A Study to Test Whether Nerandomilast Helps People With Lungfibrosis Related to Rheumatic Diseases

NCT ID: NCT06806592

Last Updated: 2025-11-12

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE3

Total Enrollment

400 participants

Study Classification

INTERVENTIONAL

Study Start Date

2025-09-13

Study Completion Date

2027-07-30

Brief Summary

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Adults 18 years of age and older or above legal age with lung fibrosis related to systemic autoimmune rheumatic disease can participate in this study. People can only take part if they show no improvement in lung function after standard treatment with immunosuppressant medicine. The main purpose of this study is to find out how a medicine called nerandomilast affects the lungs in people with systemic autoimmune rheumatic disease.

Participants are put into 2 groups randomly, which means by chance. One group takes nerandomilast tablets and the other group takes placebo tablets. Placebo tablets look like nerandomilast tablets but do not contain any medicine. Participants take a tablet 2 times a day for at least 26 weeks and up to 1 year. Participants continue immunosuppressant treatment for their underlying rheumatic disease.

Participants are in the study for about 7.5 to 13 months depending on when they join the study. During this time, they visit the study site about 9 to 10 times. At study visits, participants have lung function tests. At select visits, chest imaging is performed. Participants fill in questionnaires about their symptoms and quality of life. The results between the 2 groups are compared to see whether the treatment works. The doctors also regularly check participants' health and take note of any unwanted effects.

Detailed Description

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Conditions

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Interstitial Lung Diseases Systemic Autoimmune Rheumatic Diseases Associated Interstitial Lung Diseases

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Nerandomilast

Participants with SARD-ILDs will receive nerandomilast.

Group Type EXPERIMENTAL

Nerandomilast

Intervention Type DRUG

Nerandomilast

Placebo

Participants with SARD-ILDs will receive placebo.

Group Type PLACEBO_COMPARATOR

Placebo matching nerandomilast

Intervention Type DRUG

Placebo matching nerandomilast

Interventions

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Nerandomilast

Nerandomilast

Intervention Type DRUG

Placebo matching nerandomilast

Placebo matching nerandomilast

Intervention Type DRUG

Other Intervention Names

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JASCAYD®

Eligibility Criteria

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Inclusion Criteria

* Participant has systemic autoimmune rheumatic diseases associated interstitial lung diseases (SARD-ILD), defined as

* Diagnosis by a rheumatologist with at least 1 of the following SARDs: Rheumatoid arthritis (RA), systemic sclerosis (SSc) (participants must be anticentromere auto-antibody negative), idiopathic inflammatory myopathy (IIM), Sjögren's disease, or Mixed connective tissue disease (MCTD)
* Presence of fibrotic interstitial lung disease (ILD) on high-resolution computed tomography (HRCT), defined as presence of reticular abnormality with traction bronchiectasis with or without honeycombing (HC), with disease extent \>10% on HRCT performed within 12 months of Visit 1 or, if historical scan is not available, on baseline HRCT taken prior to Visit 2, as confirmed by central review
* No lung function improvement and no clinically significant ILD improvement as a treatment response to immunosuppressant (IS) therapy according to both criteria:

* No improvement in absolute forced vital capacity (FVC) % predicted \>5% within the 15 months prior to Visit 1, as measured by 2 spirometry assessments that must be ≥3 months apart. (Note: Visit 1 spirometry may be used to fulfill the inclusion criterion if there is only 1 spirometry reading in the 15 months prior to Visit 1)
* No clinically significant improvement in ILD based on clinician's judgement (including symptoms, imaging/HRCT, or other assessments as considered relevant and documented by the Investigator)
* FVC ≥45% of predicted normal at Visit 1
* Diffusing capacity of the lungs for carbon monoxide (DLCO) ≥25% of predicted normal corrected for haemoglobin (Hb) within 3 months prior to or at Visit 1
* Participants must be on stable treatment with any IS agent for ≥6 months (or ≥3 months for participants with IIM-ILD) with the following specifications:

* If using prednisone, participants must be on stable dose for ≥4 weeks prior to Visit 2
* If using rituximab, participants must have completed their first cycle \>6 months prior to Visit 2
* If using nintedanib, participants must be on a stable dose for ≥12 weeks prior to Visit 2
* In the opinion of the Investigator, no change in background standard of care (SoC) treatment with immunosuppressant (IS), immunomodulator (IM), or nintedanib is planned

