Phase 2 Study of EDG-5506 in Becker Muscular Dystrophy (GRAND CANYON)

NCT ID: NCT05291091

Last Updated: 2026-02-02

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE2

Total Enrollment

244 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-11-10

Study Completion Date

2026-09-30

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

A study of sevasemten (EDG-5506) in Becker muscular dystrophy (known as CANYON) and pivotal cohort (known as GRAND CANYON). The EDG-5506-201 CANYON study was expanded to include an additional 120 adult participants in a cohort called GRAND CANYON, that is a multicenter, randomized, double-blind, placebo-controlled study to evaluate the safety and efficacy of sevasemten in adults with Becker.

CANYON and GRAND CANYON are fully enrolled.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

The EDG-5506-201 protocol was amended to include an additional cohort thus consists of two parts.

Part 1: CANYON is a double-blind, randomized, placebo-controlled design to investigate the effect of sevasemten on the safety, pharmacokinetics, biomarkers, and functional measures. Approximately 32 adults and 18 adolescents with Becker muscular dystrophy are planned to enroll in this study. This study will have up to a 4-week Screening period, a 12-month Treatment period, followed by a 4-week follow-up period.

Approximately 32 adult participants will randomize to Cohort 1 or Cohort 2 in a 1:1 ratio then each cohort will further randomize to sevasemten or placebo in a 3:1 ratio.

Approximately 9 adolescent participants will enroll in Cohort 4 and randomize in a 2:1 ratio to sevasemten or placebo. Cohort 5 will randomize an additional 9 participants in a 2:1 ratio to either sevasemten or placebo after Cohort 4.

CANYON is now fully enrolled.

Part 2: GRAND CANYON or Cohort 6 is a double-blind, randomized, placebo-controlled design to investigate the safety and efficacy of sevasemten in adults with Becker muscular dystrophy after 18 months of treatment. Approximately 120 adults with Becker muscular dystrophy are planned to enroll in this study. This study will have up to a 4-week Screening period, an 18-month Treatment period, followed by a 4-week follow-up period.

Approximately 120 adult participants will be randomized in Cohort 6 in a 2:1 ratio either to sevasemten or placebo.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Becker Muscular Dystrophy

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

RANDOMIZED

Intervention Model

SEQUENTIAL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Adult Cohort 1

Drug: Sevasemten Drug: Placebo

Group Type EXPERIMENTAL

Sevasemten 10 mg

Intervention Type DRUG

Sevasemten is administered orally once per day

Placebo

Intervention Type DRUG

Placebo is administered orally once per day

Adult Cohort 2

Drug: Sevasemten Drug: Placebo

Group Type EXPERIMENTAL

Sevasemten 10 mg

Intervention Type DRUG

Sevasemten is administered orally once per day

Placebo

Intervention Type DRUG

Placebo is administered orally once per day

Adult Cohort 6

Drug: Sevasemten Drug: Placebo

Group Type EXPERIMENTAL

Sevasemten 10 mg

Intervention Type DRUG

Sevasemten is administered orally once per day

Placebo

Intervention Type DRUG

Placebo is administered orally once per day

Adolescent Cohort 4

Drug: Sevasemten Drug: Placebo

Group Type EXPERIMENTAL

Sevasemten 5 mg

Intervention Type DRUG

Sevasemten is administered orally once per day

Placebo

Intervention Type DRUG

Placebo is administered orally once per day

Adolescent Cohort 5

Drug: Sevasemten Drug: Placebo

Group Type EXPERIMENTAL

Sevasemten 12.5 mg

Intervention Type DRUG

Sevasemten is administered orally once per day

Placebo

Intervention Type DRUG

Placebo is administered orally once per day

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

Sevasemten 10 mg

Sevasemten is administered orally once per day

Intervention Type DRUG

Sevasemten 5 mg

Sevasemten is administered orally once per day

Intervention Type DRUG

Sevasemten 12.5 mg

Sevasemten is administered orally once per day

Intervention Type DRUG

Placebo

Placebo is administered orally once per day

Intervention Type DRUG

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

1. Adults (aged 18 to 50 years, inclusive) with a documented dystrophin mutation and phenotype consistent with Becker muscular dystrophy, and history of being ambulatory beyond 16 years of age without steroids; history of being ambulatory beyond 18 years of age with steroids.
2. Able to complete the 100-meter timed test in \< 200 seconds with or without use of mobility aid devices.
3. Able to perform the North Star Ambulatory Assessment scale and achieve a score of 5 to 32, inclusive.

Exclusion Criteria

1. Medical history or clinically significant physical examination/laboratory result that, in the opinion of the investigator, would render the participant unsuitable for the study. This includes contraindications to magnetic resonance imaging such as non-compatible implanted medical devices or severe claustrophobia.
2. Cardiac echocardiogram ejection fraction \< 40%
3. Forced vital capacity predicted \<60% or using daytime ventilatory support
4. Receipt of oral corticosteroids for the treatment of BMD in the previous 6 months.
5. Receipt of an investigational drug within 30 days or 5 half-lives (whichever is longer) of the screening visit in the present study.
Minimum Eligible Age

12 Years

Maximum Eligible Age

50 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Medpace, Inc.

