A Study to Investigate the Safety and Biodistribution of a Single Intrathecal (IT) Injection of INS1201 in Ambulatory Males With Duchenne Muscular Dystrophy (DMD)

NCT ID: NCT06817382

Last Updated: 2025-11-10

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1

Total Enrollment

12 participants

Study Classification

INTERVENTIONAL

Study Start Date

2025-07-22

Study Completion Date

2028-03-31

Brief Summary

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The primary objective of this study is to evaluate the safety and tolerability of a single dose of INS1201 via IT administration in ambulatory male participants with DMD.

Detailed Description

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Conditions

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Duchenne Muscular Dystrophy

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

SEQUENTIAL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Part 1: Cohort 1

Participants aged 3 to \<5 years will receive a single dose level 1 of INS1201 by IT injection on Day 1.

Group Type EXPERIMENTAL

INS1201

Intervention Type GENETIC

Suspension for IT injection.

Part 1: Cohort 2

Participants aged 3 to \<5 years will receive a single dose level 2 of INS1201 by IT injection on Day 1.

Group Type EXPERIMENTAL

INS1201

Intervention Type GENETIC

Suspension for IT injection.

Part 2: Cohort 3

Participants aged 2 to \<3 years will receive a single dose level 1 of INS1201 by IT injection on Day 1.

Group Type EXPERIMENTAL

INS1201

Intervention Type GENETIC

Suspension for IT injection.

Part 2: Cohort 4

Participants aged 2 to \<3 years will receive a single dose level 2 of INS1201 by IT injection on Day 1.

Group Type EXPERIMENTAL

INS1201

Intervention Type GENETIC

Suspension for IT injection.

Interventions

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INS1201

Suspension for IT injection.

Intervention Type GENETIC

Eligibility Criteria

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Inclusion Criteria

* Participant must be male at birth, 3 to \<5 years of age, inclusive (Part 1) and 2 to \<3 years of age (Part 2), at the time of legally authorized representative (LAR) signing and dating the informed consent form.
* Ambulatory -as defined as the ability to walk at least 10 meters unassisted (ie, without personal assistance or use of any assistive devices) Note: children who have not yet developed the ability to walk by the time of screening (for whatever reason) will not be eligible for the study.
* Has a definitive diagnosis of DMD prior to Screening or as part of Screening based on genetic testing. Note that participants who rescreen do not have to repeat genetic testing for the diagnosis of DMD if one is already on file. Genetic reports must describe a frameshift deletion, frameshift duplication, premature stop ("nonsense"), canonical splice site mutation, or other pathogenic variant in the DMD gene fully contained between exons 18 to 58 (inclusive) that is expected to lead to absence of a functional dystrophin protein (mutations in exons 1-17 or 59-71 are therefore not permitted).
* Able to cooperate with motor assessment testing.
* Has received vaccinations recommended for the participant's age and DMD disease according to Centers for Disease Control and Prevention (CDC) Child and Adolescent Immunization Schedule by Age, World Health Organization, or local recommendation incorporating the Advisory Committee on Immunization Practices (ACIP) Vaccine Recommendations and Guidelines for Patients with Altered Immunocompetence.

Exception is made for seasonal influenza and coronavirus disease 2019 (COVID-19) vaccines, for which shared decision-making with the participant's physician is encouraged.

Exclusion Criteria

* Prior treatment with gene or cell-based therapy at any time.
* Oligonucleotide-based exon skipping or small molecule stop codon readthrough-promoting therapies for at least 6 months prior to enrolment.
* Has left ventricular ejection fraction \< 50% on the screening echocardiogram (ECHO) or clinical signs and/or symptoms of cardiomyopathy.
* Has cardiac arrhythmia or significant electrocardiogram (ECG) interval abnormalities.
* Major surgery within 3 months prior to Day 1 or planned surgery or procedures that would interfere with the conduct of the study at any time during this study.
* The presence of any other clinically significant illness, including cardiac, pulmonary, hepatic, renal, hematologic, immunologic/allergic, behavioural disease, infection, unhealed injury, malignancy, concomitant illness, extenuating circumstance, or requirement for chronic drug treatment that, in the opinion of the Investigator:

1. Creates unnecessary risks for undergoing gene transfer;
2. Might compromise the participant's ability to comply with the protocol-required testing or procedures; or
3. Might compromise the participant's well-being, safety, or clinical interpretability.
* Has serological evidence of current, chronic, or active human immunodeficiency virus, hepatitis C, or hepatitis B infection.
* Has signs of clinically significant symptomatic infection (eg, upper respiratory tract infection, pneumonia, pyelonephritis, meningitis) within 4 weeks prior to Day 1.
* Has contraindications for IT administration of the product or for lumbar puncture, such as anatomical abnormalities, bleeding disorders or other medical conditions (eg, spina bifida, meningitis, or significant clotting abnormalities).
* Demonstrates cognitive or developmental delay or impairment that could confound assessment of motor development in the opinion of the Investigator.
* Total serum anti-AAV9 antibody titers of \> 1:50 as determined by ELISA within 14 days of Day 1.
Minimum Eligible Age

2 Years

Maximum Eligible Age

4 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Insmed Gene Therapy LLC

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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USA012

Little Rock, Arkansas, United States

Site Status RECRUITING

USA010

Davis, California, United States

Site Status RECRUITING

USA002

Palo Alto, California, United States

Site Status RECRUITING

Rare Disease Research (USA004)

Atlanta, Georgia, United States

Site Status RECRUITING

USA008

Rochester, New York, United States

Site Status RECRUITING

USA006

Columbus, Ohio, United States

Site Status RECRUITING

USA001

Memphis, Tennessee, United States

Site Status RECRUITING

USA015

Norfolk, Virginia, United States

Site Status RECRUITING

Countries

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United States

Central Contacts

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Insmed Medical Information

Role: CONTACT

Phone: 18444467633

Email: [email protected]

Facility Contacts

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Kendra Stroud

Role: primary

Amanda Marie Figueroa Lopez

Role: primary

Rabia Farooquee

Role: primary

Laura Sutton

Role: primary

Role: primary

Abigail Hanson

Role: primary

Colin Quillivan

Role: primary

Patty Smith

Role: primary

Other Identifiers

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INS1201-101

Identifier Type: -

Identifier Source: org_study_id