Exclusion Criteria

* Organising pneumonia as predominant pattern in the HRCT
* Prebronchodilator forced expiratory volume in 1 second (FEV1)/ forced vital capacity (FVC) \<0.7 at Visit 1
* Acute ILD exacerbation within 3 months prior to Visit 1 and/or during the screening period, based on Investigator judgement
* Active vasculitis, unstable or uncontrolled within 8 weeks prior to Visit 1 or during the screening period
* Any suicidal behaviour in the past 2 years
* Any suicidal ideation of type 4 or 5 on the Columbia-Suicide Severity Rating Scale (C-SSRS) in the past 3 months or at Visit 1, and/or at Visit 2
* Use of any of the following medications: cyclophosphamide within 6 months of Visit 1, pirfenidone within 8 weeks of Visit 1
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Boehringer Ingelheim

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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University of Alabama at Birmingham

Birmingham, Alabama, United States

Site Status NOT_YET_RECRUITING

Mayo Clinic-Arizona

Scottsdale, Arizona, United States

Site Status NOT_YET_RECRUITING

University of California Los Angeles

Los Angeles, California, United States

Site Status NOT_YET_RECRUITING

Paradigm Clinical Research - San Diego

San Diego, California, United States

Site Status NOT_YET_RECRUITING

National Jewish Health

Denver, Colorado, United States

Site Status RECRUITING

Yale University School of Medicine

New Haven, Connecticut, United States

Site Status NOT_YET_RECRUITING

Meris Clinical Research-Brandon-69466

Brandon, Florida, United States

Site Status NOT_YET_RECRUITING

Miami VA Healthcare System

Miami, Florida, United States

Site Status NOT_YET_RECRUITING

Piedmont Physicians Pulmonary & Sleep Medicine of Buckhead

Atlanta, Georgia, United States

Site Status NOT_YET_RECRUITING

Augusta University

Augusta, Georgia, United States

Site Status NOT_YET_RECRUITING

Northwestern University

Chicago, Illinois, United States

Site Status NOT_YET_RECRUITING

University of Chicago

Chicago, Illinois, United States

Site Status NOT_YET_RECRUITING

Northshore University Health System

Evanston, Illinois, United States

Site Status NOT_YET_RECRUITING

University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status RECRUITING

LSU Health Sciences Center

New Orleans, Louisiana, United States

Site Status NOT_YET_RECRUITING

Massachusetts General Hospital

Boston, Massachusetts, United States

Site Status NOT_YET_RECRUITING

Brigham and Women's Hospital

Boston, Massachusetts, United States

Site Status NOT_YET_RECRUITING

University of Minnesota

Minneapolis, Minnesota, United States

Site Status RECRUITING

Mayo Clinic

Rochester, Minnesota, United States

Site Status NOT_YET_RECRUITING

University of Nebraska Medical Center

Omaha, Nebraska, United States

Site Status NOT_YET_RECRUITING

Northwell Health

Great Neck, New York, United States

Site Status NOT_YET_RECRUITING

NYU Langone Health

New York, New York, United States

Site Status RECRUITING

Columbia University Medical Center-New York Presbyterian Hospital

New York, New York, United States

Site Status NOT_YET_RECRUITING

Onsite Clinical Solutions

Salisbury, North Carolina, United States

Site Status NOT_YET_RECRUITING

Southeastern Research Center-Winston Salem-69289

Winston-Salem, North Carolina, United States

Site Status RECRUITING

Cleveland Clinic

Cleveland, Ohio, United States

Site Status NOT_YET_RECRUITING

Temple Lung Center

Philadelphia, Pennsylvania, United States

Site Status RECRUITING

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, United States

Site Status NOT_YET_RECRUITING

The University of Texas Health Science Center at Houston

Houston, Texas, United States

