A Clinical Trial to Evaluate Efficacy and Safety of TransCon CNP Compared With Placebo in Infants (0 to <2 Years of Age) With Achondroplasia

NCT ID: NCT06079398

Last Updated: 2025-11-26

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

RECRUITING

Clinical Phase

PHASE2

Total Enrollment

72 participants

Study Classification

INTERVENTIONAL

Study Start Date

2024-01-23

Study Completion Date

2027-03-31

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

This trial is a Phase 2, multicenter, double-blind, randomized (ratio 2:1 TransCon CNP vs. placebo), placebo-controlled trial, designed to evaluate the safety, tolerability, and efficacy of 100 μg CNP/kg of Navepegritide (TransCon CNP) administered SC once-weekly for 52 weeks in infants with genetically verified heterozygous ACH, aged 0 to \< 2 years at the time of randomization.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Achondroplasia

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Navepegritide

Once weekly double-blinded treatment with SC injection of 100 µg/kg of Navepegritide for 52 weeks

Group Type EXPERIMENTAL

Navepegritide

Intervention Type DRUG

Once-weekly subcutaneous injection of 100 µg/kg Navepegritide

Placebo for Navepegritide

Once weekly double-blinded treatment with SC injection of 100 µg/kg of Placebo for Navepegritide for 52 weeks

Group Type PLACEBO_COMPARATOR

Placebo for Navepegritide

Intervention Type DRUG

Once-weekly subcutaneous injection of 100 µg/kg placebo for Navepegritide

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

Navepegritide

Once-weekly subcutaneous injection of 100 µg/kg Navepegritide

Intervention Type DRUG

Placebo for Navepegritide

Once-weekly subcutaneous injection of 100 µg/kg placebo for Navepegritide

Intervention Type DRUG

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

* Written, signed informed consent by the parent(s)/caregiver(s) of the participant, and as required by the institutional review board/human research ethics committee/independent ethics committee (IRB/HREC/IEC).
* Male or female younger than 2 years of age at the time of randomization; or for open label sentinel participants, at the time of first administration of IMP.
* Clinical diagnosis of achondroplasia (ACH) with genetic confirmation of heterozygous genotype present during screening.
* Parent(s)/caregiver(s) willing to follow the protocol and instructions provided, including being able to administer weekly subcutaneous injections of trial treatment.
* Compliance to daily Vitamin D supplementation for infants aged 14 days to 1 year. All participants older than 1 year of age with serum 25-hydroxyvitamin D (25OHD) measured below lower limit of reference range at screening should start daily Vitamin D supplementation prior to randomization.
* Considered eligible based on the medical history, physical examination, and the results of vital signs, ECG, imaging, and clinical laboratory tests performed during the screening period.

Exclusion Criteria

* Known or suspected hypersensitivity to the investigational product or related products (trehalose, tris\[hydroxymethyl\]aminomethane, succinate, and polyethylene glycol \[PEG\]).
* Genetic confirmation of ACH homozygous genotype.
* Premature birth with gestational age \< 32 weeks.
* Premature birth with gestational age 32 to 37 weeks, unless time from birth is \> 6 months at the time of screening and the child is in good nutritional status, defined as gain in body weight expected for age and diagnosis of ACH, as determined by the Investigator and confirmed with the Medical Monitor.
* Anticipated, as assessed by Investigator and confirmed with Medical Monitor, to undergo surgical intervention during trial participation, including cervicomedullary decompression. Evaluation of immediate risk of requiring cervicomedullary decompression surgery will rely on the following assessments:

* Physical examination (e.g., neurologic findings of clonus, opisthotonus, exaggerated reflexes, dilated facial veins)
* Evidence of uncontrolled sleep apnea as confirmed by local standard of care assessment (e.g. polysomnography or simple sleep test) performed within 6 months prior to screening.
* MRI performed at screening indicating presence of severe cervicomedullary compression (CMC) or spinal cord damage. Presence of abnormal MRI T2 signal intensity at and immediately above and below the cervicomedullary junction should be considered high risk for requiring surgery and the participant is not eligible for trial participation.

