Open-Label Safety Study of Acoramidis (AG10) in Symptomatic ATTR Participants

NCT ID: NCT04988386

Last Updated: 2025-10-14

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

389 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-10-27

Study Completion Date

2028-05-15

Brief Summary

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Open-Label Extension and Safety Monitoring Study of Acoramidis (AG10) in Participants with Symptomatic Transthyretin Amyloid Cardiomyopathy Who Completed the Phase 3 ATTRibute-CM Trial (AG10-301)

Detailed Description

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The primary objective of this prospective, multi-center, open-label study is to evaluate the long-term safety and tolerability of acoramidis in patients with an established diagnosis of ATTR-CM and heart failure who are concomitantly treated with currently recommended heart failure therapies. Secondary efficacy and PD objectives will be assessed. Exploratory objectives may also be assessed.

All participants who complete 30 months of blinded study treatment and the Month 30 assessments of the double-blind treatment period of the Phase 3 ATTRibute-CM trial (AG10-301) may be eligible to participate in this Open Label Extension (OLE) study of acoramidis. The Day 1 visit in Study AG10-304 may be the same as the Month 30 visit in Study AG10-301. Under these circumstances, the last dose of Investigational Medicinal Product (IMP) in Study AG10-301 (either blinded acoramidis or matching placebo) will be the night before the day of the Month 30 visit. The first dose of open-label acoramidis in Study AG10-304 will be during the Study AG10-304 Day 1 visit after baseline assessments have been completed.

Currently, tafamidis is approved for the treatment of ATTR-CM in some regions. Participants are not allowed to be treated with tafamidis or any other ATTR-CM-specific approved or investigational treatment, or therapies used off-label or as non-prescription supplements for ATTR-CM at any time during the study. If participants choose treatment with an alternative treatment as described above, they will be asked to discontinue acoramidis and complete an End of Treatment (EoT) form, and they may be asked to discontinue/withdraw from the study. If a participant discontinues/withdraws from the study, the participant will be asked to complete an early termination visit and a safety follow-up visit.

Participants are not permitted to participate in another interventional clinical trial (except Study AG10-301) within 30 days prior to dosing and throughout Study AG10-304. Participants who choose to participate in another interventional clinical trial will be asked to withdraw from acoramidis and complete an EoT form, and they may be asked to discontinue/withdraw from the study. If a participant discontinues/withdraws from the study, the participant will be asked to complete an early termination visit and a safety follow-up visit. Participation in observational and/or registry studies should be discussed with the Medical Monitor.

Conditions

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Amyloid Cardiomyopathy, Transthyretin-Related

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Open-label study extension study from the AG10-301 double-blind study.
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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AG10

Open-label study all participants will receive AG10 during this study.

Group Type EXPERIMENTAL

Acoramidis (AG10)

Intervention Type DRUG

Acoramidis (AG10) twice daily

Interventions

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Acoramidis (AG10)

Acoramidis (AG10) twice daily

Intervention Type DRUG

Other Intervention Names

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AG10 ALXN 2060

Eligibility Criteria

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Inclusion Criteria

1. Completed 30 months of the blinded study treatment in Study AG10-301 and the Study AG10-301 Month 30 visit including assessments and procedures.
2. Have the ability to understand and sign a written informed consent form, which must be obtained prior to initiation of study procedures.
3. Female participants of childbearing potential who engage in heterosexual intercourse must agree to use a highly effective method of contraception beginning with enrollment and continuing for 30 days after the last dose of acoramidis. Female participants using oral contraceptives must agree to use an additional birth control method. While not considered highly effective, a double-barrier method is acceptable. A male participant who is sexually active with a female of childbearing potential and has not had a vasectomy must agree to use a double-barrier method of birth control.