Site Status NOT_YET_RECRUITING

University of Texas Health Science Center at San Antonio

San Antonio, Texas, United States

Site Status NOT_YET_RECRUITING

University of Utah Health Sciences Center

Salt Lake City, Utah, United States

Site Status NOT_YET_RECRUITING

Rheumatology and Pulmonary Clinic

Beckley, West Virginia, United States

Site Status NOT_YET_RECRUITING

University of Wisconsin

Madison, Wisconsin, United States

Site Status NOT_YET_RECRUITING

Royal Prince Alfred Hospital

Camperdown, Sydney, New South Wales, Australia

Site Status NOT_YET_RECRUITING

St Vincent's Hospital Sydney

Darlinghurst, New South Wales, Australia

Site Status NOT_YET_RECRUITING

The Prince Charles Hospital

Chermside, Queensland, Australia

Site Status NOT_YET_RECRUITING

Austin Hospital

Heidelberg, Victoria, Australia

Site Status NOT_YET_RECRUITING

Fiona Stanley Hospital

Murdoch, Western Australia, Australia

Site Status NOT_YET_RECRUITING

Krems University Hospital

Krems, , Austria

Site Status NOT_YET_RECRUITING

AKH - Medical University of Vienna

Vienna, , Austria

Site Status NOT_YET_RECRUITING

Klinikum Wels - Grieskirchen GmbH

Wels, , Austria

Site Status NOT_YET_RECRUITING

Beijing Chao-Yang Hospital

Beijing, , China

Site Status NOT_YET_RECRUITING

China-Japan Friendship Hospital

Beijing, , China

Site Status RECRUITING

Peking Union Medical College Hospital

Beijing, , China

Site Status RECRUITING

West China Hospital of Sichuan University

Chengdu, , China

Site Status NOT_YET_RECRUITING

People's Hospital of Sichuan Province

Chengdu, , China

Site Status RECRUITING

Guangdong Provincial People's Hospital

Guangzhou, , China

Site Status RECRUITING

The First Affiliated Hospital, Zhejiang University

Hangzhou, , China

Site Status NOT_YET_RECRUITING

The Second Affiliated Hospital Zhejiang University School of Medicine

Hangzhou, , China

Site Status NOT_YET_RECRUITING

The First Affiliated Hospital of Henan University of Science and Technology

Luoyang, , China

Site Status RECRUITING

University Hospital_Macau University of Science and Technology

Macau, , China

Site Status NOT_YET_RECRUITING

The First Affiliated Hospital of Nanchang University

Nanchang, , China

Site Status NOT_YET_RECRUITING

Huashan Hospital, Fudan University

Shanghai, , China

Site Status NOT_YET_RECRUITING

Tianjin Medical University General Hospital

Tianjin, , China

Site Status NOT_YET_RECRUITING

Wuhan Union Hospital

Wuhan, , China

Site Status NOT_YET_RECRUITING

Tongji Hospital Affiliated Tongji Medical College Huazhong University of S & T

Wuhan, , China

Site Status NOT_YET_RECRUITING

First Affiliated Hospital of Xiamen University

Xiamen, , China

Site Status NOT_YET_RECRUITING

Zhuzhou Central Hospital

Zhuzhou, , China

Site Status NOT_YET_RECRUITING

HOP d'Angers

Angers, , France

Site Status NOT_YET_RECRUITING

HOP Pellegrin

Bordeaux, , France

Site Status NOT_YET_RECRUITING

HOP Claude Huriez

Lille, , France

Site Status NOT_YET_RECRUITING

Hôpital Cochin

Paris, , France

Site Status NOT_YET_RECRUITING

HOP Bichat

Paris, , France

Site Status NOT_YET_RECRUITING

HOP Sud

Rennes, , France

Site Status NOT_YET_RECRUITING

HOP Civil

Strasbourg, , France

Site Status NOT_YET_RECRUITING

HOP Rangueil

Toulouse, , France

Site Status NOT_YET_RECRUITING

Charite Universitätsmedizin Berlin KöR

Berlin, , Germany

Site Status NOT_YET_RECRUITING

Immanuel-Krankenhaus GmbH

Berlin, , Germany

Site Status NOT_YET_RECRUITING

Universitätsklinikum Bonn AöR

Bonn, , Germany

Site Status NOT_YET_RECRUITING

Städtisches Klinikum Braunschweig gGmbH

Braunschweig, , Germany

Site Status NOT_YET_RECRUITING

Gesundheit Nord gGmbH | Klinikverbund Bremen

Bremen, , Germany

Site Status NOT_YET_RECRUITING

