Safety and Efficacy Study of Transplantation of Autologous CD34+ Cells Transduced With the G2ARTE Lentiviral Vector Expressing the DCLRE1C cDNA in Artemis (DCLRE1C) Deficient Severe Combined Immunodeficiency Patients (ARTEGENE)

NCT ID: NCT05071222

Last Updated: 2023-11-27

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

5 participants

Study Classification

INTERVENTIONAL

Study Start Date

2023-07-19

Study Completion Date

2041-07-19

Brief Summary

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The purpose of this study is to evaluate the Safety and Efficacy of Gene Therapy of the severe combined immunodeficiency (SCID) caused by mutations in the human DCLRE1C gene (Artemis) by transplantation of a single dose of autologous CD34+ cells transduced ex vivo with the G2ARTE lentiviral vector expressing the DCLRE1C cDNA.

Detailed Description

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Conditions

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Artemis (DCLRE1C ) Deficient Severe Combined Immunodeficiency

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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ARTEGENE drug product

Autologous purified CD34+ cells transduced with a self-inactivated lentiviral vector, expressing the DCLRE1C gene (alias Artemis)

Group Type EXPERIMENTAL

ARTEGENE drug product

Intervention Type GENETIC

Each patient will receive a single intravenous infusion of ARTEGENE drug product at D0.

Interventions

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ARTEGENE drug product

Each patient will receive a single intravenous infusion of ARTEGENE drug product at D0.

Intervention Type GENETIC

Eligibility Criteria

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Inclusion Criteria

* Patient to 47 months
* SCID patients with confirmed biallelic mutations in the Artemis (DCLRE1C) gene even in the case of leaky forms characterised by a residual activity
* Absence of an HLA genoidentical donor or without rapidly available HLA-compatible unrelated donor (within six weeks of diagnosis)
* The patient can be treated by gene therapy without delay in case of active life threatening infections compromising the short-term prognosis and for which the delay in finding a phenoidentical donor is incompatible with the patient's condition of health. Active life threatening infections are defined as: viral respiratory infection, CMV infection, adenovirus infection, disseminated BCGitis or other infections grade ≥ 4 according to CTCAE scale
* Beneficiary of a social security scheme
* Parental, guardian's patient signed informed consent.

Exclusion Criteria

* Unwillingness to return for follow-up during the first 2 years study and the long term follow-up
* HIV-1 or 2 or HTLV1 infections
* Hypersensitivity to G-CSF, busulfan or Fludarabine
* Unable to tolerate general anesthesia and/or marrow harvest or peripheral blood stem cell collection (apheresis) or insertion of central venous catheter.
Maximum Eligible Age

47 Months

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Assistance Publique - Hôpitaux de Paris

OTHER

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Alessandra MAGNANI, MD, PhD

Role: STUDY_DIRECTOR

Department of Biotherapy,LTCG, Necker-Enfants Malades Hospital

Chantal Lagresle-Peyrou, MD

Role: STUDY_DIRECTOR

IMAGINE

Locations

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Department of Pediatric Immunology, Hematology and Rheumatology UIHR, Necker-Enfants Malades Hospital

Paris, , France

Site Status RECRUITING

Countries

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France

Central Contacts

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Marina CAVAZZANA, MD, PhD

Role: CONTACT

+33 144495068

Jinmi BAEK, Master

Role: CONTACT

+33 1 42 19 28 49

Facility Contacts

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Despina MOSHOUS, MD, PhD

Role: primary

Other Identifiers

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2019-003555-11

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

D20180302

Identifier Type: -

Identifier Source: org_study_id