A Safety Study for Previously Treated Vatiquinone (PTC743) Participants With Inherited Mitochondrial Disease

NCT ID: NCT05218655

Last Updated: 2025-12-22

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE3

Total Enrollment

101 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-06-22

Study Completion Date

2025-04-15

Brief Summary

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The primary objective of this study is to assess the safety of vatiquinone in participants with inherited mitochondrial disease who had prior exposure to vatiquinone in a PTC/BioElectron sponsored (previously Edison) clinical study or treatment plan.

The study will continue until vatiquinone becomes commercially available or the program is terminated.

Detailed Description

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Conditions

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Inherited Mitochondrial Disease

Keywords

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Leigh syndrome Alpers Syndrome mitochondrial encephalomyopathy MELAS MERRF PCH6 refractory epilepsy

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Vatiquinone

Participants will receive vatiquinone oral solution (100 milligrams \[mg\]/milliliter \[mL\]), up to 400 mg, administered orally or via feeding tube 3 times daily (TID).

Group Type EXPERIMENTAL

Vatiquinone

Intervention Type DRUG

Vatiquinone will be administered per dose and schedule specified in the arm description.

Interventions

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Vatiquinone

Vatiquinone will be administered per dose and schedule specified in the arm description.

Intervention Type DRUG

Other Intervention Names

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PTC743

Eligibility Criteria

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Inclusion Criteria

* Participants with inherited mitochondrial disease including Leigh syndrome, Alpers syndrome, mitochondrial encephalomyopathy, lactic acidosis and stroke-like episodes (MELAS), myoclonic epilepsy with ragged-red fibers (MERRF), pontocerebellar hypoplasia type 6 (PCH6), or other mitochondrial disease who participated in a previous vatiquinone clinical study or treatment plan.
* Women of childbearing potential must have a negative pregnancy test at screening/baseline and agree to abstinence or the use of at least 1 of the highly effective forms of contraception as specified in the protocol (with a failure rate of \<1% per year when used consistently and correctly). Highly effective contraception or abstinence must be continued for the duration of the study, and for up to 30 days after the last dose of study drug.
* Fertile men who are sexually active with women of childbearing potential and who have not had a vasectomy, must agree to use a barrier method of birth control during the study and for up to 30 days after the last dose of study drug.

Exclusion Criteria

* Current participation in any other interventional study.
* Pregnancy or breast feeding.
Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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PTC Therapeutics

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Vinay Penematsa, MD

Role: STUDY_DIRECTOR

PTC Therapeutics

Locations

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University of California, San Diego Altman Clinical and Translational Research Institute

La Jolla, California, United States

Site Status

Stanford University

Stanford, California, United States

Site Status

Yale Medicine

New Haven, Connecticut, United States

Site Status

Children's National

Washington D.C., District of Columbia, United States

Site Status

Child Neurology Center of Northwest Florida

Gulf Breeze, Florida, United States

Site Status

The Johns Hopkins University

Baltimore, Maryland, United States

Site Status

Columbia University Medical Center - CUMC

New York, New York, United States

Site Status

Akron Children's Hospital

Akron, Ohio, United States

Site Status

Cleveland Clinic

Cleveland, Ohio, United States

Site Status

Children's Hospital of Philadelphia - CHOP

Philadelphia, Pennsylvania, United States

Site Status

Medical University of South Carolina - MUSC

Charleston, South Carolina, United States

Site Status

Baylor College of Medicine

Houston, Texas, United States

Site Status

UT Health The University of Texas

Houston, Texas, United States

Site Status

Seattle Children Hospital

Seattle, Washington, United States

Site Status

Chu Angers

Angers, , France

Site Status

CHU Montpellier - Hopital Saint-Eloi

Montpellier, , France

Site Status

Hopital Necker-Enfants Malades

Paris, , France

Site Status

Hôpital de Hautepierre - Hôpitaux Universitaires de Strasbourg

Strasbourg, , France

Site Status

Ospedale Pediatrico Bambino Gesù

Roma, , Italy

Site Status

PTC Clinical Site

Japanese City, , Japan

Site Status

Instytut Pomnik - Centrum Zdrowia Dziecka

Warsaw, , Poland

Site Status

Hospital Sant Joan de Déu

Barcelona, , Spain

Site Status

Hospital Universitario 12 de Octubre

Madrid, , Spain

Site Status

Hospital Ruber Internacional

Madrid, , Spain

Site Status

Great Ormond Street Hospital for Children NHS Foundation Trust

London, , United Kingdom

Site Status

The Newcastle Upon Tyne Hospitals NHS Foundation Trust

Newcastle upon Tyne, , United Kingdom

Site Status

Countries

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United States France Italy Japan Poland Spain United Kingdom

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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2022-000375-39

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

PTC743-CNS-005-LSEP

Identifier Type: -

Identifier Source: org_study_id