Phase 3, Open-label, Single-dose Study of CSL222 in Adolescent Male Subjects (≥ 12 to < 18 Years of Age) With Severe or Moderately Severe Hemophilia B

NCT ID: NCT07080905

Last Updated: 2025-12-17

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE3

Total Enrollment

20 participants

Study Classification

INTERVENTIONAL

Study Start Date

2025-07-28

Study Completion Date

2033-10-24

Brief Summary

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This is a phase 3, prospective, open-label, single-arm, single-dose, multicenter study investigating the efficacy, safety, and tolerability of CSL222 (AAV5-hFIXco-Padua) in adolescent male participants with severe or moderately severe hemophilia B.

Detailed Description

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Conditions

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Hemophilia B

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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CSL222

Participants will receive CSL222 as a single intravenous (IV) infusion of 2 × 10\^13 genome copies per kilogram of body weight (gc/kg).

Group Type EXPERIMENTAL

CSL222 (Adeno-associated viral vector serotype 5 [AAV5]-hFIXco-Padua)

Intervention Type GENETIC

Administered as a single IV infusion.

Interventions

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CSL222 (Adeno-associated viral vector serotype 5 [AAV5]-hFIXco-Padua)

Administered as a single IV infusion.

Intervention Type GENETIC

Other Intervention Names

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Etranacogene Dezaparvovec

Eligibility Criteria

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Inclusion Criteria

Assigned male sex at birth

* Aged ≥138 months (11 years and 6 months) to less than (\<) 206 months (17 years and 2 months) at the time of informed consent / assent.
* Congenital hemophilia B with known severe or moderately severe FIX deficiency (less than or equal to \[≤\] 2% of normal circulating FIX) for which the participant has been on continuous FIX prophylaxis.
* On stable continuous FIX prophylaxis for at least 2 months before Screening.
* Minimum of 75 previous exposure days of treatment with FIX protein before Screening.

Completed the Lead-in Period: minimum of 6 months (26 weeks) of lead-in data collected and eligibility has been confirmed.

* Aged ≥ 12 to \< 18 years at the time of CSL222 treatment.

Exclusion Criteria

History of FIX inhibitors or positive FIX inhibitor test at Screening (based on central laboratory results).

* Screening laboratory values (based on central laboratory results):

* Total bilirubin \> 2 × the upper limit of normal (ULN).
* Alanine aminotransferase (ALT) \> 2 × the ULN.
* Aspartate aminotransferase (AST) \> 2 × the ULN.
* Alkaline phosphatase (ALP) \> 2 × the ULN.
* Serum creatinine \> 2 × the ULN.
* Hemoglobin \< 8 g/dL.
* Any condition other than hemophilia B resulting in an increased bleeding tendency.
* Thrombocytopenia, defined as a platelet count below 50 × 10\^9/L, at screening (based on central laboratory results).
* Any uncontrolled or untreated infection (human immunodeficiency virus, hepatitis C, etc) or any other significant concurrent, uncontrolled medical condition, as evaluated by the investigator, including, but not limited to renal, hepatic, cardiovascular, hematological, gastrointestinal, endocrine, pulmonary, neurological, cerebral, or psychiatric disease, alcoholism, drug dependency, or any other psychological disorder evaluated by the investigator to interfere with adherence to the Clinical Study Protocol procedures or with the degree of tolerance to CSL222.

Positive FIX inhibitor test at Visit L-Final (based on central laboratory results)

* AAV5 NAb titer \> 1:900 as assessed at Visit LX (last visit before Visit L-Final).
* Visit L-Final laboratory values (based on central laboratory results) of:

* Total bilirubin \> 2 × the ULN
* ALT \> 2 × the ULN.
* AST \> 2 × the ULN.
* ALP \> 2 × the ULN.
* Serum creatinine \> 2 × the ULN.
* Hemoglobin \< 8 g/dL.
* Thrombocytopenia, defined as a platelet count below 50 × 10\^9/L, at Visit L-Final (based on central laboratory results).
Minimum Eligible Age

138 Months

Maximum Eligible Age

206 Months

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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CSL Behring

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Study Director

Role: STUDY_DIRECTOR

CSL Behring

Locations

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University of Florida - 84000399

Gainesville, Florida, United States

Site Status RECRUITING

University of Michigan Medical Center - 84000491

Ann Arbor, Michigan, United States

Site Status RECRUITING

Countries

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United States

Central Contacts

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Trial Registration Coordinator

Role: CONTACT

1-610-878-4697

Facility Contacts

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Trial Contact

Role: primary

352-294-8846

Trial Contact

Role: primary

734-232-9335

Other Identifiers

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2023-505805-18-00

Identifier Type: CTIS

Identifier Source: secondary_id

CSL222_3004

Identifier Type: -

Identifier Source: org_study_id