INDUSTRY

Sponsor Role collaborator

ImagingNMD

UNKNOWN

Sponsor Role collaborator

SYSNAV

INDUSTRY

Sponsor Role collaborator

Edgewise Therapeutics, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Joanne Donovan, MD, PhD

Role: STUDY_CHAIR

Edgewise Therapeutics, Inc.

Roxana D. Dreghici

Role: STUDY_CHAIR

Edgewise Therapeutics, Inc.

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Arkansas Children's Hospital

Little Rock, Arkansas, United States

Site Status

UC San Diego

La Jolla, California, United States

Site Status

UCLA Medical Center

Los Angeles, California, United States

Site Status

UC Irvine Medical Center

Orange, California, United States

Site Status

Stanford Neuroscience Health Center

Palo Alto, California, United States

Site Status

UC Davis Medical Center

Sacramento, California, United States

Site Status

UC Denver

Aurora, Colorado, United States

Site Status

University of Florida

Gainesville, Florida, United States

Site Status

Rare Disease Research

Atlanta, Georgia, United States

Site Status

Northwestern University

Chicago, Illinois, United States

Site Status

Indiana University School of Medicine

Indianapolis, Indiana, United States

Site Status

University of Iowa

Iowa City, Iowa, United States

Site Status

University of Kansas Medical Center

Kansas City, Kansas, United States

Site Status

Kennedy Krieger Institute

Baltimore, Maryland, United States

Site Status

University of Massachusetts Memorial Medical Center

Worcester, Massachusetts, United States

Site Status

University of Minnesota

Minneapolis, Minnesota, United States

Site Status

Washington University School of Medicine

St Louis, Missouri, United States

Site Status

University of Rochester Medical Center

Rochester, New York, United States

Site Status

Rare Disease Research, LLC NC

Hillsborough, North Carolina, United States

Site Status

University of Cincinnati Gardner Neuroscience Institute

Cincinnati, Ohio, United States

Site Status

Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

University of Pennsylvania

Philadelphia, Pennsylvania, United States

Site Status

University of Pittsburgh

Pittsburgh, Pennsylvania, United States

Site Status

National Neuromuscular Research Institute

Austin, Texas, United States

Site Status

Neurology Rare Disease Center

Denton, Texas, United States

Site Status

Virginia Commonwealth University Health

Richmond, Virginia, United States

Site Status

St Vincent's Hospital Melbourne

Fitzroy, , Australia

Site Status

University Hospital Gent

Ghent, , Belgium

Site Status

Universitaire Ziekenhuizen Leuven

Leuven, , Belgium

Site Status

Centre Hospitalier Régional de la Citadelle

Liège, , Belgium

Site Status

Rigshospitalet

Copenhagen, , Denmark

Site Status

Centre de Reference des Maladies Neuromusculaires et de la SLA - AP-HM Hopital de La Timone

Marseille, , France

Site Status

CHU de Nantes

Nantes, , France

Site Status

CHU de Nice - Hopital Pasteur 2 - Centre de reference des Maladies Neuromusculaires

Nice, , France

Site Status

AP-HP Hopital Pitie-Salpetriere

Paris, , France

Site Status

Klinikum der Ludwig-Maximilians-Universitaet Muenchen

Munich, , Germany

Site Status

Hadassah University Hospital

Jerusalem, , Israel

Site Status

Schneider Children's Hospital of Israel

Petah Tikva, , Israel

Site Status

Fondazione IRCCS Ca'Granda Ospedale Maggiore Policlinico di Milano

Milan, , Italy

Site Status

Azienda Ospedale - Università Padova

Padua, , Italy

Site Status

Fondazione Policlinico Universitario A. Gemelli IRCCS - Universita Cattolica del Sacro Cuore

Rome, , Italy

Site Status

Leids Universitair Medisch Centrum

Leiden, , Netherlands

Site Status

Optimal Clinical Trials

Auckland, , New Zealand

Site Status

Hospital Universitario Vall d'Hebron

Barcelona, , Spain

Site Status

Hospital Universitari de Bellvitge

Barcelona, , Spain

Site Status

Hospital Universitario Donostia

Donostia / San Sebastian, , Spain

Site Status

Hospital Universitari i Politecnic La Fe

Valencia, , Spain

Site Status

University College London Hospital

London, , United Kingdom

Site Status

St. George's University Hospitals NHS Foundation Trust

London, , United Kingdom

Site Status

Newcastle Freeman Hospital

Newcastle, , United Kingdom

Site Status

Salford Royal Hospital

Salford, , United Kingdom

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States Australia Belgium Denmark France Germany Israel Italy Netherlands New Zealand Spain United Kingdom

Related Links

Access external resources that provide additional context or updates about the study.

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

EDG-5506-201

Identifier Type: -

Identifier Source: org_study_id

More Related Trials

Additional clinical trials that may be relevant based on similarity analysis.

Study Evaluating MYO-029 in Adult Muscular Dystrophy
NCT00104078 COMPLETED PHASE1/PHASE2
Defining Endpoints in Becker Muscular Dystrophy
NCT05257473 ACTIVE_NOT_RECRUITING
Phase I/II Study of SRP-4053 in DMD Patients
NCT02310906 COMPLETED PHASE1/PHASE2