravulizumab treatment is planned to be initiated within 14 days after onset of the latest TMA episode.
* Participants consenting to meningococcal vaccine administration and appropriate antibiotic prophylaxis (if required).

Exclusion Criteria

* Participants with TTP, STEC-HUS, secondary TMA that is obviously unrelated to complement abnormality.
* Participants with TMA caused by malignant tumors, abnormal Cobalamin C metabolism, Streptococcus pneumoniae, drugs, autoimmune diseases other than systemic lupus erythematosus and related diseases (e.g. scleroderma etc.), or hematopoietic stem cell transplantation
* Participants with pathological complement gene variants (CFH, CFI , CD46 (MCP), C3, CFB, THBD, DGKE) associated with the development of aHUS at enrolment
* Participants with positive anti-factor H antibodies
* More than 14 day from onset of TMA to the planned start of ravulizumab treatment
* Chronic kidney disease or irreversible renal impairment that requires chronic dialysis
* Presence of unresolved meningococcal disease
* Judgement by the investigator that the participant is not eligible for the study
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Alexion Pharmaceuticals, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Research Site

Bunkyō City, , Japan

Site Status

Research Site

Hirakata-shi, , Japan

Site Status

Research Site

Iruma-Gun, , Japan

Site Status

Research Site

Kyoto, , Japan

Site Status

Research Site

Matsumoto-shi, , Japan

Site Status

Research Site

Miyazaki, , Japan

Site Status

Research Site

Nagoya, , Japan

Site Status

Research Site

Nara, , Japan

Site Status

Research Site

Nerima-ku, , Japan

Site Status

Research Site

Sapporo, , Japan

Site Status

Research Site

Shinjuku-ku, , Japan

Site Status

Research Site

Tsu, , Japan

Site Status

Countries

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Japan

Central Contacts

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Alexion Pharmaceuticals, Inc. (Sponsor)

Role: CONTACT

Phone: 1-855-752-2356

Email: [email protected]

Other Identifiers

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NEPH-ULT-501

Identifier Type: REGISTRY

Identifier Source: secondary_id

D928BL00001

Identifier Type: -

Identifier Source: org_study_id