A Phase 2 Trial of ALN-APP in Patients With Cerebral Amyloid Angiopathy

NCT ID: NCT06393712

Last Updated: 2025-11-13

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE2

Total Enrollment

200 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-05-17

Study Completion Date

2029-11-01

Brief Summary

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The purpose of the study is to evaluate the effect of ALN-APP on measures of CAA disease progression and to characterize the safety, tolerability, and pharmacodynamics (PD) of ALN-APP in adult patients with sporadic CAA (sCAA) and Dutch-type CAA (D-CAA). The study will be conducted over 2 periods: a 24-month double-blind treatment period and an optional 18-month open-label extension (OLE) period. The estimated duration of study participation, inclusive of screening, treatment, and additional safety follow-up, is up to 50 months.

Detailed Description

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Conditions

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Cerebral Amyloid Angiopathy

Keywords

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CAA

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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ALN-APP

Participants will be administered multiple doses of ALN-APP during the double-blind treatment period and optional open-label extension period.

Group Type EXPERIMENTAL

ALN-APP

Intervention Type DRUG

ALN-APP will be administered intrathecally

Placebo/ALN-APP

Participants will be administered multiple doses of placebo during the double-blind treatment period. Participants who continue into the optional open-label extension period will be administered multiple doses of ALN-APP.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Placebo will be administered intrathecally

ALN-APP

Intervention Type DRUG

ALN-APP will be administered intrathecally

Interventions

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Placebo

Placebo will be administered intrathecally

Intervention Type DRUG

ALN-APP

ALN-APP will be administered intrathecally

Intervention Type DRUG

Other Intervention Names

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mivelsiran

Eligibility Criteria

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Inclusion Criteria

* Is 50 years or older
* Has probable CAA per the Boston Criteria Version 2.0


* Is 30 years or older
* Has known E693Q amyloid precursor protein (APP) gene mutation for Dutch-type CAA

Exclusion Criteria

* Moderate or severe stage Alzheimer's disease (AD) or significant cognitive impairment (CI)
* Has a history of previous clinical intracerebral hemorrhage (ICH) with onset less than 90 days prior to anticipated randomization in the study
* Has alanine aminotransferase (ALT) or aspartate aminotransferase (AST) \>3×upper limit of normal (ULN) at Screening
* Has estimated glomerular filtration rate (eGFR) \<30 mL/min/1.73m\^2 at Screening
* Has recently received an investigational agent
* Has had treatment with amyloid-targeting antibody
Minimum Eligible Age

30 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Alnylam Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Medical Director

Role: STUDY_DIRECTOR

Alnylam Pharmaceuticals

Locations

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Clinical Trial Site

Palo Alto, California, United States

Site Status RECRUITING

Clinical Trial Site

Sacramento, California, United States

Site Status RECRUITING

Clinical Trial Site

San Francisco, California, United States

Site Status RECRUITING

Clinical Trial Site

Aurora, Colorado, United States

Site Status RECRUITING

Clinical Trial Site

Gainesville, Florida, United States

Site Status RECRUITING

Clinical Trial Site

Jacksonville, Florida, United States

Site Status RECRUITING

Clinical Trial Site

Maitland, Florida, United States

Site Status RECRUITING

Clinical Trial Site

Naples, Florida, United States

Site Status RECRUITING

Clinical Trial Site

Chicago, Illinois, United States

Site Status RECRUITING

Clinical Trial Site

Lexington, Kentucky, United States

Site Status RECRUITING

Clinical Trial Site

New Orleans, Louisiana, United States

Site Status RECRUITING

Clinical Trial Site

Boston, Massachusetts, United States

Site Status RECRUITING

Clinical Trial Site

Plymouth, Massachusetts, United States

Site Status RECRUITING

Clinical Trial Site

Rochester, Minnesota, United States

Site Status RECRUITING

Clinical Trial Site

St Louis, Missouri, United States

Site Status RECRUITING

Clinical Trial Site

Hackensack, New Jersey, United States

Site Status RECRUITING

Clinical Trial Site

New York, New York, United States

Site Status RECRUITING

Clinical Trial Site

New York, New York, United States

Site Status RECRUITING

Clinical Trial Site

New York, New York, United States

Site Status RECRUITING

Clinical Trial Site

Durham, North Carolina, United States

Site Status RECRUITING

Clinical Trial Site

Canton, Ohio, United States

Site Status RECRUITING

Clinical Trial Site

Cleveland, Ohio, United States

Site Status RECRUITING

Clinical Trial Site

Abington, Pennsylvania, United States

Site Status RECRUITING

Clinical Trial Site

Philadelphia, Pennsylvania, United States

Site Status RECRUITING

Clinical Trial Site

Dallas, Texas, United States

Site Status RECRUITING

Clinical Trial Site

Dallas, Texas, United States

Site Status RECRUITING

Clinical Trial Site

Houston, Texas, United States

Site Status RECRUITING

Clinical Trial Site

San Antonio, Texas, United States

Site Status RECRUITING

Clinical Trial Site

Seattle, Washington, United States

Site Status RECRUITING

Clinical Trial Site

Heidelberg, , Australia

Site Status RECRUITING

Clinical Trial Site

Herston, , Australia

Site Status RECRUITING

Clinical Trial Site

Nedlands, , Australia

Site Status RECRUITING

Clinical Trial Site

Parkville, , Australia

Site Status RECRUITING

Clinical Trial Site

Calgary, Alberta, Canada

Site Status RECRUITING

Clinical Trial Site

Richmond, British Columbia, Canada

Site Status RECRUITING

Clinical Trial Site

Victoria, British Columbia, Canada

Site Status RECRUITING

Clinical Trial Site

Moncton, New Brunswick, Canada

Site Status RECRUITING

Clinical Trial Site

Hamilton, Ontario, Canada

Site Status RECRUITING

Clinical Trial Site

Ottawa, Ontario, Canada

Site Status RECRUITING

Clinical Trial Site

Toronto, Ontario, Canada

Site Status RECRUITING

Clinical Trial Site

Montreal, Quebec, Canada

Site Status RECRUITING

Clinical Trial Site

Montreal, , Canada

Site Status RECRUITING

Clinical Trial Site

Richmond, , Canada

Site Status RECRUITING

Clinical Trial Site

Amsterdam, , Netherlands

Site Status RECRUITING

Clinical Trial Site

Leiden, , Netherlands

Site Status RECRUITING

Clinical Trial Site

Nijmegen, , Netherlands

Site Status RECRUITING

Clinical Trial Site

Bern, , Switzerland

Site Status RECRUITING

Clinical Trial Site

Geneva, , Switzerland

Site Status RECRUITING

Clinical Trial Site

Denmark Hill, , United Kingdom

Site Status RECRUITING

Clinical Trial Site

Glasgow, , United Kingdom

Site Status RECRUITING

Clinical Trial Site

London, , United Kingdom

Site Status RECRUITING

Countries

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United States Australia Canada Netherlands Switzerland United Kingdom

Central Contacts

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Alnylam Clinical Trial Information Line

Role: CONTACT

Phone: 1-877-ALNYLAM

Email: [email protected]

Alnylam Clinical Trial Information Line

Role: CONTACT

Phone: 1-877-256-9526

Email: [email protected]

Other Identifiers

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2023-510137-29-00

Identifier Type: CTIS

Identifier Source: secondary_id

ALN-APP-002

Identifier Type: -

Identifier Source: org_study_id