Krankenhaus Porz am Rhein gGmbH

Cologne, , Germany

Site Status NOT_YET_RECRUITING

Universitätsklinikum Düsseldorf

Düsseldorf, , Germany

Site Status NOT_YET_RECRUITING

Universitätsklinikum Erlangen

Erlangen, , Germany

Site Status NOT_YET_RECRUITING

Ruhrlandklinik, Westdeutsches Lungenzentrum am Universitätsklinikum Essen gGmbH

Essen, , Germany

Site Status NOT_YET_RECRUITING

Universitätsklinikum Freiburg

Freiburg im Breisgau, , Germany

Site Status NOT_YET_RECRUITING

Helios Fachklinik Vogelsang-Gommern GmbH

Gommern, , Germany

Site Status NOT_YET_RECRUITING

Medizinische Hochschule Hannover

Hanover, , Germany

Site Status NOT_YET_RECRUITING

St. Elisabeth Gruppe GmbH Katholische Kliniken Rhein-Ruhr

Herne, , Germany

Site Status NOT_YET_RECRUITING

medius Kliniken gGmbH

Kirchheim unter Teck, , Germany

Site Status NOT_YET_RECRUITING

Klinikum Konstanz

Konstanz, , Germany

Site Status NOT_YET_RECRUITING

Universitätsklinikum Schleswig-Holstein, Campus Lübeck

Lübeck, , Germany

Site Status NOT_YET_RECRUITING

Johannes Wesling Klinikum Minden

Minden, , Germany

Site Status NOT_YET_RECRUITING

Klinikum der Universität München AÖR

München, , Germany

Site Status NOT_YET_RECRUITING

Krankenhaus Barmherzige Brüder Regensburg

Regensburg, , Germany

Site Status NOT_YET_RECRUITING

ASST degli Spedali Civili di Brescia

Brescia, , Italy

Site Status NOT_YET_RECRUITING

A. O. Universitaria Careggi

Frienze, , Italy

Site Status NOT_YET_RECRUITING

Fondazione IRCCS Ca'Granda-Ospedale Maggiore Policlinico

Milan, , Italy

Site Status NOT_YET_RECRUITING

Ospedale San Raffaele S.r.l.

Milan, , Italy

Site Status NOT_YET_RECRUITING

Azienda Ospedaliera Policlinico di Modena

Modena, , Italy

Site Status NOT_YET_RECRUITING

Università degli Studi Padova

Padua, , Italy

Site Status NOT_YET_RECRUITING

Fondazione IRCCS Policlinico S. Matteo

Pavia, , Italy

Site Status NOT_YET_RECRUITING

AOU Policlinico Umberto I

Roma, , Italy

Site Status NOT_YET_RECRUITING

Fujita Health University Hospital

Aichi, Toyoake, , Japan

Site Status NOT_YET_RECRUITING

Hospital of the University of Occupational and Environmental Health

Fukuoka, Kitakyushu, , Japan

Site Status NOT_YET_RECRUITING

Hiroshima University Hospital

Hiroshima, Hiroshima, , Japan

Site Status NOT_YET_RECRUITING

Sapporo Medical University Hospital

Hokkaido, Sapporo, , Japan

Site Status NOT_YET_RECRUITING

Hokkaido University Hospital

Hokkaido, Sapporo, , Japan

Site Status NOT_YET_RECRUITING

Kagawa University Hospital

Kagawa, Kita-gun, , Japan

Site Status NOT_YET_RECRUITING

St. Marianna University Hospital

Kanagawa, Kawasaki, , Japan

Site Status NOT_YET_RECRUITING

Kitasato University Hospital

Kanagawa, Sagamihara, , Japan

Site Status NOT_YET_RECRUITING

Kyoto University Hospital

Kyoto, Kyoto, , Japan

Site Status NOT_YET_RECRUITING

Nagasaki University Hospital

Nagasaki, Nagasaki, , Japan

Site Status NOT_YET_RECRUITING

Osaka Medical and Pharmaceutical University Hospital

Osaka, Takatsuki, , Japan

Site Status NOT_YET_RECRUITING

Saitama Medical University Hospital

Saitama, Iruma-gun, , Japan

Site Status NOT_YET_RECRUITING

Juntendo University Hospital

Tokyo, Bunkyo-Ku, , Japan

Site Status NOT_YET_RECRUITING

Nippon Medical School Hospital

Tokyo, Bunkyo-ku, , Japan

Site Status RECRUITING

Keio University Hospital

Tokyo, Shinjuku-ku, , Japan

Site Status NOT_YET_RECRUITING

Investigacion y Biomedicina de Chihuahua S.C.

Chihuahua City, , Mexico

Site Status NOT_YET_RECRUITING

Centro Integral en Reumatologia, SA. de CV.

Guadalajara, , Mexico

Site Status NOT_YET_RECRUITING

Soltmed Smo

Mexico City, , Mexico

Site Status NOT_YET_RECRUITING

CITER Centro de Investigación y Tratamiento de las Enfermedades Reumaticas SA de CV