Exclusion Criteria

1. Acute myocardial infarction, acute coronary syndrome or coronary revascularization within 90 days prior to Day 1 stroke or transient ischemic attack (TIA) within 90 days prior to Day 1.
2. Has hemodynamic instability, that in the judgment of the Investigator, would pose too great a risk for participation in the study.
3. Has had a heart and/or liver transplant or is on the heart transplantation list within the year prior to Day 1
4. Has had implantation of a cardiac mechanical assist device (CMAD) or is scheduled for implantation of a CMAD
5. Has confirmed diagnosis of light-chain (AL) amyloidosis at any time during Study AG10-301.
6. Has estimated glomerular filtration rate (eGFR) by modification of diet for renal disease (MDRD) formula \< 15 mL/min/1.73 m2 at Month 27 of Study AG10-301 or at any subsequent central lab value prior to Day 1.
7. Known hypersensitivity to acoramidis, its metabolites, or formulation excipients.
8. At the end of Study AG10-301 or at Day 1 of Study AG10-304 (or any time during the study), participant is on prohibited medication.
9. Females who are pregnant or breastfeeding. A negative urine pregnancy test at the Day 1 visit and at each study visit are required for female participants of childbearing potential.
10. In the judgment of the Investigator or Medical Monitor, has any clinically important ongoing medical condition or laboratory abnormality or condition that might jeopardize the participant's safety, increase their risk from participation, or interfere with the study.
11. Participation in another interventional clinical trial (with the exception of Study AG10-301) within 30 days prior to dosing. Participation in observational and/or registry studies should be discussed with the Medical Monitor.
12. Has any condition that in the opinion of the Investigator or Medical Monitor would preclude compliance with the study protocol such as a history of substance abuse, alcoholism, or a psychiatric condition.
Minimum Eligible Age

18 Years

Maximum Eligible Age

90 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Eidos Therapeutics, a BridgeBio company

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Cedars-Sinai Medical Center

Los Angeles, California, United States

Site Status

University of Colorado Hospital - Anschutz Medical Campus

Aurora, Colorado, United States

Site Status

Northwestern University

Chicago, Illinois, United States

Site Status

University of Chicago Medical Center

Chicago, Illinois, United States

Site Status

NorthShore University Health System

Evanston, Illinois, United States

Site Status

MedStar Medical Group Cardiology at Franklin Square

Baltimore, Maryland, United States

Site Status

Boston University Medical Center General Clinical Research Unit

Boston, Massachusetts, United States

Site Status

Mayo Clinic - Rochester

Rochester, Minnesota, United States

Site Status

Saint Luke's Hospital of Kansas City

Kansas City, Missouri, United States

Site Status

Washington University

St Louis, Missouri, United States

Site Status

New York University Langone Health

New York, New York, United States

Site Status

Columbia University Irving Medical Center

New York, New York, United States

Site Status

Laurelton Heart Specialists

Rosedale, New York, United States

Site Status

Montefiore Medical Center at Hutchinson

The Bronx, New York, United States

Site Status

Duke University Health System - Duke Clinic

Durham, North Carolina, United States

Site Status

Cleveland Clinic Main Campus

Cleveland, Ohio, United States

Site Status

Oregon Health & Science University

Portland, Oregon, United States

Site Status

Penn Presbyterian Medical Center

Philadelphia, Pennsylvania, United States

Site Status

University of Pittsburgh Medical Center (UPMC)

Pittsburgh, Pennsylvania, United States

Site Status

Medical University of South Carolina

Charleston, South Carolina, United States

Site Status

University of Texas Southwestern Medical Center

Dallas, Texas, United States

Site Status

University of Utah

Salt Lake City, Utah, United States

Site Status

Virginia Commonwealth University Health System

Richmond, Virginia, United States

Site Status

Roanoke Heart Institute

Roanoke, Virginia, United States

Site Status

University of Washington School of Medicine

Seattle, Washington, United States

Site Status

Providence Sacred Heart Children's Hospital

Spokane, Washington, United States

Site Status

Saint Vincent's Hospital Sydney

Darlinghurst, New South Wales, Australia

Site Status

Princess Alexandra Hospital

Woolloongabba, Queensland, Australia

Site Status

Royal Adelaide Hospital

Adelaide, South Australia, Australia

Site Status

Royal Hobart Hospital

Hobart, Tasmania, Australia

Site Status

Box Hill Hospital

Box Hill, Victoria, Australia

Site Status

Fiona Stanley Hospital

Murdoch, Western Australia, Australia

Site Status

Ziekenhuis Oost-Limburg

Genk, Limburg, Belgium

Site Status

Algemeen Ziekenhuis Sint-Jan Brugge-Oostende - Campus Sint-Jan

Bruges, West Vlaanderen, Belgium

Site Status

Instituto de Cardiologia do Rio Grande do Sul

Porto Alegre, Rio Grande do Sul, Brazil

Site Status

Centro Avançado de Pesquisa e Estudos para o Diagnóstico CAPED

Ribeirão Preto, São Paulo, Brazil

Site Status

Instituto do Coração de São Paulo

São Paulo, São Paulo, Brazil

Site Status

Vancouver General Hospital

Vancouver, British Columbia, Canada

Site Status

Saint Boniface Hospital

Winnipeg, Manitoba, Canada

Site Status

Queen Elizabeth II Health Sciences Centre - Halifax Infirmary

Halifax, Nova Scotia, Canada

Site Status

Toronto Heart Centre

Toronto, Ontario, Canada

Site Status

L' Institut de Cardiologie de Montréal

Montreal, Quebec, Canada

Site Status

Centre de Recherche du Centre Hospitalier de l'Université de Montréal (CHUM)

