A Study in Children With Achondroplasia

NCT ID: NCT07301463

Last Updated: 2025-12-24

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Total Enrollment

260 participants

Study Classification

OBSERVATIONAL

Study Start Date

2025-06-20

Study Completion Date

2039-04-30

Brief Summary

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The goal of this observational study is to collect the anthropometric parameters, clinical characteristics, related medical complications, health-related quality of life and treatments of children with ACH, and complete a natural history observation of ACH for at least 6 months and up to 2 years.

Detailed Description

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Primary Objectives To evaluate the safety, tolerability, and recommended dose for expansion (RDE) of oral ABSK061 in children with ACH To evaluate the efficacy of oral ABSK061 in children with ACH

Secondary Objectives To characterize the pharmacokinetics (PK) of ABSK061 and potential disproportional metabolites (if applicable) To evaluate changes from baseline in anthropometric parameters after administration of oral ABSK061 To evaluate the acceptability of ABSK061 minitablets for peroral administration in children with ACH

Exploratory Objectives To evaluate changes in ACH complications and disease burden after oral administration of ABSK061 To evaluate the pharmacodynamic (PD) profile in children with ACH after oral administration of ABSK061

Conditions

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Achondroplasia

Study Design

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Observational Model Type

COHORT

Study Time Perspective

PROSPECTIVE

Study Groups

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Children with Achondroplasia

Male or female aged ≥2.5 to \<11 years old at screening

No Interventions

Intervention Type OTHER

No Interventions

complete a natural history observation of ACH for at least 6 months and up to 2 years

Intervention Type OTHER

no interventions

Interventions

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No Interventions

No Interventions

Intervention Type OTHER

complete a natural history observation of ACH for at least 6 months and up to 2 years

no interventions

Intervention Type OTHER

Eligibility Criteria

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Inclusion Criteria

1. Prior to screening, the guardians and children with ACH (if applicable) must be willing and able to provide signed informed consent.
2. Clinical diagnosis of ACH confirmed FGFR3 mutation by genetic testing.
3. Male or female aged ≥2.5 to \<11 years old at screening.
4. Tanner Stage 1 breast development for females or Tanner Stage 1 external genitalia development for males at screening.
5. Ambulatory and able to stand without assistance.

Exclusion Criteria

1. Bone age ≥14 years as assessed by the investigator based on hand and wrist X-ray taken within 6 months prior to Day 1.
2. Current evidence of growth plate closure (proximal tibia, distal femur), or AGV ≤ 1.5 cm/year over a period ≥6 months prior to screening.
3. Have a form of skeletal dysplasia other than ACH or known medical conditions that result in short stature or abnormal growth, including but not limited to severe achondroplasia with developmental delay and acanthosis nigricans (SADDAN), Turner syndrome, pseudoachondroplasia, inflammatory bowel disease, chronic renal insufficiency, active celiac disease a, Vitamin D deficiency b, untreated hypothyroidism c, poorly controlled diabetes (HbA1c ≥8.0%) or diabetic complications d.

1. Celiac disease responsive to a gluten-free diet is allowed
2. Vitamin D deficiency or insufficiency with a 25-hydroxyvitamin D \[25- (OH) D\] level ≥ 30 nmol/L after supplementation is allowed. Vitamin D deficiency is defined as 25-(OH) D level \<30 nmol/L. Vitamin D insufficiency is defined as 25-(OH) D level 30\~50 nmol/L. Patients with Vitamin D deficiency or insufficiency must be on Vitamin D regimen prior to screening
3. Patients with hypothyroidism meeting the following criteria are allowed to enroll: must be clinically euthyroid for one month prior to screening and, in the opinion of the investigator, have achieved any catch-up growth expected from thyroxine replacement
4. Patients with diabetes must have been on stable medication regimen for 3 months prior to screening
4. History or presence of injury or disease of the growth plate(s), other than ACH, that affects growth potential of long bones.
5. Impaired cardiac function or clinically significant cardiovascular disease, including any one of the following: New York Heart Association class II or higher heart disease, congenital heart disease (patients with repaired uncomplicated patent ductus arteriosus or atrial/ventricular septal defect with repair are allowed), clinically significant arrhythmias requiring therapy, aortic regurgitation, congestive heart failure, or any other uncontrolled heart disease.
6. For ACH-related complications: Current severe sleep apnea, symptomatic and/or requiring intervention for hydrocephalus, or spinal cord compression at the cranio-cervical junction, and has previously undergone ventriculoperitoneal shunt surgery.
7. Bone fracture within 6 months prior to screening (within 2 months for finger and toe fractures).
8. Have received any dose of medications affecting stature or body proportionality, such as human growth hormone, insulin-like growth factor 1 (IGF-1), or anabolic steroids within 3 months prior to screening, or long-term treatment (\>3 months) with the above drugs at any time.
9. Prior treatment with any CNP analogues or FGFR inhibitors. Prior use of any investigational drugs or investigational medical devices that affect stature or body proportionality.
10. Any comorbidities, disease or condition that, in the opinion of the investigator, may make the patient unlikely to fully complete the study-related procedures, may affect protocol compliance.
Minimum Eligible Age

30 Months

Maximum Eligible Age

11 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Abbisko Therapeutics Co, Ltd

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Yuan Lu

Role: STUDY_DIRECTOR

12B, Building 1, No 515, Huanke Road, Pudong New Area, Shanghai 201210, China

Locations

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Beijing Children's Hospital, Capital Medical University

Beijing, Beijing Municipality, China

Site Status RECRUITING

Guangzhou Women and Childrens Medical Center

Guangzhou, Guangzhou, China

Site Status NOT_YET_RECRUITING

Henan Children's Hospital, Zhengzhou Children's Hospital

Zhengzhou, Henan, China

Site Status NOT_YET_RECRUITING

Tongji Hospital, Tongji Medical College, Huazhong University of Science and Technology

Wuhan, Hubei, China

Site Status RECRUITING

Xin Hua Hospital Affiliatod to Shanghai Jiao Tong University School of Medicine

Shanghai, Shanghai Municipality, China

Site Status RECRUITING

Chengdu Women's and Children's Central Hospital

Chengdu, Sichuan, China

Site Status NOT_YET_RECRUITING

West China Second University Hospital, Sichuan University

Chengdu, Sichuan, China

Site Status ACTIVE_NOT_RECRUITING

Children's Hospital Zhejiang University School of Medicine

Hangzhou, Zhejiang, China

Site Status NOT_YET_RECRUITING

Countries

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China

Central Contacts

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Jing Zhang

Role: CONTACT

Phone: +86-15002126439

Email: [email protected]

Facility Contacts

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Di Wu

Role: primary

Li Liu

Role: primary

Haiyan Wei

Role: primary

Yanqin Ying

Role: primary

Yongguo Yu

Role: primary

Xinran Cheng

Role: primary

Wei Wu

Role: primary

Other Identifiers

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ABSK061-001

Identifier Type: -

Identifier Source: org_study_id