Common surgeries, such as insertion of grommets, adenoidectomy, tonsillectomy, or myringotomy tube placement are permitted during trial participation.

* Have a growth disorder or medical condition, other than ACH, resulting in short stature or abnormal growth as determined by the Investigator and confirmed with the Medical Monitor.
* Have received any dose of prescription medications and/or investigational medicinal product or device intended to affect stature, growth, or body proportionality (including human growth hormone or vosoritide) at any time.
* Requires or anticipated to require chronic (\> 4 weeks) or repeated treatment (more than twice/year) with oral corticosteroids, or high-dose inhaled corticosteroids during trial participation.
* History or presence of injury or disease of the growth plate(s), other than ACH, affecting growth potential of long bones, including Salter-Harris fracture and recent bone-related surgery, as determined by Investigator and confirmed with the Medical Monitor.
* Have a clinically significant finding indicating abnormal cardiac function, including but not limited to:

* Repaired or unrepaired coarctation.
* Moderate or greater complexity congenital heart disease including tetralogy of Fallot, atrioventricular septal defects, truncus arteriosus, total anomalous pulmonary venous return, double outlet right ventricle, or single ventricle heart disease.
* QTcF ≥ 450 msec on screening 12-lead ECG.
* History or presence of a condition impacting hemodynamic stability (such as autonomic dysfunction and orthostatic intolerance).
* History or presence of the following:

* Chronic anemia.
* Chronic renal insufficiency.
* Chronic or recurrent illness that can affect hydration or volume status, including conditions associated with decreased nutritional intake or increased volume loss.
* History or presence of malignant disease.
* Any disease or condition that, in the opinion of the Investigator, may make the participant unlikely to fully complete the trial, not adhering to trial procedures, may confound interpretation of trial results, or may present undue risk from receiving trial treatment. This could include family situations, comorbid conditions, or medications that might impact safety or be considered confounding.
Minimum Eligible Age

0 Years

Maximum Eligible Age

2 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Ascendis Pharma A/S

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Medical Director, MD

Role: STUDY_DIRECTOR

Ascendis Pharma A/S

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Ascendis Investigational Site

Saint Paul, Minnesota, United States

Site Status RECRUITING

Ascendis Investigational Site

Houston, Texas, United States

Site Status RECRUITING

Ascendis Investigational Site

Madison, Wisconsin, United States

Site Status RECRUITING

Ascendis Investigational Site

Parkville, , Australia

Site Status RECRUITING

Ascendis Investigational Site

Linz, , Austria

Site Status RECRUITING

Ascendis Investigational Site

Copenhagen, , Denmark

Site Status RECRUITING

Ascendis Investigational Site

Helsinki, , Finland

Site Status RECRUITING

Ascendis Investigational Site

Paris, , France

Site Status RECRUITING

Ascendis Investigational Site

Berlin, , Germany

Site Status RECRUITING

Ascendis Investigational Site

Cologne, , Germany

Site Status RECRUITING

Ascendis Investigational Site

Dublin, , Ireland

Site Status RECRUITING

Ascendis Investigational Site

Milan, , Italy

Site Status RECRUITING

Ascendis Investigational Site

Auckland, , New Zealand

Site Status RECRUITING

Ascendis Investigational Site

Oslo, , Norway

Site Status RECRUITING

Ascendis Investigational Site

Coimbra, , Portugal

Site Status RECRUITING

Ascendis Investigational Site

Stockholm, , Sweden

Site Status RECRUITING

Ascendis Investigational Site

London, , United Kingdom

Site Status RECRUITING

Countries

Review the countries where the study has at least one active or historical site.

United States Australia Austria Denmark Finland France Germany Ireland Italy New Zealand Norway Portugal Sweden United Kingdom

Central Contacts

Reach out to these primary contacts for questions about participation or study logistics.

Ascendis Registry Inquiries

Role: CONTACT

+45 61242484

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

ASND0030

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.