Mexico City, , Mexico

Site Status NOT_YET_RECRUITING

Inst Nac de Ciencias Medicas y Nutricion Salvador Zubiran

Mexico City, , Mexico

Site Status NOT_YET_RECRUITING

Medical Care & Research SA de CV

Mérida, , Mexico

Site Status NOT_YET_RECRUITING

Hospital Universitario Dr Jose Eleuterio Gonzalez

Monterrey, , Mexico

Site Status NOT_YET_RECRUITING

Zuyderland Medisch Centrum

Heerlen, , Netherlands

Site Status NOT_YET_RECRUITING

St. Antonius ziekenhuis, locatie Nieuwegein

Nieuwegein, , Netherlands

Site Status NOT_YET_RECRUITING

Erasmus Medisch Centrum-ROTTERDAM-50697

Rotterdam, , Netherlands

Site Status NOT_YET_RECRUITING

Akershus Universitetssykehus HF

Nordbyhagen, , Norway

Site Status NOT_YET_RECRUITING

Sykehuset Telemark HF, Avd. Skien

Skien, , Norway

Site Status NOT_YET_RECRUITING

GCM Medical Group, PSC

San Juan, , Puerto Rico

Site Status NOT_YET_RECRUITING

Seoul National University Bundang Hospital

Seongnam, , South Korea

Site Status NOT_YET_RECRUITING

Kyung Hee University Hospital

Seoul, , South Korea

Site Status NOT_YET_RECRUITING

Seoul National University Hospital

Seoul, , South Korea

Site Status NOT_YET_RECRUITING

Soonchunhyang University Hospital Seoul

Seoul, , South Korea

Site Status RECRUITING

Hospital Santa Creu i Sant Pau

Barcelona, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitari Vall D Hebron

Barcelona, , Spain

Site Status NOT_YET_RECRUITING

Hospital de Basurto

Bilbao, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitario Reina Sofía

Córdoba, , Spain

Site Status NOT_YET_RECRUITING

Hospital Juan Ramón Jimenez

Huelva, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitari de Bellvitge

L'Hospitalet de Llobregat, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitario Ramon Y Cajal

Madrid, , Spain

Site Status NOT_YET_RECRUITING

Fundación Jiménez Díaz

Madrid, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitario 12 de Octubre

Madrid, , Spain

Site Status NOT_YET_RECRUITING

Hospital Clínico de Santiago

Santiago de Compostela, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitario Virgen De La Macarena

Seville, , Spain

Site Status NOT_YET_RECRUITING

Hospital Virgen del Rocío

Seville, , Spain

Site Status NOT_YET_RECRUITING

Hospital Dr. Peset

Valencia, , Spain

Site Status NOT_YET_RECRUITING

Complejo Hospitalario Universitario de Vigo

Vigo, , Spain

Site Status NOT_YET_RECRUITING

Cantonal Hospital of Aarau

Aarau, , Switzerland

Site Status NOT_YET_RECRUITING

Universitätsspital Basel

Basel, , Switzerland

Site Status NOT_YET_RECRUITING

Hopitaux Universitaires de Geneve (HUG)

Geneva, , Switzerland

Site Status NOT_YET_RECRUITING

Neuchatel Hospital Network

Neuchâtel, , Switzerland

Site Status NOT_YET_RECRUITING

Kantonsspital St.Gallen

Sankt Gallen, , Switzerland

Site Status NOT_YET_RECRUITING

University Hospital Zurich

Zurich, , Switzerland

Site Status NOT_YET_RECRUITING

Antrim Area Hospital

Antrim, , United Kingdom

Site Status RECRUITING

Royal United Hospital, Bath

Bath, , United Kingdom

Site Status NOT_YET_RECRUITING

Heartlands Hospital

Birmingham, , United Kingdom

Site Status NOT_YET_RECRUITING

Chapel Allerton Hospital

Leeds, , United Kingdom

Site Status NOT_YET_RECRUITING

St George's Hospital-London-26733

London, , United Kingdom

Site Status RECRUITING

University College Hospital

London, , United Kingdom

Site Status NOT_YET_RECRUITING

Altnagelvin Area Hospital

Londonderry, , United Kingdom

Site Status NOT_YET_RECRUITING

Luton & Dunstable University Hospital

Luton, , United Kingdom

Site Status NOT_YET_RECRUITING

NIHR Lancashire Clinical Research Facility

Preston, , United Kingdom

Site Status NOT_YET_RECRUITING

Northern General Hospital

Sheffield, , United Kingdom

Site Status NOT_YET_RECRUITING

Royal Cornwall Hospital

Truro, , United Kingdom

Site Status NOT_YET_RECRUITING

Southend University Hospital

Westcliffe-on-Sea, , United Kingdom

Site Status NOT_YET_RECRUITING

Countries

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United States Australia Austria China France Germany Italy Japan Mexico Netherlands Norway Puerto Rico South Korea Spain Switzerland United Kingdom

Central Contacts

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Boehringer Ingelheim

Role: CONTACT

Phone: 1-800-243-0127

Email: [email protected]

Facility Contacts

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Boehringer Ingelheim

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Related Links

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Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

2024-512849-17-00

Identifier Type: REGISTRY

Identifier Source: secondary_id

U1111-1305-5857

Identifier Type: REGISTRY

Identifier Source: secondary_id

1305-0046

Identifier Type: -

Identifier Source: org_study_id