Montreal, Quebec, Canada

Site Status

Hôpital du Sacré-Coeur de Montréal

Montreal, Quebec, Canada

Site Status

Hôpital régional de Rimouski

Rimouski, Quebec, Canada

Site Status

Vseobecna Fakultni Nemocnice v Praze

Prague, Prague, Czechia

Site Status

Institut Klinické a Experimentální Medicíny

Prague, Prague, Czechia

Site Status

Fakultní Nemocnice u sv. Anny v Brně

Brno, South Moravian, Czechia

Site Status

Aarhus Universitets Hospital

Aarhus N, Palle Juul-Jensens, Denmark

Site Status

Alexandra General Hospital of Athens

Athens, Attica, Greece

Site Status

Mater Misericordiae University Hospital

Dublin, Dublin, Ireland

Site Status

The Chaim Sheba Medical Center

Ramat Gan, Tel Aviv, Israel

Site Status

Hadassah University Hospital Ein Kerem

Jerusalem, , Israel

Site Status

Ospedale San Donato

Arezzo, Arezzo, Italy

Site Status

Azienda Ospedaliero - Universitaria Careggi

Florence, Florence, Italy

Site Status

Fondazione Toscana Gabriele Monasterio per la Ricerca Medica e di Sanità Pubblica

Pisa, Pisa, Italy

Site Status

Fondazione IRCCS Policlinico San Matteo

Pavia, , Italy

Site Status

Universitair Medisch Centrum Groningen

Groningen, Provincie Groningen, Netherlands

Site Status

Universitair Medisch Centrum Utrecht

Utrecht, Utrecht, Netherlands

Site Status

Middlemore Clinical Trials - Middlemore Hospital

Papatoetoe, Auckland, New Zealand

Site Status

Waikato Hospital

Hamilton, Waikato Region, New Zealand

Site Status

Centro Hospitalar Universitário Lisboa Norte EPE- Hospital Santa Maria

Lisbon, Lisbon District, Portugal

Site Status

Seoul National University Bundang Hospital

Seongnam-si, Gyeonggi-do, South Korea

Site Status

Seoul National University Hospital

Seoul, Gyeonggi-do, South Korea

Site Status

Hospital Son Llàtzer

Palma de Mallorca, Balearic Islands, Spain

Site Status

Complejo Hospitalario Universitario de Santiago (CHUS)

Santiago de Compostela, La Coruña, Spain

Site Status

Clinica Universidad de Navarra Madrid

Madrid, Madrid, Spain

Site Status

Hospital Universitario Puerta de Hierro - Majadahonda

Majadahonda, Madrid, Spain

Site Status

Clínica Universidad de Navarra

Pamplona, Navarre, Spain

Site Status

Hospital Clínico Universitario de Valencia

Valencia, Valencia, Spain

Site Status

National Amyloidosis Centre, Division of Medicine - Royal Free

London, England, United Kingdom

Site Status

Richmond Pharmacology Ltd

London, England, United Kingdom

Site Status

Countries

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United States Australia Belgium Brazil Canada Czechia Denmark Greece Ireland Israel Italy Netherlands New Zealand Portugal South Korea Spain United Kingdom

References

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Judge DP, Gillmore JD, Alexander KM, Ambardekar AV, Cappelli F, Fontana M, Garcia-Pavia P, Grodin JL, Grogan M, Hanna M, Masri A, Nativi-Nicolau J, Obici L, Hvitfeldt Poulsen S, Sarswat N, Shah K, Soman P, Lystig T, Cao X, Wang K, Pecoraro ML, Tamby JF, Katz L, Sinha U, Fox JC, Maurer MS. Long-Term Efficacy and Safety of Acoramidis in ATTR-CM: Initial Report From the Open-Label Extension of the ATTRibute-CM Trial. Circulation. 2025 Mar 4;151(9):601-611. doi: 10.1161/CIRCULATIONAHA.124.072771. Epub 2024 Nov 18.

Reference Type DERIVED
PMID: 39556242 (View on PubMed)

Other Identifiers

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2020-005643-22

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

AG10-304

Identifier Type: -

Identifier Source: org_study_id

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